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Review

New concepts for the treatment of pediatric nonrhabdomyosarcoma soft tissue sarcomas

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Pages 307-318 | Published online: 10 Jan 2014

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Read on this site (9)

Giacomo G. Baldi, Daniel Orbach, Rossella Bertulli, Chiara Magni, Giovanna Sironi, Michela Casanova & Andrea Ferrari. (2019) Standard treatment and emerging drugs for managing synovial sarcoma: adult’s and pediatric oncologist perspective. Expert Opinion on Emerging Drugs 24:1, pages 43-53.
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Andrea Ferrari, Stefano Chiaravalli, Michela Casanova, Patrizia Gasparini, Nadège Corradini & Daniel Orbach. (2015) Considering chemotherapy in synovial sarcoma. Expert Opinion on Orphan Drugs 3:10, pages 1111-1124.
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Gianni Bisogno, Andrea Ferrari, Rita Alaggio & Daniel Orbach. (2014) Treatment options for alveolar soft part sarcoma in pediatric patients. Expert Opinion on Orphan Drugs 2:6, pages 579-589.
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Andrea Ferrari, Rita Alaggio, Cristina Meazza, Stefano Chiaravalli, Marco Vajna de Pava, Michela Casanova, Elena Cavaliere & Gianni Bisogno. (2013) Fibroblastic tumors of intermediate malignancy in childhood. Expert Review of Anticancer Therapy 13:2, pages 225-236.
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Andrea Ferrari, Gianni Bisogno, Cristina Meazza, Marco Vajna de Pava, Iyad Sultan, Gian Luca De Salvo, Carlo Alfredo Clerici, Laura Veneroni & Michela Casanova. (2012) The challenge of access to care for soft tissue sarcomas bridging pediatric and adult age: the Italian pediatric oncology view. Expert Review of Anticancer Therapy 12:2, pages 243-254.
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Michela Casanova & Andrea Ferrari. (2011) Pharmacotherapy for pediatric soft-tissue sarcomas. Expert Opinion on Pharmacotherapy 12:4, pages 517-531.
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Andrea Ferrari, Michela Casanova, Maura Massimino & Iyad Sultan. (2010) Peculiar features and tailored management of adult cancers occurring in pediatric age. Expert Review of Anticancer Therapy 10:11, pages 1837-1851.
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Andrea Ferrari. (2009) Harmonizing adult and pediatric approaches to the treatment of soft-tissue sarcoma. Expert Review of Anticancer Therapy 9:11, pages 1541-1543.
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Andrea Ferrari. (2008) Role of chemotherapy in pediatric nonrhabdomyosarcoma soft-tissue sarcomas. Expert Review of Anticancer Therapy 8:6, pages 929-938.
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Articles from other publishers (57)

Markus Weber, Frederik von KunowAxel Hillmann. (2023) Marginal resection as a potential curative treatment option of infantile fibrosarcoma with good response after chemotherapy: A case report of an ETV6-NTRK3 positive infantile fibrosacroma of the distal tibia. Medicine 102:27, pages e34194.
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Elysia Alvarez, Jiayi He, Sheri L. Spunt, Andrea Hayes-Jordan, Simon C. Kao, David M. Parham, Lynn Million, Aaron R. Weiss & Donald A. Barkauskas. (2023) Lymph node metastases in paediatric and young adult patients with non-rhabdomyosarcoma soft tissue sarcoma (NRSTS): Findings from Children's Oncology Group (COG) study ARST0332. European Journal of Cancer 180, pages 89-98.
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Stefan M. Pfister, Miguel Reyes-Múgica, John K.C. Chan, Henrik Hasle, Alexander J. Lazar, Sabrina Rossi, Andrea Ferrari, Jason A. Jarzembowski, Kathy Pritchard-Jones, D. Ashley Hill, Thomas S. Jacques, Pieter Wesseling, Dolores H. López Terrada, Andreas von Deimling, Christian P. Kratz, Ian A. Cree & Rita Alaggio. (2022) A Summary of the Inaugural WHO Classification of Pediatric Tumors: Transitioning from the Optical into the Molecular Era. Cancer Discovery 12:2, pages 331-355.
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Andrea Ferrari & Rita Alaggio. 2022. Rare Tumors in Children and Adolescents. Rare Tumors in Children and Adolescents 535 582 .
E. Rossetti, G. Gonzalez Diaz, J. Lopez Marti, S. Innocenti, W. Cacciavillano, G. Felizzia, M. Viso, M.L. Ramos, P. Zubizarreta & A. Rose. (2021) Synovial sarcoma in children: A 15-YEAR experience at a tertiary pediatric center in Argentina. Pediatric Hematology Oncology Journal 6:4, pages 175-185.
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Andrea A. Hayes-Jordan & Valerae O. Lewis. 2021. Pediatric Surgery. Pediatric Surgery 971 987 .
Daniel Orbach, Sheri L. Spunt & Andrea Ferrari. 2021. Sarcomas of Bone and Soft Tissues in Children and Adolescents. Sarcomas of Bone and Soft Tissues in Children and Adolescents 65 85 .
Yasir Khan, Richard Carey‐Smith, Mandy Taylor, Jennifer Woodhouse, Angela Jacques, David Wood & Anne Long. (2020) Treatment and outcomes for synovial sarcoma patients in Western Australia: the role of neoadjuvant chemoradiotherapy. Cancer Reports 3:6.
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Andrea A. Hayes-Jordan & Valerae O. Lewis. 2020. Pediatric Surgery. Pediatric Surgery 1 17 .
Arpanna Singh, Hariom Singh, Dipanshu Kumar, Aparna Singh & Biranchi Narayan Biswal. (2019) Intraoral Soft Tissue Fibrosarcoma in a Four-Year-Old Child: An Unusual Case Report. Journal of Clinical Pediatric Dentistry 43:6, pages 408-412.
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Patrizia Gasparini, Orazio Fortunato, Loris De Cecco, Michela Casanova, Maria Federica Iannó, Andrea Carenzo, Giovanni Centonze, Massimo Milione, Paola Collini, Mattia Boeri, Matteo Dugo, Chiara Gargiuli, Mavis Mensah, Miriam Segale, Luca Bergamaschi, Stefano Chiaravalli, Maria Luisa Sensi, Maura Massimino, Gabriella Sozzi & Andrea Ferrari. (2019) Age-Related Alterations in Immune Contexture Are Associated with Aggressiveness in Rhabdomyosarcoma. Cancers 11:9, pages 1380.
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Andrea Ferrari, Archie Bleyer, Shreyaskumar Patel, Stefano Chiaravalli, Patrizia Gasparini & Michela Casanova. (2018) The challenge of the management of adolescents and young adults with soft tissue sarcomas. Pediatric Blood & Cancer 65:7.
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Sameer Farouk Sait, Enrico Danzer, Daniel Ramirez, Michael P. LaQuaglia & Meyers Paul. (2018) Spontaneous Regression in a Patient With Infantile Fibrosarcoma. Journal of Pediatric Hematology/Oncology 40:4, pages e253-e255.
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Christina L. Boull & Sheilagh M. Maguiness. 2018. Skin Tumors and Reactions to Cancer Therapy in Children. Skin Tumors and Reactions to Cancer Therapy in Children 81 99 .
Christopher L. Tinkle, Israel Fernandez-Pineda, April Sykes, Zhaohua Lu, Chia-ho Hua, Michael D. Neel, Armita Bahrami, Barry L. Shulkin, Sue C. Kaste, Alberto Pappo, Sheri L. Spunt & Matthew J. Krasin. (2017) Nonrhabdomyosarcoma soft tissue sarcoma (NRSTS) in pediatric and young adult patients: Results from a prospective study using limited-margin radiotherapy. Cancer 123:22, pages 4419-4429.
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Vincenza Rita Lo Vasco, Martina Leopizzi, Anna Scotto d’Abusco & Carlo Della Rocca. (2017) Different Expression and Localization of Phosphoinositide Specific Phospholipases C in Human Osteoblasts, Osteosarcoma Cell Lines, Ewing Sarcoma and Synovial Sarcoma. Avicenna Journal of Medical Biochemistry 5:1, pages 1-8.
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Winette T A van der Graaf, Daniel Orbach, Ian R Judson & Andrea Ferrari. (2017) Soft tissue sarcomas in adolescents and young adults: a comparison with their paediatric and adult counterparts. The Lancet Oncology 18:3, pages e166-e175.
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Andrea Ferrari, Michela Casanova & Paola Collini. 2017. Encyclopedia of Cancer. Encyclopedia of Cancer 3121 3129 .
Andrea Ferrari, Shreyaskumar R. Patel, Jay Wunder & Karen H. Albritton. 2017. Cancer in Adolescents and Young Adults. Cancer in Adolescents and Young Adults 383 416 .
Yassine Eid, Claire Dupont-Lucas, Daniel Orbach, Philippe Ravasse & Julien Rod. (2017) Synovial sarcoma presenting as colonic intussusception in a child. Pediatric Blood & Cancer 64:1, pages 207-208.
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Ivan J. Golub, Roberto A. Garcia & James C. Wittig. (2016) A 15-Year-Old Male Baseball Player With a Mass in the Brachialis Muscle. Orthopedics 39:3.
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Ludovic Mansuy, Valérie Bernier, Dominique Ranchère-Vince, Laurence Mainard, Daniel Orbach & Nadège Corradini. (2016) Les synovialosarcomes de l’enfant et l’adolescent. Bulletin du Cancer 103:2, pages 210-218.
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Susanne A. Gatz, Khin Thway, Henry Mandeville, Cyrus Kerawala, David MacVicar & Julia Chisholm. (2015) Chemotherapy responsiveness in a patient with multiply relapsed ameloblastic fibro‐odontosarcoma of the maxilla. Pediatric Blood & Cancer 62:11, pages 2029-2032.
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A. Ferrari, G.L. De Salvo, B. Brennan, M.M. van Noesel, A. De Paoli, M. Casanova, N. Francotte, A. Kelsey, R. Alaggio, O. Oberlin, M. Carli, M. Ben-Arush, C. Bergeron, J.H.M. Merks, M. Jenney, M.C. Stevens, G. Bisogno & D. Orbach. (2015) Synovial sarcoma in children and adolescents: the European Pediatric Soft Tissue Sarcoma Study Group prospective trial (EpSSG NRSTS 2005). Annals of Oncology 26:3, pages 567-572.
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Frederick Soole, Carole Maupain, Anne-Sophie Defachelles, Sophie Taque, Veronique Minard-Colin, Christophe Bergeron, Yann De Rycke & Daniel Orbach. (2014) Synovial sarcoma relapses in children and adolescents: Prognostic factors, treatment, and outcome. Pediatric Blood & Cancer 61:8, pages 1387-1393.
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Anna Kerouanton, Irene Jimenez, Cecile Cellier, Valerie Laurence, Sylvie Helfre, Stephanie Pannier, Pierre Mary, Paul Freneaux & Daniel Orbach. (2014) Synovial Sarcoma in Children and Adolescents. Journal of Pediatric Hematology/Oncology 36:4, pages 257-262.
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Andrea Ferrari, Michela Casanova & Paola Collini. 2016. Encyclopedia of Cancer. Encyclopedia of Cancer 1 10 .
Iyad Sultan, Roberta Ortiz & Andrea Ferrari. 2014. Pediatric Hematology-Oncology in Countries with Limited Resources. Pediatric Hematology-Oncology in Countries with Limited Resources 303 322 .
D. Orbach, B. Brennan, M. Casanova, C. Bergeron, V. Mosseri, N. Francotte, M. Van Noesel, A. Rey, G. Bisogno, G. Pierron & A. Ferrari. (2013) Paediatric and adolescent alveolar soft part sarcoma: A joint series from European cooperative groups. Pediatric Blood & Cancer 60:11, pages 1826-1832.
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Andrea Ferrari & Michela Casanova. (2013) Relapse in synovial sarcoma: what can be done for poor outcomes?. Clinical Practice 10:4, pages 389-391.
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Francesco Peia, Marco Gessi, Paola Collini, Andrea Ferrari, Alessandra ErbettaLaura G. Valentini. (2013) Pediatric primitive intraneural synovial sarcoma of L-5 nerve root. Journal of Neurosurgery: Pediatrics 11:4, pages 473-477.
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Andrea Ferrari, Gian Luca De Salvo, Patrizia Dall’Igna, Cristina Meazza, Francesco De Leonardis, Carla Manzitti, Maria Antonietta de Ioris, Michela Casanova, Modesto Carli & Gianni Bisogno. (2012) Salvage rates and prognostic factors after relapse in children and adolescents with initially localised synovial sarcoma. European Journal of Cancer 48:18, pages 3448-3455.
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Andrea Ferrari, Daniel Orbach, Iyad Sultan, Michela Casanova & Gianni Bisogno. (2012) Neonatal soft tissue sarcomas. Seminars in Fetal and Neonatal Medicine 17:4, pages 231-238.
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Iacopo Sardi, Maura Massimino, Lorenzo Genitori, Anna Maria Buccoliero, Felice Giangaspero & Andrea Ferrari. (2010) Intracranial mesenchymal chondrosarcoma: Report of two pediatric cases. Pediatric Blood & Cancer 56:4, pages 685-686.
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Michael C. Cheung, Ying Zhuge, Relin Yang, Michael P. Ogilvie, Leonidas G. Koniaris, Maria M. Rodríguez & Juan E. Sola. (2010) Incidence and Outcomes of Extremity Soft-Tissue Sarcomas in Children. Journal of Surgical Research 163:2, pages 282-289.
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Daniel OrbachAnnie ReyGiovanni CecchettoOdile OberlinMichela CasanovaEstelle ThebaudMarcelo ScopinaroGianni BisognoModesto CarliAndrea Ferrari. (2010) Infantile Fibrosarcoma: Management Based on the European Experience. Journal of Clinical Oncology 28:2, pages 318-323.
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Francesca Favini, Iyad Sultan, Cristina Meazza, Michela Casanova & Andrea Ferrari. (2009) Prognostic role of tumor size in childhood cancer. Future Oncology 5:10, pages 1605-1613.
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Melinda S. Merchant & Crystal L. Mackall. (2009) Current Approach to Pediatric Soft Tissue Sarcomas. The Oncologist 14:11, pages 1139-1153.
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Hatem Soliman, Andrea Ferrari & David Thomas. (2009) Sarcoma in the Young Adult Population: An International View. Seminars in Oncology 36:3, pages 227-236.
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Federico Antillon, Mauricio Castellanos, Patricia Valverde, Sandra Luna‐Fineman, Claudia Garrido, Tania Serrato, Carlos Rodriguez‐Galindo, Michela Casanova & Andrea Ferrari. (2008) Treating Pediatric soft tissue sarcomas in a country with limited resources: The experience of the Unidad Nacional de Oncologia Pediatrica in Guatemala. Pediatric Blood & Cancer 51:6, pages 760-764.
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P.-U. Tunn, D. Andreou, H. Illing, B. Fleige, S. Dresel & P.M. Schlag. (2008) Sentinel node biopsy in synovial sarcoma. European Journal of Surgical Oncology (EJSO) 34:6, pages 704-707.
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Andrea Ferrari, Gianni Bisogno, Rita Alaggio, Giovanni Cecchetto, Paola Collini, Angelo Rosolen, Cristina Meazza, Paolo Indolfi, Alberto Garaventa, Luigi De Sio, Paolo D’Angelo, Paolo Tamaro, Michela Casanova & Modesto Carli. (2008) Synovial sarcoma of children and adolescents: The prognostic role of axial sites. European Journal of Cancer 44:9, pages 1202-1209.
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Francisco Luis San Miguel, William Spurbeck, Carlos Budding & John Horton. (2008) Kaposiform hemangioendothelioma: a rare cause of spontaneous hemothorax in infancy. Review of the literature. Journal of Pediatric Surgery 43:1, pages e37-e41.
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Ravi S. Radhakrishnan & Richard J. Andrassy. 2008. Reoperative Pediatric Surgery. Reoperative Pediatric Surgery 447 457 .
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Andrea Ferrari, Rosalba Miceli, Michela Casanova, Alessandro Gronchi, Paola Collini, Cristina Meazza, Elena Zaffignani, Maura Massimino, Filippo Spreafico & Luigi Mariani. (2007) Adult-type soft tissue sarcomas in paediatric age: A nomogram-based prognostic comparison with adult sarcoma. European Journal of Cancer 43:18, pages 2691-2697.
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Michela Casanova, Cristina Meazza, Alessandro Gronchi, Marco Fiore, Elena Zaffignani, Marta Podda, Paola Collini, Lorenza Gandola & Andrea Ferrari. (2007) Soft-tissue sarcomas of the extremities in patients of pediatric age. Journal of Children's Orthopaedics 1:3, pages 195-203.
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Andrea Ferrari, Gianni Bisogno & Modesto Carli. (2007) Management of Childhood Malignant Peripheral Nerve Sheath Tumor. Pediatric Drugs 9:4, pages 239-248.
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Andrea Ferrari & Michela Casanova. (2006) Specification on the Definition of Adult-Type Soft Tissue Sarcoma. Journal of Clinical Oncology 24:24, pages 4042-4043.
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Michela Casanova, Andrea Ferrari, Paola Collini, Gianni Bisogno, Rita Alaggio, Giovanni Cecchetto, Alessandro Gronchi, Cristina Meazza, Alberto Garaventa, Andrea Di Cataldo & Modesto Carli. (2005) Epithelioid sarcoma in children and adolescents. Cancer 106:3, pages 708-717.
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Modesto CarliAndrea FerrariAdrian MattkeIlaria ZanettiMichela CasanovaGianni BisognoGiovanni CecchettoRita AlaggioLuigi De SioEura KoscielniakGuido SottiJoern Treuner. (2005) Pediatric Malignant Peripheral Nerve Sheath Tumor: The Italian and German Soft Tissue Sarcoma Cooperative Group. Journal of Clinical Oncology 23:33, pages 8422-8430.
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