Effective surgical treatment of progressive nodular histiocytosis

Abstract

Progressive nodular histiocytosis (PNH) is a rare benign self-limiting histiocytic disorder of the skin that is characterised by the progressive appearance of widespread xanthomatous lesions with no spontaneous remission. We operated on a 13-year-old girl with PNH four times with a result that had stabilised the condition at 1 year.

Key Words::

• Progressive nodular histiocytosis
• juvenile xanthogranuloma
• radical surgical treatment

Declaration of interest

The authors report no conflicts of interest. The authors alone are responsible for the content and writing of the paper.