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Scandinavian Journal of Clinical and Laboratory Investigation Volume 29, 1972 - Issue 3
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Original Article

The Metabolism of L-Pyroglutamic Acid in Fibroblasts from a Patient with Pyroglutamic Aciduria: The Demonstration of an L-Pyroglutamate Hydrolase System

J. H. Strömme Institute of Clinical Biochemistry, University of Oslo, Rikshospitalet, Oslo, Norway
&
L. Eldjarn Institute of Clinical Biochemistry, University of Oslo, Rikshospitalet, Oslo, Norway
Pages 335-342 | Received 21 Dec 1971, Accepted 17 Feb 1972, Published online: 08 Jul 2009

References

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  • Eldjarn L., Jellum E., Stokke O. Pyroglutamic aciduria: Demonstration of the enzyme defect and studies of the metabolic origin of pyroglutamic acid. Clin. chim. Acta., In press
  • Eldjarn L., Stokke O., Jellum E. Pyroglutamic aciduria. A new inborn error of metabolism possibly localized to the ‘γ-glutamyl cycle’ proposed for amino acid transport. SSIEM Symp. No 9, Leeds 1971. Churchill Livingstone, Edinburgh-London, In press
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