298
Views
6
CrossRef citations to date
0
Altmetric
Grand Rounds

Neurocognitive Profile of a Woman with Susac’s Syndrome: Further Evidence of Cognitive Variability

, , &
Pages 689-706 | Received 27 Oct 2014, Accepted 22 Jul 2015, Published online: 14 Sep 2015

References

  • Assuras, S., & Lacy, M. (2011). Psychiatric presentation in possible Susac's syndrome. Journal of Neuropsychiatry and Clinical Neurosciences, 23, E30.10.1176/jnp.23.3.jnpe30
  • Ballard, E., Butzer, B. F., & Donders, J. (1996). Susac’s syndrome: Neuropsychological characteristics in a young man. Neurology, 47, 266–268.10.1212/WNL.47.1.266
  • Barona, A., & Chastain, R. L. (1986). An improved estimate of premorbid IQ for Blacks and Whites on the WAIS-R. International Journal of Clinical Neuropsychology, 8, 167–173.
  • Beck, A. T., Steer, R. A., & Brown, G. K. (1996). Beck depression inventory (BDI-II). Toronto: The Psychological Corporation.
  • Benton, A. L., Sivan, A. B., Hamsher, K. deS., Varney, N. R., & Spreen, O. (1994). Contributions to neuropsychological assessment: A clinical manual (2nd ed.). New York, NY: Oxford University Press.
  • Bogousslavsky, J., Gaio, J. M., Caplan, L. R., Regli, F., Hommel, M., Hedges, T. R., … Pollak, P. (1989). Encephalopathy, deafness and blindness in young women: A distinct retinocochleocerebral arteriolopathy? Journal of Neuropsychiatry & Clinical Neurosciences, 52, 43–46.
  • Coppeto, J. R., Monteiro, M. L. R., Currie, J. N., & Lessell, S. (1984). A syndrome of arterial-occlusive retinopathy and encephalopathy. American Journal of Ophthalmology, 98, 189–202.10.1016/0002-9394(87)90354-0
  • Delis, D. C., Kramer, J. H., Kaplan, E., & Ober, B. A. (2000). The California verbal learning test (2nd ed.). San Antonio, TX: The Psychological Corporation.
  • Dörr J., Krautwald S., Wildemann B., Wildemann, B., Jarius, S., Ringelstein, M., … Kleffner, I. (2013). Characteristics of Susac syndrome: A review of all reported cases. Nature Reviews Neurology, 9, 307–316.10.1038/nrneurol.2013.82
  • Golden, C. J. (1978). Stroop color and word test: A manual for clinical and experimental-uses. Chicago, IL: Stoelting.
  • Goodglass, H., Kaplan, E., & Barresi, B. (2001). The assessment of aphasia and related disorders (3rd ed.). Philadelphia, PA: Lea & Feibiger.
  • Gordon, D. L., Hayreh, S. S., & Adams Jr., H. P. (1991). Microangiopathy of the brain, retina, and ear: Improvement without immunosuppressive therapy. Stroke, 22, 933–937.10.1161/01.STR.22.7.933
  • Greco, A., De Virgilio, A., Gallo, A., Fusconi, M., Turchetta, R., Tombolini, M., … de Vincentiis, M. (2014). Susac's syndrome-pathogenesis, clinical variants and treatment approaches. Autoimmunity Reviews, 13, 814–821.10.1016/j.autrev.2014.04.004
  • Gronwall, D. (1977). Paced auditory serial-addition task: A measure of recovery from concussion. Perceptual and Motor Skills, 44, 367–373.10.2466/pms.1977.44.2.367
  • Hahn, J. S., Lannin, W. C., & Sarwal, M. M. (2004). Microangiopathy of brain, retina, and inner ear (Susac's Syndrome) in an adolescent female presenting as acute disseminated encephalomyelitis. Pediatrics, 114, 276–281.10.1542/peds.114.1.276
  • Heaton, R. K. (1981). The Wisconsin card sorting test manual. Odessa: Psychological Assessment Resources.
  • Heiskala, H., Somer, H., Kovanen, J., Poutiainen, E., Karli, H., & Haltia, M. (1988). Microangiopathy with encephalopathy, hearing loss and retinal arteriolar occlusions: Two new cases. Journal of Neurological Sciences, 86, 239–250.10.1016/0022-510X(88)90102-5
  • Kaplan, E., Goodglass, H., & Weintraub, S. (1983). Boston naming test. Philadelphia, PA: Lea & Febiger.
  • Kleffner, I., Deppe, M., Mohammadi, S., Schiffbauer, H., Stupp, N., Lohmann, H., … Ringelstein, E. B. (2008). Diffusion tensor imaging demonstrates fiber impairment in Susac syndrome. Neurology, 70, 1867–1869.10.1212/01.wnl.0000280580.95671.01
  • Lezak, M. D., Howieson, D. B., & Loring, D. W. (2004). Neuropsychological assessment (4th ed.). New York, NY: Oxford University Press.
  • Mittenberg, W., DiGiulio, D. V., Perrin, S., & Bass, A. E. (1992). Symptoms following mild head injury: Expectation as aetiology. Journal of Neurology, Neurosurgery & Psychiatry, 55, 200–204.
  • Monteiro, M. L., Swanson, R. A., Coppeto, J. R., Cuneo, R. A., DeArmond, S. J., & Prusiner, S. B. (1985). A microangiopathic syndrome of encephalopathy, hearing loss, and retinal arteriolar occlusions. Neurology, 35, 1113–1121.10.1212/WNL.35.8.1113
  • O'Halloran, H. S., Pearson, P. A., Lee, W. B., Susac, J. O., & Berger, J. R. (1998). Microangiopathy of the brain retina, and cochlea (Susac’s syndrome): A report of five cases and a review of the literature. Ophthalmoscopy, 105, 1038–1044.10.1016/S0161-6420(98)96005-5
  • Rennebohm, R. M., Egan, R. A., & Susac, J. O. (2008). Treatment of Susac’s syndrome. Current Treatment Options in Neurology, 10, 67–74.10.1007/s11940-008-0008-y
  • Rennebohm, R. M., & Susac, J. O. (2007). Treatment of Susac’s syndrome. Journal of the Neurological Sciences, 257, 215–220.10.1016/j.jns.2007.01.031
  • Rey, A. (1941). L'examen psychologique dans les cas d'encéphalopathie traumatique [The psychological examination of cases of traumatic encephalopathy]. Archives de Psycholige, 37, 126–139.
  • Saw, V. P., Canty, P. A., Green, C. M., Briggs, R. J., Cremer, P. D., Harrisberg, B., … Watson, J. D. (2000). Susac syndrome: Microangiopathy of the retina, cochlea and brain. Clinical & Experimental Ophthalmology, 28, 373–381.
  • Spielberger, C. D. (1977). The state-trait anxiety inventory. Redwood City, CA: Mind Garden.
  • Spreen, O., & Strauss, E. (1998). A compendium of neuropsychological tests (2nd ed.). New York, NY:Oxford University Press.
  • Susac, J. O. (1994). Susac's syndrome: The triad of microangiopathy of the brain and retina with hearing loss in young women. Neurology, 44, 591–593.10.1212/WNL.44.4.591
  • Susac, J. O. (2004). Susac’s syndrome. American Journal of Neuroradiology, 25, 351–352.
  • Susac, J. O., Calabrese, L. H., Baylin, E., Prayson, R. A., Medeiros, N. E., Hull, R. P., Tucker, J.P. (2004). Branch retinal artery occlusions as the presenting feature of primary central nervous system vasculitis. Clinical and Experimental Rheumatology, 22, 70–74.
  • Susac, J. O., Hardman, J. M., & Selhorst, J. B. (1979). Microangiopathy of the brain and retina. Neurology, 29, 313–316.10.1212/WNL.29.3.313
  • Susac, J. O., Murtagh, F. R., Egan, R. A., Berger, J. R., Bakshi, R., Lincoff, N., … Daroff, R. B. (2003). MRI findings in Susac’s syndrome. Neurology, 61, 1783–1787.10.1212/01.WNL.0000103880.29693.48
  • Tashima, K., Uyama, E., Hashimoto, Y., Yonehara, T., & Uchino, M. (2001). Susac's syndrome: Beneficial effects of corticosteroid therapy in a Japanese case. Internal Medicine, 40, 135–139.10.2169/internalmedicine.40.135
  • The Psychological Corporation. (2001). Wechsler test of adult reading. New York, NY: Author.
  • Wechsler, D. (2008). Wechsler Adult Intelligence Scale (4th ed.). San Antonio, TX: Pearson.
  • Wechsler, D. A. (1997). Wechsler memory scale-third edition manual. San Antonio, TX: The Psychological Corporation.

Reprints and Corporate Permissions

Please note: Selecting permissions does not provide access to the full text of the article, please see our help page How do I view content?

To request a reprint or corporate permissions for this article, please click on the relevant link below:

Academic Permissions

Please note: Selecting permissions does not provide access to the full text of the article, please see our help page How do I view content?

Obtain permissions instantly via Rightslink by clicking on the button below:

If you are unable to obtain permissions via Rightslink, please complete and submit this Permissions form. For more information, please visit our Permissions help page.