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Expert Review of Clinical Immunology Volume 12, 2016 - Issue 2
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Reviews

Risk factors for severity and manifestations in systemic sclerosis and prediction of disease course

Mike O. BeckerDepartment of Rheumatology and Clinical Immunology, University Hospital Charité Berlin, Berlin, GermanyCorrespondence[email protected]
&
Gabriela RiemekastenDepartment of Rheumatology, University Hospital Lübeck, Lübeck, Germany
Pages 115-135 | Received 29 Mar 2015, Accepted 30 Oct 2015, Published online: 02 Dec 2015

References

  • Papers of special note have been highlighted as:
  • • of interest
  • •• of considerable interest
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•• Important study identifying factors associated with the development of systemic sclerosis.

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•• New diagnostic criteria for systemic sclerosis.

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•• Describes the large data set of the European systemic sclerosis study group EUSTAR

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•• Staging of interstitial lung disease in systemic sclerosis (SSc) with lung function parameters and extent of fibrosis on high-resolution computed tomography allows for risk stratification.

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• Screening in SSc-pulmonary arterial hypertension (PAH) improves survival.

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