Chiari Malformation

Abstract

Chiari malformations were first reported in 1891 by Chiari¹ and again in 1894 by Arnold.² There is inferior herniation of the cerebellum causing a host of neurological deficits. There are three clinical types. With the first two a patient is usually able to perform normally. The third, more severe, type, is incompatible with living. We have found that eliminating the activity that causes the symptoms is occasionally all the treatment that is needed. Surgical decompression of the posterior fossa may also reverse the complaints of diplopia and oscillopsia. Highlighting the posterior fossa clearly in the MRI is the key to the proper diagnosis and management.

• Chiari malformation
• nystagmus
• strabismus