Audiological profiling of 198 individuals with auditory neuropathy spectrum disorder

References

• Berlin CI, Hood LJ, Morlet T, Wilensky D, Li L, Mattingly KR, et al. Multi-site diagnosis and management of 260 patients with auditory neuropathy/dys-synchrony (auditory neuropathy spectrum disorder). Int J Audiol. 2010;49:30–43.
   PubMed Web of Science ®Google Scholar
• Foerst A, Beutner D, Lang-Roth R, Huttenbrink KB, von Wedel H, Walger M, et al. Prevalence of auditory neuropathy/synaptopathy in a population of children with profound hearing loss. Int J Pediatr Otorhinolaryngol. 2006;70:1415–22.
   PubMed Web of Science ®Google Scholar
• Berlin CI, Hood LJ, Morlet T, Den Z, Goforth L, Tedesco H, et al. The search for auditory neuropathy patients and connexin 26 patients in schools for the deaf. ARO Abstracts. 2000;23:23.
   Google Scholar
• Lee JSM, McPherson B, Yuen KCP, Wong LLN. Screening for auditory neuropathy in a school for hearing impaired children. Int J Pediatr Otorhinolaryngol. 2001;61:39–46.
   PubMed Web of Science ®Google Scholar
• Cheng X, Li L, Brashears S, Morlet T, Ng SS, Berlin CI, et al. Connexin 26 variants and auditory neuropathy/dys-synchrony among children in schools for the deaf. Am J Med Genet. 2005;139:13–8.
   PubMed Web of Science ®Google Scholar
• Sininger YS. Identification of auditory neuropathy in infants and children. Semin Hear. 2002;23:193–200.
   Google Scholar
• Rea PA, Gibson WPR. Evidence for surviving outer hair cell function in congenitally deaf ears. Laryngoscope. 2003; 113:230–4.
   Web of Science ®Google Scholar
• Sininger YS, Oba S. Patients with auditory neuropathy: who are they and what can they hear? In: Sininger YS, Starr A, editors. Auditory Neuropathy: A New Perspective on Hearing Disorders. San Diego: Singular; 2001. p. 15–35.
   Google Scholar
• Kumar AU, Jayaram M. Prevalence and audiological characteristics in individuals with auditory neuropathy/ dys-synchrony. Int J Audiol. 2006;45:360–6.
   PubMed Web of Science ®Google Scholar
• Starr A, Sininger Y, Pratt H. The varieties of auditory neuropathy. J Basic Clin Pharmacol. 2000;11:215–30.
   Google Scholar
• Prabhu P, Avilala VKY, Manjula P. Predisposing factors in individuals with late-onset auditory dys-synchrony. Asia Pacif J Speech Lang Hear. 2012;15:41–50.
   Google Scholar
• Starr A, Picton TW, Kim R. Pathophysiology of auditory neuropathy. In: Sininger Y, Starr A, editors. Auditory neuropathy: a new perspective on hearing disorder. Canada: Singular Publishing Group; 2001. p. 67–82.
   Google Scholar
• Zeng FG, Oba S, Garde S, Sininger Y, Starr A. Temporal and speech processing deficits in auditory neuropathy. NeuroReport. 1999;10:3429–35.
   PubMed Web of Science ®Google Scholar
• Kraus N, Bradlow AR, Cheatham MA, Cunningham J, King CD, Koch CD. Consequences of neural asynchrony: a case of auditory neuropathy. J Assoc Res Otolaryngol. 2000; 1:33–45.
   PubMed Web of Science ®Google Scholar
• Rance G, McKay C, Grayden D. Perceptual characterization of children with auditory neuropathy. Ear Hear. 2004;25:34–46.
   PubMed Web of Science ®Google Scholar
• Rance G, Beer DE, Cone-Wesson B, Shepherd RK, Dowell RC, King AM, et al. Clinical findings for a group of infants and young children with auditory neuropathy. Ear Hear. 1999;20:238–52.
   PubMed Web of Science ®Google Scholar
• Berlin CI, Hood LJ, Hurely A, Wen H. Hearing aids: only for hearing impaired patients with abnormal otoacoustic emissions. In: Berlin CI, editor. Hair cells and hearing aids. San Diego: Singular Publishing Group; 1996. p. 99–111.
   Google Scholar
• Berlin C, Hood L, Morlet T, Rose K, Brashears S. Auditory Neuropathy/Dys-synchrony: Diagnosis and Management. Ment Retard Dev Disabil Res Rev. 2003;9:225–31.
   PubMedGoogle Scholar
• Starr A, Picton TW, Sininger Y, Hood LJ, Berlin CI. Auditory neuropathy. Brain. 1996;119:741–53.
   PubMed Web of Science ®Google Scholar
• Rance G, Barker EJ. Speech perception in children with auditory neuropathy/dys-synchrony managed with either hearing aids or cochlear implants. Otol Neurotol. 2008;29:179–82.
   PubMed Web of Science ®Google Scholar
• Rance G, Cone-Wesson B, Wunderlich J, Dowell R. Speech perception and cortical event related potentials in children with auditory neuropathy. Ear Hear. 2002;23:239–53.
   PubMed Web of Science ®Google Scholar
• Mason J, Michele A, Stevens C, Ruth R, Hashisaki G. Cochlear Implantation in Patients with Auditory Neuropathy of Varied Etiologies. The Laryngoscope. 2003;113:45–9.
   PubMed Web of Science ®Google Scholar
• Shallop J. Auditory Neuropathy/Dys-Synchrony in Adults and Children. Semin Hear. 2002;23:215–23.
   Google Scholar
• Narne VK, Vanaja CS. Effect of envelope enhancement on speech perception in individuals with auditory neuropathy. Ear Hear. 2008;29:45–53.
   PubMed Web of Science ®Google Scholar
• Vanaja CS, Manjula P. LLR as a measure of benefit derived from hearing devices with auditory dys-synchrony. In: Shivashanker N, Shashikala HR, editors. In: First conference on Auditory Neuropathy. Bangalore: Department of Speech Pathology and Audiology, National Institute of Mental Health and Neurosciences. 2004;136–46.
   Google Scholar
• Carhart R, Jerger JF. Preferred method for clinical determination of pure tone thresholds. J Speech Hear Disord. 1959; 24:330–45.
   Google Scholar
• Yathiraj A, Vijayalakshmi CS. Phonemically Balanced Word List in Kannada. Developed in Department of Audiology, All India Institute of Speech and Hearing, Mysore, 2005.
   Google Scholar
• Mayadevi 1974. The development and standardization of a common speech discrimination test for Indians. Unpublished dissertation submitted to University of Mysore, in part fulfillment of Masters Degree in Speech and Hearing, 1974.
   Google Scholar
• Podwall A, Podwall D, Gordon TG, Lamendola P, Gold AP. Unilateral auditory neuropathy: case study. J Child Neurol. 2002;17:306–9.
   PubMed Web of Science ®Google Scholar
• Konrádsson KS. Bilaterally, preserved otoacoustic emissions in four children with profound idiopathic unilateral sensorineural hearing loss. Audiology. 1996;35:217–27.
   PubMedGoogle Scholar
• Deltenre P, Mansbach AL, Bozet C, Christiaens F, Barthelemy P, Paulissen D, et al. Auditory neuropathy with preserved cochlear microphonics and secondary loss of otoacoustic emissions. Audiology. 1999;38:187–95.
   PubMed Web of Science ®Google Scholar
• Rance G. Auditory neuropathy/dys-synchrony and its perceptual consequences. Trends Amplif. 2005;9:1–43.
   PubMedGoogle Scholar
• Prieve BA, Gorga MP, Neely ST. Otoacoustic emissions in an adult with severe hearing loss. J Speech Hear Res. 1991;31:379–85.
   Google Scholar
• Starr A, Zeng FG, Michalewski HJ, Moser T. Perspectives on auditory neuropathy: disorders of inner hair cell, auditory nerve, and their synapse. In: Basbaum AI, Kaneko A, Shepherd GM, Westheimer G, editors. The Senses: A Comprehensive Reference. Dallos P, Oertel D, eds. Vol 3: Audition. San Diego: Academic Press; 2008. p. 397–412.
   Google Scholar
• Amatuzzi MG, Northrop C, Liberman MC, Thornton A, Halpin C, Herrmann B, et al. Selective inner hair cell loss in premature infants and cochlea pathological patterns from neonatal intensive care unit autopsies. Arch Otolaryngol Head Neck Surg. 2001;127:629–36.
   PubMedGoogle Scholar
• Sek A, Moore BCJ. Frequency discrimination as a function of frequency measured in several ways. J Acoust Soc Am. 1995;97:2479–86.
   PubMed Web of Science ®Google Scholar
• Zeng FG, Kong YY, Michaleski HJ, Starr A. Perceptual consequences of disrupted auditory nerve activity. J Neurophysiol. 2005;93:3050–63.
   PubMed Web of Science ®Google Scholar
• Rance G, Ryan MM, Carew P, Corben A, Yiu E, Tana J, et al. Binaural speech processing in individuals with auditory neuropathy. Neuroscience. 2012;226;227–35.
   PubMed Web of Science ®Google Scholar
• Michalewski HJ, Starr A, Zeng FG, Dimitrijevic A. N100 cortical potentials accompanying disrupted auditory nerve activity in auditory neuropathy (AN): effects of signal intensity and continuous noise. Clin Neurophysiol. 2009;120:1352–63.
   PubMed Web of Science ®Google Scholar
• Lee JSM, McPherson B, Yuen KCP, Wong LLN. Screening for auditory neuropathy in a school for hearing impaired children. Int J Pediatr Otorhinolaryngol. 2001;61:39–46.
   PubMed Web of Science ®Google Scholar
• Javel E. Basic response properties of auditory nerve fibres. In: Altschuler RA, Bobbin RP, Hoffman DP, editors. Neurobiology of hearing: the cochlea. New York: Raven; 1986. p. 213–46.
   Google Scholar