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Review

Update and new approaches in the treatment of Castleman disease

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Pages 145-158 | Published online: 03 Aug 2016

Keep up to date with the latest research on this topic with citation updates for this article.

Read on this site (3)

Alexander S. Fein, Humberto E. Trejo Bittar, Manisha R. Shende, Ernest M. Scalzetti & Melissa W. Ko. (2019) Castleman Disease Presenting with Pseudotumour Cerebri and Myasthenia Gravis: A Case Report and Literature Review . Neuro-Ophthalmology 43:3, pages 185-191.
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Jenna Sitenga, Gregory Aird, Aabra Ahmed & Peter T Silberstein. (2018) Impact of siltuximab on patient-related outcomes in multicentric Castleman’s disease. Patient Related Outcome Measures 9, pages 35-41.
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Dan Yang, Xuan Zhou, Youcai Zhao, Shibin Cao, Ailing Su, Xuezhong Zhang, Yanli Xu & Xiuqun Zhang. (2018) A rare case of multicentric castleman's disease transforms into multiple myeloma and its successful treatment. Cancer Biology & Therapy 19:11, pages 949-952.
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Articles from other publishers (55)

Hao Yu, Yuepeng Wang, Yijun Li, Jin Du, Qinghua Guo, Weijun Gu, Zhaohui Lyu, Jingtao Dou, Yiming Mu & Li Zang. (2023) Analysis of characteristics of four patients with adrenal unicentric Castleman disease. Frontiers in Endocrinology 14.
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Galal El‐Enany, Medhat El‐Mofty, Mona R.E. Abdel‐Halim, Dip Dermpath, Noha Nagui, Hanan Nada, Marwah Adly Saleh, Iman Sany, Ahmad Nada, Omar El‐Ghanam, Lobna Gamal Alieldin & Heba Ahmed Abdelkader. (2022) Postpartum Castleman disease presenting as paraneoplastic pemphigus: a case report. International Journal of Dermatology 62:3.
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David T Khalil & Kellee Slater. (2022) Castleman Disease Mimicking Pancreatic Neuroendocrine Tumour: Interpretation of Positron Emission Tomography in Pancreatic Incidentaloma. Cureus.
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Gi-June Min, Young-Woo Jeon, Tong Yoon Kim, Dae Hun Kwag, Jong Hyuk Lee, Joon Yeop Lee, Sung-Soo Park, Silvia Park, Jae-Ho Yoon, Sung-Eun Lee, Byung-Sik Cho, Ki-Seong Eom, Yoo-Jin Kim, Seok Lee, Hee-Je Kim, Chang-Ki Min, Jong Wook Lee & Seok-Goo Cho. (2022) Long-term treatment outcome of Castleman’s disease: A real-world experience. Frontiers in Oncology 12.
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Fumihiro Shoji, Ken Takase, Yuka Kozuma, Koji Yamazaki, Shigeto Kawauchi & Sadanori Takeo. (2022) Induction immunotherapy followed by surgery for hilar unicentric Castleman disease. Thoracic Cancer 13:11, pages 1722-1725.
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F. Din, F. Mellor, T. Millard, E. Pace, N. Khan, A.D. Attygalle, D. Cunningham, S. Zafar & B. Sharma. (2022) Radiology of Castleman disease: the pivotal role of imaging in diagnosis, staging, and response assessment of this rare entity. Clinical Radiology 77:6, pages 399-408.
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Dafydd J. Jones, Matthew Marino & Robert Bohmer. (2021) Castleman's disease: A rare cause for a symptomatic retroperitoneal mass. ANZ Journal of Surgery 92:3, pages 555-556.
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Eren Gündüz, Hakkı Onur Kırkızlar, Elif Gülsüm Ümit, Sedanur Karaman Gülsaran, Vildan Özkocaman, Fahir Özkalemkaş, Ömer Candar, Tuğrul Elverdi, Selin Küçükyurt, Semra Paydaş, Özcan Ceneli, Sema Karakuş, Senem Maral, Ömer Ekinci, Yıldız İpek, Cem Kis, Zeynep Tuğba Güven, Aydan Akdeniz, Tiraje Celkan, Ayşe Hilal Eroğlu Küçükdiler, Gülsüm Akgün Çağlıyan, Ceyda Özçelik Şengöz, Ayse Karataş, Tuba Bulduk & Alper Özcan. (2022) Castleman Disease: A Multicenter Case Series from Turkey. Turkish Journal of Hematology.
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Christian Zanza, Tatsiana Romenskaya, Alice Chiara Manetti, Francesco Franceschi, Raffaele La Russa, Giuseppe Bertozzi, Aniello Maiese, Gabriele Savioli, Gianpietro Volonnino & Yaroslava Longhitano. (2022) Cytokine Storm in COVID-19: Immunopathogenesis and Therapy. Medicina 58:2, pages 144.
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Neeraja Swaminathan, Scott M. Lieberman, Sharathkumar Bhagavathi & Anjali Sharathkumar. (2021) Iron-Refractory Iron Deficiency Anemia in an 11-year-old Girl. Pediatrics In Review 42:7, pages 393-398.
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Kyle Pribyl, Victor Vakayil, Najiha Farooqi, Nivedita Arora, Benjamin Kreitz, Salman Ikramuddin, Michael A. Linden & James Harmon. (2021) Castleman disease: A single-center case series. International Journal of Surgery Case Reports 80, pages 105650.
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Wenda Wang, Dexin Dong, Jin Wen & Hanzhong Li. (2021) A 10-year observational single-center study of retroperitoneal unicentric Castleman disease. Medicine 100:10, pages e25088.
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Kristin B. Highland & Augustine S. Lee. 2021. Diffuse Cystic Lung Diseases. Diffuse Cystic Lung Diseases 161 177 .
Frits van Rhee, Eric Oksenhendler, Gordan SrkalovicPeter VoorheesMegan LimAngela Dispenzieri, Makoto IdeSophia ParenteStephen ScheyMatthew StreetlyRaymond WongDavid WuIvan MaillardJoshua BrandstadterNikhil MunshiWilbur BowneKojo S. Elenitoba-JohnsonAlexander FössaMary Jo LechowiczShanmuganathan ChandrakasanSheila K. PiersonAmy GreenwaySunita NastaKazuyuki YoshizakiRazelle Kurzrock, Thomas S. UldrickCorey Casper, Amy Chadburn & David C. Fajgenbaum. (2020) International evidence-based consensus diagnostic and treatment guidelines for unicentric Castleman disease. Blood Advances 4:23, pages 6039-6050.
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Nicoleta Iftode, Mihaela Andreea Rădulescu, Ștefan Sorin Aramă & Victoria Aramă. (2020) Update on Kaposi sarcoma-associated herpesvirus (KSHV or HHV8) – review. Romanian Journal of Internal Medicine 58:4, pages 199-208.
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Abhishek Aher, Trishang Udhwani, Ravina Khandelwal, Akanksha Limaye, Tajamul Hussain, Anuraj Nayarisseri & Sanjeev Kumar Singh. (2020) In silico Insights on IL-6: A Potential Target for Multicentric Castleman Disease. Current Computer-Aided Drug Design 16:5, pages 641-653.
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Anabela Salgueiro Marque, Carolina Sequeira & Paula Antunes. (2020) Valganciclovir in an HIV-infected patient with Castleman's disease. Medicina Clínica 155:8, pages 369-370.
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Anabela Salgueiro Marque, Carolina Sequeira & Paula Antunes. (2020) Valganciclovir in an HIV-infected patient with Castleman's disease. Medicina Clínica (English Edition) 155:8, pages 369-370.
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Margarida R. Fonseca, Miguel Oliva Teles, Ana Rita Barradas, João Domingos, Ana Pãosinho & Isabel Madruga. (2020) Putting the pieces together: Castleman disease in a patient with HIV. Revista da Associação Médica Brasileira 66:6, pages 721-723.
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Meagan M. Jennings, Ankur R. Sangoi & Varsha Salunkhe. (2020) Rare Presentation of Kaposi's Sarcoma in an HIV-Negative Patient. The Journal of Foot and Ankle Surgery 59:3, pages 608-610.
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Rabia Miray Kisla Ekinci, Sibel Balci, Melek Ergin, Serhan Kupeli, Ibrahim Bayram, Mustafa Yilmaz & Emine Kocabas. (2020) Unicentric Castleman Disease Mimicking an Autoinflammatory Disorder: A Diagnostic Challenge in a Pediatric Patient With Recurrent Fever. Journal of Pediatric Hematology/Oncology 42:3, pages 204-207.
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Dimitris Kounatidis, Dimitra Rontogianni, Dimitrios Sampaziotis, Maria Vardaka, Chara Giatra, Christodoulos Dolapsakis, Evangelia Margellou & Natalia G. Vallianou. (2020) An HHV-8 Positive HIV Negative Multicentric Castleman’s Disease, who Responded well to Rituximab Alone. Cardiovascular & Hematological Disorders-Drug Targets 20:1, pages 84-86.
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Ruchi Goel, Akash Raut, Ayushi Agarwal, Shweta Raghav, Sumit Kumar, Simmy Chaudhary, Priyanka Golhait, Sushil Kumar & Ravindra Saran. (2020) A Rare Presentation of Orbital Castleman’s Disease. Case Reports in Ophthalmological Medicine 2020, pages 1-4.
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Zhen Wang, Shiwei Yang, Zunmin Zhu, Pingchong Lei, Jing Yang, Ping Zhang & Kai Sun. (2020) A Case of Successful Allogeneic Hematopoietic Stem Cell Transplantation for HHV8-Positive Castleman’s Disease with a Review of the Literature. Cell Transplantation 29, pages 096368972094357.
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Ping Li, Huaipu Liu, Hao Li, Ang Li, Guangyin Yu & Weihua Yin. (2019) Hyaline vascular variant of unicentric Castleman disease of the tonsil: a case report. Diagnostic Pathology 14:1.
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Robert M. Kwee & Thomas C. Kwee. (2019) Calcified or ossified benign soft tissue lesions that may simulate malignancy. Skeletal Radiology 48:12, pages 1875-1890.
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Ming‐Tsung Chen, Shih‐Chun Lee, Chun‐Chi Lu & Chen‐Liang Tsai. (2019) Unusual presentation of Castleman's disease mimicking lung cancer. Respirology Case Reports 7:4, pages e00416.
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David Boutboul, Jehane Fadlallah, Sylvain Chawki, Claire Fieschi, Marion Malphettes, Antoine Dossier, Laurence Gérard, Pierre Mordant, Véronique Meignin, Eric Oksenhendler & Lionel Galicier. (2019) Treatment and outcome of Unicentric Castleman Disease: a retrospective analysis of 71 cases. British Journal of Haematology.
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David Leo Choi, Kristina Brannock & Alice L Tang. (2019) Castleman Disease Presenting as a Parapharyngeal Mass: A Case Report and Review of the Literature. Clinical Medicine Insights: Case Reports 12, pages 117954761985379.
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Stavros Tsotsolis, I. A. Ziogas, D. Miliaras & G. Tsoulfas. (2019) Castleman’s Disease: A Unicentric Case of Abdominal Origin and Literature Review. Hellenic Journal of Surgery 91:1, pages 33-43.
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Anne Musters & Sander W. Tas. 2019. Rare Rheumatic Diseases of Immunologic Dysregulation. Rare Rheumatic Diseases of Immunologic Dysregulation 121 138 .
Jie Li, Jia Wang, Zhitao Yang, Hexiang Wang, Junyi Che & Wenjian Xu. (2018) Castleman disease versus lymphoma in neck lymph nodes: a comparative study using contrast-enhanced CT. Cancer Imaging 18:1.
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Masatoshi Matsunami, Yoshifumi Ubara, Keiichi Sumida, Yoichi Oshima, Masahiko Oguro, Kazuya Kinoshita, Kiho Tanaka, Yuki Nakamura, Keiichi Kinowaki, Kenichi Ohashi, Takeshi Fujii, Takuro Igawa, Yasuharu Sato & Yasuo Ishii. (2018) The efficacy and safety of anti-interleukin-6 receptor monoclonal blockade in a renal transplant patient with Castleman disease: early post-transplant outcome. BMC Nephrology 19:1.
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Jia-Lin Cheng, Jing Cui, Yi Wang, Zong-Zhen Xu, Feng Liu, Shu-Bin Liang & Hu Tian. (2018) Unicentric Castleman disease presenting as a retroperitoneal peripancreatic mass: A report of two cases and review of literature. World Journal of Gastroenterology 24:34, pages 3958-3964.
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Jhen-Hao Jhan, Ching-Chia Li, Wen-Jeng Wu & Hsiang-Ying Lee. (2018) Isolated retroperitoneal Castleman's disease: A case report and literature review. Clinical Case Reports 6:8, pages 1543-1548.
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Negin Rassouli, Verena C. Obmann, Linda M. Sandhaus & Karin A. Herrmann. (2018) (18F)-FDG-PET/MRI of unicentric retroperitoneal Castleman disease in a pediatric patient. Clinical Imaging 50, pages 175-180.
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Elie Cousin, Hugues Flodrops, Olivia Boyer, Julien Hogan, Mahe Ruin, Anne Couderc, Jean-Michel Goujon & Sophie Taque. (2018) Renal failure in pediatric Castleman disease: Four French cases with thrombotic microangiopathy. Pediatric Blood & Cancer 65:7, pages e27045.
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Flavius Mocian, Sorin Sorlea & Marius Coros. (2018) Left Para-Renal Castleman Disease: Case Report. Journal of Interdisciplinary Medicine 3:2, pages 102-105.
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Xiaotong He, Qiong Wang, Yaping Wu, Jiaan Hu, Dongmiao Wang, Bin Qi, Wei Zhang, Yanling Wang & Jie Cheng. (2017) Comprehensive analysis of 225 Castleman’s diseases in the oral maxillofacial and neck region: a rare disease revisited. Clinical Oral Investigations 22:3, pages 1285-1295.
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Alberto Testori, Emanuele Voulaz, Marco Alloisio, Valentina Errico, Umberto Cariboni, Matilde De Simone & Ugo Cioffi. (2018) Multicentric castleman's disease resembling metastatic lung carcinoma. A case report. Clinical Case Reports 6:3, pages 473-475.
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M. Filippini, S. Cartella, O. Bonzanini, E. Morello & A. Tincani. (2018) A Case of Spondyloarthritis in Patient Affected by Unicentric Castleman’s Disease Effectively Managed with Surgery Resection and Tocilizumab Treatment. Case Reports in Rheumatology 2018, pages 1-3.
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Hui Huang, Ruie Feng, Jian Li, Xinyu Song, Shan Li, Kai Xu, Jian Cao, Lu Zhang, Yalan Bi & Zuojun Xu. (2017) Castleman disease-associated diffuse parenchymal lung disease. Medicine 96:39, pages e8173.
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Xiang Tong, Min Bai, Weiya Wang, Qingbing Han, Panwen Tian & Hong Fan. (2017) IgG4-related disease involving polyserous effusions with elevated serum interleukin-6 levels: a case report and literature review. Immunologic Research 65:4, pages 944-950.
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L. Filliatre-Clement, H. Busby-Venner, C. Moulin, G. Roth-Guepin & A. Perrot. (2017) Hodgkin Lymphoma and Castleman Disease: When One Blood Disease Can Hide Another. Case Reports in Hematology 2017, pages 1-3.
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Hannah K. Bayes, Iain B. McInnes & George W. Chalmers. (2016) Castleman disease and lymphocytic interstitial pneumonia: a complex diagnostic and management challenge. Rheumatology, pages kew420.
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