Gamma-delta T-cell Lymphoma with CNS Involvement Presenting with Proptosis: A Case Study Workup, Treatment and Prognosis

Abstract

Introduction: Ocular adnexal lymphomas are rare and T cell variants are a minor subset of these lymphomas. We aim to describe a case report which underlines the diagnostic and treatment challenge of this rare pathology.

Case: A 34-year-old gentleman has been shown to have exophthalmos and dysfunction of cranial nerve V andVII unilaterally. Imaging including CT and MRI brain and orbits do not show a CNS component to the disease. It was later identified as an ocular adnexal lymphoma with a central nervous system (CNS) component diagnosed via lumbar puncture.

Discussion: We highlight the importance of excluding ocular adnexal lymphoma and difficulty of management of the disease where it presents as a masquerade syndrome for orbital cellulitis.

KEYWORDS::

• Lymphoma
• Proptosis
• Gamma-Delta T-Cell lymphoma

Declaration of interest: The authors report no conflicts of interest. The authors alone are responsible for the content and writing of the paper.