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Review

Sudden cardiac death in adults with congenital heart disease

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Pages 1605-1620 | Published online: 10 Jan 2014

References

  • Marelli AJ, Mackie AS, Ionescu-Ittu R, Rahme E, Pilote L. Congenital heart disease in the general population: changing prevalence and age distribution. Circulation115, 163–172 (2007).
  • Warnes CA, Liberthson R, Danielson GK et al. Task force 1: the changing profile of congenital heart disease in adult life. J. Am. Coll. Cardiol.37, 1170–1175 (2001).
  • Warnes CA. The adult with congenital heart disease: born to be bad? J. Am. Coll. Cardiol.46, 1–8 (2005).
  • Deanfield J, Thaulow E, Warnes C et al. Management of grown up congenital heart disease. Eur. Heart J.24, 1035–1084 (2003).
  • Therrien J, Warnes C, Daliento L et al. Canadian Cardiovascular Society Consensus Conference 2001 update: recommendations for the management of adults with congenital heart disease part III. Can. J. Cardiol.17, 1135–1158 (2001).
  • Therrien J, Gatzoulis M, Graham T et al. Canadian Cardiovascular Society Consensus Conference 2001 update: Recommendations for the Management of Adults with Congenital Heart Disease – Part II. Can. J. Cardiol.17, 1029–1050 (2001).
  • Therrien J, Dore A, Gersony W et al. CCS Consensus Conference 2001 update: recommendations for the management of adults with congenital heart disease. Part I. Can. J. Cardiol.17, 940–959 (2001).
  • Warnes CA, Williams RG, Bashore TM et al. ACC/AHA 2008 Guidelines for the Management of Adults with Congenital Heart Disease: Executive Summary: a report of the American College of Cardiology/American Heart Association Task Force on Practice Guidelines (writing committee to develop guidelines for the management of adults with congenital heart disease). Circulation118, 2395–2451 (2008).
  • Nieminen HP, Jokinen EV, Sairanen HI. Causes of late deaths after pediatric cardiac surgery: a population-based study. J. Am. Coll. Cardiol.50, 1263–1271 (2007).
  • Oechslin EN, Harrison DA, Connelly MS, Webb GD, Siu SC. Mode of death in adults with congenital heart disease. Am. J. Cardiol.86, 1111–1116 (2000).
  • Silka MJ, Hardy BG, Menashe VD, Morris CD. A population-based prospective evaluation of risk of sudden cardiac death after operation for common congenital heart defects. J. Am. Coll. Cardiol.32, 245–251 (1998).
  • Zipes DP, Wellens HJ. Sudden cardiac death. Circulation98, 2334–2351 (1998).
  • Murphy JG, Gersh BJ, Mair DD et al. Long-term outcome in patients undergoing surgical repair of tetralogy of Fallot. N. Engl. J. Med.329, 593–599 (1993).
  • Nollert G, Fischlein T, Bouterwek S, Bohmer C, Klinner W, Reichart B. Long-term survival in patients with repair of tetralogy of Fallot: 36-year follow-up of 490 survivors of the first year after surgical repair. J. Am. Coll. Cardiol.30, 1374–1383 (1997).
  • Gatzoulis MA, Balaji S, Webber SA et al. Risk factors for arrhythmia and sudden cardiac death late after repair of tetralogy of Fallot: a multicentre study. Lancet356, 975–981 (2000).
  • Oechslin E, Jenni R. 40 years after the first atrial switch procedure in patients with transposition of the great arteries: long-term results in Toronto and Zurich. Thorac. Cardiovasc. Surg.48, 233–237 (2000).
  • Gelatt M, Hamilton RM, McCrindle BW et al. Arrhythmia and mortality after the Mustard procedure: a 30-year single-center experience. J. Am. Coll. Cardiol.29, 194–201 (1997).
  • Gewillig M, Cullen S, Mertens B, Lesaffre E, Deanfield J. Risk factors for arrhythmia and death after Mustard operation for simple transposition of the great arteries. Circulation84, III187–III192 (1991).
  • Flinn CJ, Wolff GS, Dick M 2nd et al. Cardiac rhythm after the Mustard operation for complete transposition of the great arteries. N. Engl. J. Med.310, 1635–1638 (1984).
  • Wilson NJ, Clarkson PM, Barratt-Boyes BG et al. Long-term outcome after the mustard repair for simple transposition of the great arteries. 28-year follow-up. J. Am. Coll. Cardiol.32, 758–765 (1998).
  • Janousek J, Paul T, Luhmer I, Wilken M, Hruda J, Kallfelz HC. Atrial baffle procedures for complete transposition of the great arteries: natural course of sinus node dysfunction and risk factors for dysrhythmias and sudden death. Z. Kardiol.83, 933–938 (1994).
  • Lange R, Horer J, Kostolny M et al. Presence of a ventricular septal defect and the Mustard operation are risk factors for late mortality after the atrial switch operation: thirty years of follow-up in 417 patients at a single center. Circulation114, 1905–1913 (2006).
  • Khairy P, Landzberg MJ, Lambert J, O’Donnell CP. Long-term outcomes after the atrial switch for surgical correction of transposition: a meta-analysis comparing the Mustard and Senning procedures. Cardiol. Young14, 284–292 (2004).
  • Rhodes LA, Wernovsky G, Keane JF et al. Arrhythmias and intracardiac conduction after the arterial switch operation. J. Thorac. Cardiovasc. Surg.109, 303–310 (1995).
  • Horer J, Schreiber C, Cleuziou J et al. Improvement in long-term survival after hospital discharge but not in freedom from reoperation after the change from atrial to arterial switch for transposition of the great arteries. J. Thorac. Cardiovasc. Surg.137, 347–354 (2009).
  • Khairy P, Fernandes SM, Mayer JE Jr et al. Long-term survival, modes of death, and predictors of mortality in patients with Fontan surgery. Circulation117, 85–92 (2008).
  • Diller GP, Dimopoulos K, Broberg CS et al. Presentation, survival prospects, and predictors of death in Eisenmenger syndrome: a combined retrospective and case-control study. Eur. Heart J.27, 1737–1742 (2006).
  • Niwa K, Perloff JK, Kaplan S, Child JS, Miner PD. Eisenmenger syndrome in adults: ventricular septal defect, truncus arteriosus, univentricular heart. J. Am. Coll. Cardiol.34, 223–232 (1999).
  • Daliento L, Somerville J, Presbitero P et al. Eisenmenger syndrome. Factors relating to deterioration and death. Eur. Heart J.19, 1845–1855 (1998).
  • Walsh EP. Interventional electrophysiology in patients with congenital heart disease. Circulation115, 3224–3234 (2007).
  • Zeppenfeld K, Schalij MJ, Bartelings MM et al. Catheter ablation of ventricular tachycardia after repair of congenital heart disease: electroanatomic identification of the critical right ventricular isthmus. Circulation116, 2241–2252 (2007).
  • Manning PB, Mayer JE Jr, Wernovsky G, Fishberger SB, Walsh EP. Staged operation to Fontan increases the incidence of sinoatrial node dysfunction. J. Thorac. Cardiovasc. Surg.111, 833–839; discussion 839–840 (1996).
  • Triedman JK, Jenkins KJ, Colan SD, Saul JP, Walsh EP. Intra-atrial reentrant tachycardia after palliation of congenital heart disease: characterization of multiple macroreentrant circuits using fluoroscopically based three-dimensional endocardial mapping. J. Cardiovasc. Electrophysiol.8, 259–270 (1997).
  • Gatzoulis MA, Walters J, McLaughlin PR, Merchant N, Webb GD, Liu P. Late arrhythmia in adults with the mustard procedure for transposition of great arteries: a surrogate marker for right ventricular dysfunction? Heart84, 409–415 (2000).
  • Khairy P, Harris L, Landzberg MJ et al. Sudden death and defibrillators in transposition of the great arteries with intra-atrial baffles. A multicenter study. Circ. Arrhythmia Electrophysiol.1, 250–257 (2008).
  • Garson A Jr, Bink-Boelkens M, Hesslein PS et al. Atrial flutter in the young: a collaborative study of 380 cases. J. Am. Coll. Cardiol.6, 871–878 (1985).
  • Hebe J. Ebstein’s anomaly in adults. Arrhythmias: diagnosis and therapeutic approach. Thorac. Cardiovasc. Surg.48, 214–219 (2000).
  • Smith WM, Gallagher JJ, Kerr CR et al. The electrophysiologic basis and management of symptomatic recurrent tachycardia in patients with Ebstein’s anomaly of the tricuspid valve. Am. J. Cardiol.49, 1223–1234 (1982).
  • Weindling SN, Saul JP, Gamble WJ, Mayer JE, Wessel D, Walsh EP. Duration of complete atrioventricular block after congenital heart disease surgery. Am. J. Cardiol.82, 525–527 (1998).
  • Anderson RH, Becker AE, Arnold R, Wilkinson JL. The conducting tissues in congenitally corrected transposition. Circulation50, 911–923 (1974).
  • Connelly MS, Liu PP, Williams WG, Webb GD, Robertson P, McLaughlin PR. Congenitally corrected transposition of the great arteries in the adult: functional status and complications. J. Am. Coll. Cardiol.27, 1238–1243 (1996).
  • Huhta JC, Maloney JD, Ritter DG, Ilstrup DM, Feldt RH. Complete atrioventricular block in patients with atrioventricular discordance. Circulation67, 1374–1377 (1983).
  • Walsh EP, Cecchin F. Arrhythmias in adult patients with congenital heart disease. Circulation115, 534–545 (2007).
  • Tuzcu EM, Moodie DS, Chambers JL, Keyser P, Hobbs RE. Congenital heart diseases associated with coronary artery anomalies. Cleve. Clin. J. Med.57, 147–152 (1990).
  • Barth CW 3rd, Roberts WC. Left main coronary artery originating from the right sinus of Valsalva and coursing between the aorta and pulmonary trunk. J. Am. Coll. Cardiol.7, 366–373 (1986).
  • Frommelt PC. Congenital coronary artery abnormalities predisposing to sudden cardiac death. Pacing Clin. Electrophysiol.32, S63–S66 (2009).
  • Krahn AD, Healey JS, Chauhan V et al. Systematic assessment of patients with unexplained cardiac arrest: Cardiac Arrest Survivors With Preserved Ejection Fraction Registry (CASPER). Circulation120, 278–285 (2009).
  • Gatzoulis MA, Till JA, Somerville J, Redington AN. Mechanoelectrical interaction in tetralogy of Fallot. QRS prolongation relates to right ventricular size and predicts malignant ventricular arrhythmias and sudden death. Circulation92, 231–237 (1995).
  • Ghai A, Silversides C, Harris L, Webb GD, Siu SC, Therrien J. Left ventricular dysfunction is a risk factor for sudden cardiac death in adults late after repair of tetralogy of Fallot. J. Am. Coll. Cardiol.40, 1675–1680 (2002).
  • Balaji S, Lau YR, Case CL, Gillette PC. QRS prolongation is associated with inducible ventricular tachycardia after repair of tetralogy of Fallot. Am. J. Cardiol.80, 160–163 (1997).
  • Schwerzmann M, Salehian O, Harris L et al. Ventricular arrhythmias and sudden death in adults after a Mustard operation for transposition of the great arteries. Eur. Heart J. (2009).
  • Huang CJ, Chiu IS, Lin FY et al. Role of electrophysiological studies and arrhythmia intervention in repairing Ebstein’s anomaly. Thorac. Cardiovasc. Surg.48, 347–350 (2000).
  • Garson A Jr, Randall DC, Gillette PC et al. Prevention of sudden death after repair of tetralogy of Fallot: treatment of ventricular arrhythmias. J. Am. Coll. Cardiol.6, 221–227 (1985).
  • Harrison DA, Harris L, Siu SC et al. Sustained ventricular tachycardia in adult patients late after repair of tetralogy of Fallot. J. Am. Coll. Cardiol.30, 1368–1373 (1997).
  • Khairy P, Landzberg MJ, Gatzoulis MA et al. Value of programmed ventricular stimulation after tetralogy of Fallot repair: a multicenter study. Circulation109, 1994–2000 (2004).
  • Cullen S, Celermajer DS, Franklin RC, Hallidie-Smith KA, Deanfield JE. Prognostic significance of ventricular arrhythmia after repair of tetralogy of Fallot: a 12-year prospective study. J. Am. Coll. Cardiol.23, 1151–1155 (1994).
  • Garson A Jr, Gillette PC, Gutgesell HP, McNamara DG. Stress-induced ventricular arrhythmia after repair of tetralogy of Fallot. Am. J. Cardiol.46, 1006–1012 (1980).
  • Kavey RE, Thomas FD, Byrum CJ, Blackman MS, Sondheimer HM, Bove EL. Ventricular arrhythmias and biventricular dysfunction after repair of tetralogy of Fallot. J. Am. Coll. Cardiol.4, 126–131 (1984).
  • Simson MB. Use of signals in the terminal QRS complex to identify patients with ventricular tachycardia after myocardial infarction. Circulation64, 235–242 (1981).
  • Perloff JK, Middlekauf HR, Child JS, Stevenson WG, Miner PD, Goldberg GD. Usefulness of post-ventriculotomy signal averaged electrocardiograms in congenital heart disease. Am. J. Cardiol.98, 1646–1651 (2006).
  • Omeroglu RE, Olgar S, Nisli K. Signal-averaged electrocardiogram may be a beneficial prognostic procedure in the postoperative follow-up tetralogy of Fallot patients to determine the risk of ventricular arrhythmias. Pediatr. Cardiol.28, 208–212 (2007).
  • Tede NH, Shivkumar K, Perloff JK et al. Signal-averaged electrocardiogram in Ebstein’s anomaly. Am. J. Cardiol.93, 432–436 (2004).
  • Janousek J, Paul T, Bartakova H. Role of late potentials in identifying patients at risk for ventricular tachycardia after surgical correction of congenital heart disease. Am. J. Cardiol.75, 146–150 (1995).
  • Stelling JA, Danford DA, Kugler JD et al. Late potentials and inducible ventricular tachycardia in surgically repaired congenital heart disease. Circulation82, 1690–1696 (1990).
  • Chow T, Kereiakes DJ, Bartone C et al. Microvolt T-wave alternans identifies patients with ischemic cardiomyopathy who benefit from implantable cardioverter-defibrillator therapy. J. Am. Coll. Cardiol.49, 50–58 (2007).
  • Hohnloser SH, Klingenheben T, Bloomfield D, Dabbous O, Cohen RJ. Usefulness of microvolt T-wave alternans for prediction of ventricular tachyarrhythmic events in patients with dilated cardiomyopathy: results from a prospective observational study. J. Am. Coll. Cardiol.41, 2220–2224 (2003).
  • Gold MR, Bloomfield DM, Anderson KP et al. A comparison of T-wave alternans, signal averaged electrocardiography and programmed ventricular stimulation for arrhythmia risk stratification. J. Am. Coll. Cardiol.36, 2247–2253 (2000).
  • Costantini O, Hohnloser SH, Kirk MM et al. The ABCD (Alternans Before Cardioverter Defibrillator) Trial: strategies using T-wave alternans to improve efficiency of sudden cardiac death prevention. J. Am. Coll. Cardiol.53, 471–479 (2009).
  • Gold MR, Ip JH, Costantini O et al. Role of microvolt T-wave alternans in assessment of arrhythmia vulnerability among patients with heart failure and systolic dysfunction: primary results from the T-wave alternans sudden cardiac death in heart failure trial substudy. Circulation118, 2022–2028 (2008).
  • Chow T, Kereiakes DJ, Onufer J et al. Does microvolt T-wave alternans testing predict ventricular tachyarrhythmias in patients with ischemic cardiomyopathy and prophylactic defibrillators? The MASTER (Microvolt T Wave Alternans Testing for Risk Stratification of Post-Myocardial Infarction Patients) trial. J. Am. Coll. Cardiol.52, 1607–1615 (2008).
  • Alexander ME, Cecchin F, Huang KP, Berul CI. Microvolt t-wave alternans with exercise in pediatrics and congenital heart disease: limitations and predictive value. Pacing Clin. Electrophysiol.29, 733–741 (2006).
  • Cheung MM, Weintraub RG, Cohen RJ et al. T wave alternans threshold late after repair of tetralogy of Fallot. J. Cardiovasc. Electrophysiol.13, 657–661 (2002).
  • La Rovere MT, Pinna GD, Hohnloser SH et al. Baroreflex sensitivity and heart rate variability in the identification of patients at risk for life-threatening arrhythmias: implications for clinical trials. Circulation103, 2072–2077 (2001).
  • Davos CH, Davlouros PA, Wensel R et al. Global impairment of cardiac autonomic nervous activity late after repair of tetralogy of Fallot. Circulation106, I69–I75 (2002).
  • Davos CH, Francis DP, Leenarts MF et al. Global impairment of cardiac autonomic nervous activity late after the Fontan operation. Circulation108(Suppl. 1), II180–II185 (2003).
  • Daliento L, Caneve F, Turrini P et al. Clinical significance of high-frequency, low-amplitude electrocardiographic signals and QT dispersion in patients operated on for tetralogy of Fallot. Am. J. Cardiol.76, 408–411 (1995).
  • Schmidt G, Malik M, Barthel P et al. Heart-rate turbulence after ventricular premature beats as a predictor of mortality after acute myocardial infarction. Lancet353, 1390–1396 (1999).
  • Barthel P, Schneider R, Bauer A, Ulm K, Schmitt C, Schomig A, Schmidt G. Risk stratification after acute myocardial infarction by heart rate turbulence. Circulation108, 1221–1226 (2003).
  • Lammers A, Kaemmerer H, Hollweck R et al. Impaired cardiac autonomic nervous activity predicts sudden cardiac death in patients with operated and unoperated congenital cardiac disease. J. Thorac. Cardiovasc. Surg.132, 647–655 (2006).
  • Bardy GH, Lee KL, Mark DB et al. Amiodarone or an implantable cardioverter-defibrillator for congestive heart failure. N. Engl. J. Med.352, 225–237 (2005).
  • Moss AJ, Zareba W, Hall WJ et al. Prophylactic implantation of a defibrillator in patients with myocardial infarction and reduced ejection fraction. N. Engl. J. Med.346, 877–883 (2002).
  • Knauth AL, Gauvreau K, Powell AJ et al. Ventricular size and function assessed by cardiac MRI predict major adverse clinical outcomes late after tetralogy of Fallot repair. Heart94, 211–216 (2008).
  • Khairy P, Harris L, Landzberg MJ et al. Implantable cardioverter-defibrillators in tetralogy of Fallot. Circulation117, 363–370 (2008).
  • Roos-Hesselink JW, Meijboom FJ, Spitaels SE et al. Decline in ventricular function and clinical condition after Mustard repair for transposition of the great arteries (a prospective study of 22–29 years). Eur. Heart J.25, 1264–1270 (2004).
  • Millane T, Bernard EJ, Jaeggi E et al. Role of ischemia and infarction in late right ventricular dysfunction after atrial repair of transposition of the great arteries. J. Am. Coll. Cardiol.35, 1661–1668 (2000).
  • Deanfield JE, Ho SY, Anderson RH et al. Late sudden death after repair of tetralogy of Fallot: a clinicopathologic study. Circulation67, 626–631 (1983).
  • Babu-Narayan SV, Kilner PJ, Li W et al. Ventricular fibrosis suggested by cardiovascular magnetic resonance in adults with repaired tetralogy of Fallot and its relationship to adverse markers of clinical outcome. Circulation113, 405–413 (2006).
  • Hornung TS, Kilner PJ, Davlouros PA, Grothues F, Li W, Gatzoulis MA. Excessive right ventricular hypertrophic response in adults with the mustard procedure for transposition of the great arteries. Am. J. Cardiol.90, 800–803 (2002).
  • Singh TP, Humes RA, Muzik O, Kottamasu S, Karpawich PP, Di Carli MF. Myocardial flow reserve in patients with a systemic right ventricle after atrial switch repair. J. Am. Coll. Cardiol.37, 2120–2125 (2001).
  • Babu-Narayan SV, Goktekin O, Moon JC et al. Late gadolinium enhancement cardiovascular magnetic resonance of the systemic right ventricle in adults with previous atrial redirection surgery for transposition of the great arteries. Circulation111, 2091–2098 (2005).
  • Wald RM, Haber I, Wald R, Valente AM, Powell AJ, Geva T. Effects of regional dysfunction and late gadolinium enhancement on global right ventricular function and exercise capacity in patients with repaired tetralogy of Fallot. Circulation119, 1370–1377 (2009).
  • Oosterhof T, Mulder BJ, Vliegen HW, de Roos A. Corrected tetralogy of Fallot: delayed enhancement in right ventricular outflow tract. Radiology237, 868–871 (2005).
  • Alexander ME, Walsh EP, Saul JP, Epstein MR, Triedman JK. Value of programmed ventricular stimulation in patients with congenital heart disease. J. Cardiovasc. Electrophysiol.10, 1033–1044 (1999).
  • Vliegen HW, van Straten A, de Roos A et al. Magnetic resonance imaging to assess the hemodynamic effects of pulmonary valve replacement in adults late after repair of tetralogy of Fallot. Circulation106, 1703–1707 (2002).
  • Oosterhof T, van Straten A, Vliegen HW et al. Preoperative thresholds for pulmonary valve replacement in patients with corrected tetralogy of Fallot using cardiovascular magnetic resonance. Circulation116, 545–551 (2007).
  • Therrien J, Provost Y, Merchant N, Williams W, Colman J, Webb G. Optimal timing for pulmonary valve replacement in adults after tetralogy of Fallot repair. Am. J. Cardiol.95, 779–782 (2005).
  • Therrien J, Siu SC, Harris L et al. Impact of pulmonary valve replacement on arrhythmia propensity late after repair of tetralogy of Fallot. Circulation103, 2489–2494 (2001).
  • van Huysduynen BH, van Straten A, Swenne CA et al. Reduction of QRS duration after pulmonary valve replacement in adult Fallot patients is related to reduction of right ventricular volume. Eur. Heart J.26, 928–932 (2005).
  • Gengsakul A, Harris L, Bradley TJ et al. The impact of pulmonary valve replacement after tetralogy of Fallot repair: a matched comparison. Eur. J. Cardiothorac. Surg.32, 462–468 (2007).
  • Oosterhof T, Vliegen HW, Meijboom FJ et al. Long-term effect of pulmonary valve replacement on QRS duration in patients with corrected tetralogy of Fallot. Heart93, 506–509 (2007).
  • Harrild DM, Berul CI, Cecchin F et al. Pulmonary valve replacement in tetralogy of Fallot: impact on survival and ventricular tachycardia. Circulation119, 445–451 (2009).
  • Alexander ME, Cecchin F, Walsh EP, Triedman JK, Bevilacqua LM, Berul CI. Implications of implantable cardioverter defibrillator therapy in congenital heart disease and pediatrics. J. Cardiovasc. Electrophysiol.15, 72–76 (2004).
  • Dore A, Santagata P, Dubuc M, Mercier LA. Implantable cardioverter defibrillators in adults with congenital heart disease: a single center experience. Pacing Clin. Electrophysiol.27, 47–51 (2004).
  • Yap SC, Roos-Hesselink JW, Hoendermis ES et al. Outcome of implantable cardioverter defibrillators in adults with congenital heart disease: a multi-centre study. Eur. Heart J.28, 1854–1861 (2007).
  • Sueblinvong V, Ovadia M. Defibrillator for primary prevention in congenital heart disease. Pacing Clin. Electrophysiol.27, 1167–1169 (2004).
  • Roos-Hesselink J, Perlroth MG, McGhie J, Spitaels S. Atrial arrhythmias in adults after repair of tetralogy of Fallot. Correlations with clinical, exercise, and echocardiographic findings. Circulation91, 2214–2219 (1995).
  • Puley G, Siu S, Connelly M et al. Arrhythmia and survival in patients >18 years of age after the mustard procedure for complete transposition of the great arteries. Am. J. Cardiol.83, 1080–1084 (1999).
  • Wathen MS, DeGroot PJ, Sweeney MO et al. Prospective randomized multicenter trial of empirical antitachycardia pacing versus shocks for spontaneous rapid ventricular tachycardia in patients with implantable cardioverter-defibrillators: Pacing Fast Ventricular Tachycardia Reduces Shock Therapies (PainFREE Rx II) trial results. Circulation110, 2591–2596 (2004).
  • Epstein AE, DiMarco JP, Ellenbogen KA et al. ACC/AHA/HRS 2008 Guidelines for Device-Based Therapy of Cardiac Rhythm Abnormalities: a report of the American College of Cardiology/American Heart Association Task Force on Practice Guidelines (Writing Committee to Revise the ACC/AHA/NASPE 2002 Guideline Update for Implantation of Cardiac Pacemakers and Antiarrhythmia Devices): developed in collaboration with the American Association for Thoracic Surgery and Society of Thoracic Surgeons. Circulation117, e350–e408 (2008).
  • Maron BJ, Shen WK, Link MS et al. Efficacy of implantable cardioverter-defibrillators for the prevention of sudden death in patients with hypertrophic cardiomyopathy. N. Engl. J. Med.342, 365–373 (2000).
  • Stephenson EA, Batra AS, Knilans TK et al. A multicenter experience with novel implantable cardioverter defibrillator configurations in the pediatric and congenital heart disease population. J. Cardiovasc. Electrophysiol.17, 41–46 (2006).
  • Kaltman JR, Gaynor JW, Rhodes LA et al. Subcutaneous array with active can implantable cardioverter defibrillator configuration: a follow-up study. Congenit. Heart Dis.2, 125–129 (2007).
  • Stefanelli CB, Bradley DJ, Leroy S, Dick M 2nd, Serwer GA, Fischbach PS. Implantable cardioverter defibrillator therapy for life-threatening arrhythmias in young patients. J. Interv. Cardiol. Electrophysiol.6, 235–244 (2002).
  • Korte T, Koditz H, Niehaus M, Paul T, Tebbenjohanns J. High incidence of appropriate and inappropriate ICD therapies in children and adolescents with implantable cardioverter defibrillator. Pacing Clin. Electrophysiol.27, 924–932 (2004).
  • Berul CI, Van Hare GF, Kertesz NJ et al. Results of a multicenter retrospective implantable cardioverter-defibrillator registry of pediatric and congenital heart disease patients. J. Am. Coll. Cardiol.51, 1685–1691 (2008).
  • DeMaso DR, Lauretti A, Spieth L et al. Psychosocial factors and quality of life in children and adolescents with implantable cardioverter-defibrillators. Am. J. Cardiol.93, 582–587 (2004).
  • Khairy P, Dore A, Poirier N et al. Risk stratification in surgically repaired tetralogy of Fallot. Expert Rev. Cardiovasc. Ther.7, 755–762 (2009).
  • Ellenbogen KA, Levine JH, Berger RD et al. Are implantable cardioverter defibrillator shocks a surrogate for sudden cardiac death in patients with nonischemic cardiomyopathy? Circulation113, 776–782 (2006).
  • Triedman JK. Implantable cardioverter defibrillator implantation guidelines based solely on left ventricular ejection fraction do not apply to adults with congenital heart disease. Circ. Arrhythmia Electrophysiol.1, 307–316 (2008).
  • Silka MJ, Bar-Cohen Y. Patients with congenital heart disease and a systemic ventricular ejection fraction less than 30% should undergo prophylactic implantation of an implantable cardioverter defibrillator. Circ. Arrhythmia Electrophysiol.1, 298–306 (2008).
  • Hallstrom A, Pratt CM, Greene HL et al. Relations between heart failure, ejection fraction, arrhythmia suppression and mortality: analysis of the Cardiac Arrhythmia Suppression Trial. J. Am. Coll. Cardiol.25, 1250–1257 (1995).
  • Huikuri HV, Makikallio TH, Raatikainen MJ, Perkiomaki J, Castellanos A, Myerburg RJ. Prediction of sudden cardiac death: appraisal of the studies and methods assessing the risk of sudden arrhythmic death. Circulation108, 110–115 (2003).
  • Cleland JG, Daubert JC, Erdmann E et al. The effect of cardiac resynchronization on morbidity and mortality in heart failure. N. Engl. J. Med.352, 1539–1549 (2005).
  • Uretsky BF, Thygesen K, Daubert JC et al. Predictors of mortality from pump failure and sudden cardiac death in patients with systolic heart failure and left ventricular dyssynchrony: results of the CARE-HF trial. J. Card. Fail.14, 670–675 (2008).
  • Strieper M, Karpawich P, Frias P et al. Initial experience with cardiac resynchronization therapy for ventricular dysfunction in young patients with surgically operated congenital heart disease. Am. J. Cardiol.94, 1352–1354 (2004).
  • Cecchin F, Frangini PA, Brown DW et al. Cardiac resynchronization therapy (and multisite pacing) in pediatrics and congenital heart disease: five years experience in a single institution. J. Cardiovasc. Electrophysiol.20, 58–65 (2009).
  • Kiesewetter C, Michael K, Morgan J, Veldtman GR. Left ventricular dysfunction after cardiac resynchronization therapy in congenital heart disease patients with a failing systemic right ventricle. Pacing Clin. Electrophysiol.31, 159–162 (2008).
  • Dubin AM, Janousek J, Rhee E et al. Resynchronization therapy in pediatric and congenital heart disease patients: an international multicenter study. J. Am. Coll. Cardiol.46, 2277–2283 (2005).
  • Kriebel T, Saul JP, Schneider H, Sigler M, Paul T. Noncontact mapping and radiofrequency catheter ablation of fast and hemodynamically unstable ventricular tachycardia after surgical repair of tetralogy of Fallot. J. Am. Coll. Cardiol.50, 2162–2168 (2007).
  • Gonska BD, Cao K, Raab J, Eigster G, Kreuzer H. Radiofrequency catheter ablation of right ventricular tachycardia late after repair of congenital heart defects. Circulation94, 1902–1908 (1996).
  • Furushima H, Chinushi M, Sugiura H et al. Ventricular tachycardia late after repair of congenital heart disease: efficacy of combination therapy with radiofrequency catheter ablation and class III antiarrhythmic agents and long-term outcome. J. Electrocardiol.39, 219–224 (2006).
  • Morwood JG, Triedman JK, Berul CI et al. Radiofrequency catheter ablation of ventricular tachycardia in children and young adults with congenital heart disease. Heart Rhythm1, 301–308 (2004).
  • Triedman JK, Alexander ME, Love BA et al. Influence of patient factors and ablative technologies on outcomes of radiofrequency ablation of intra-atrial re-entrant tachycardia in patients with congenital heart disease. J. Am. Coll. Cardiol.39, 1827–1835 (2002).
  • Triedman JK, Bergau DM, Saul JP, Epstein MR, Walsh EP. Efficacy of radiofrequency ablation for control of intraatrial reentrant tachycardia in patients with congenital heart disease. J. Am. Coll. Cardiol.30, 1032–1038 (1997).
  • Collins KK, Love BA, Walsh EP, Saul JP, Epstein MR, Triedman JK. Location of acutely successful radiofrequency catheter ablation of intraatrial reentrant tachycardia in patients with congenital heart disease. Am. J. Cardiol.86, 969–974 (2000).
  • Triedman JK, DeLucca JM, Alexander ME, Berul CI, Cecchin F, Walsh EP. Prospective trial of electroanatomically guided, irrigated catheter ablation of atrial tachycardia in patients with congenital heart disease. Heart Rhythm2, 700–705 (2005).
  • Reich JD, Auld D, Hulse E, Sullivan K, Campbell R. The Pediatric Radiofrequency Ablation Registry’s experience with Ebstein’s anomaly. Pediatric Electrophysiology Society. J. Cardiovasc. Electrophysiol.9, 1370–1377 (1998).
  • Chetaille P, Walsh EP, Triedman JK. Outcomes of radiofrequency catheter ablation of atrioventricular reciprocating tachycardia in patients with congenital heart disease. Heart Rhythm1, 168–173 (2004).
  • Chandar JS, Wolff GS, Garson A Jr et al. Ventricular arrhythmias in postoperative tetralogy of Fallot. Am. J. Cardiol.65, 655–661 (1990).
  • Jonsson H, Ivert T, Brodin LA, Jonasson R. Late sudden deaths after repair of tetralogy of Fallot. Electrocardiographic findings associated with survival. Scand J. Thorac. Cardiovasc. Surg.29, 131–139 (1995).
  • Dietl CA, Cazzaniga ME, Dubner SJ, Perez-Balino NA, Torres AR, Favaloro RG. Life-threatening arrhythmias and RV dysfunction after surgical repair of tetralogy of Fallot. Comparison between transventricular and transatrial approaches. Circulation90, II7–12 (1994).
  • Kammeraad JA, van Deurzen CH, Sreeram N et al. Predictors of sudden cardiac death after Mustard or Senning repair for transposition of the great arteries. J. Am. Coll. Cardiol.44, 1095–1102 (2004).
  • Katz NM, Blackstone EH, Kirklin JW, Pacifico AD, Bargeron LM, Jr. Late survival and symptoms after repair of tetralogy of Fallot. Circulation65, 403–410 (1982).
  • Russo G, Folino AF, Mazzotti E, Rebellato L, Daliento L. Comparison between QRS duration at standard ECG and signal-averaging ECG for arrhythmic risk stratification after surgical repair of tetralogy of Fallot. J. Cardiovasc. Electrophysiol.16, 288–292 (2005).
  • Chen D, Moller JH. Comparison of late clinical status between patients with different hemodynamic findings after repair of tetralogy of Fallot. Am. Heart J.113, 767–772 (1987).
  • Daliento L, Rizzoli G, Menti L, Baratella MC, Turrini P, Nava A, Dalla Volta S. Accuracy of electrocardiographic and echocardiographic indices in predicting life threatening ventricular arrhythmias in patients operated for tetralogy of Fallot. Heart81, 650–655 (1999).
  • Sarkar D, Bull C, Yates R et al. Comparison of long-term outcomes of atrial repair of simple transposition with implications for a late arterial switch strategy. Circulation100, II176–81 (1999).
  • Hokanson JS, Moller JH. Significance of early transient complete heart block as a predictor of sudden death late after operative correction of tetralogy of Fallot. Am. J. Cardiol.87, 1271–1277 (2001).
  • Gatzoulis MA, Till JA, Redington AN. Depolarization–repolarization inhomogeneity after repair of tetralogy of Fallot. The substrate for malignant ventricular tachycardia? Circulation95, 401–404 (1997).
  • Vogel M, Sponring J, Cullen S, Deanfield JE, Redington AN. Regional wall motion and abnormalities of electrical depolarization and repolarization in patients after surgical repair of tetralogy of Fallot. Circulation103, 1669–1673 (2001).
  • Lucron H, Marcon F, Bosser G, Lethor JP, Marie PY, Brembilla-Perrot B. Induction of sustained ventricular tachycardia after surgical repair of tetralogy of Fallot. Am. J. Cardiol.83, 1369–1373 (1999).

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