Distraction osteogenesis of the sternum for thoracic expansion in a severe case of jeune syndrome: a preliminary report

Abstract

Severe asphyxiating thoracic dystrophy (Jeune syndrome) is usually fatal. The authors used distraction osteogenesis in a severe case and achieved 45 mm distraction of the sternum and improvement in tidal volume, lung compliance, and mean airway pressure.

Keywords:

• Jeune syndrome
• distraction osteogenesis
• thoracic expansion