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Review

Efficacy and safety of pirfenidone for idiopathic pulmonary fibrosis

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Pages 361-370 | Published online: 21 Mar 2014

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Maria Hollmen, Marlies Wijsenbeek, Tom Bromilow, Adam B Smith, Stuart Mealing, Damian Lewis, Liam Galvin, Steve Jones, Guus Asijee, Stéphane Soulard & Antoine Froidure. (2023) I-PreFer Study: A Discrete Choice Experiment to Explore Patient, Caregiver and Pulmonologist Preferences of Idiopathic Pulmonary Fibrosis Pharmacological Treatment Options. Patient Preference and Adherence 17, pages 1895-1906.
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Jing Tang, Jianming Li, Guo Li, Haitao Zhang, Ling Wang, Dai Li & Jinsong Ding. (2017) Spermidine-mediated poly(lactic-co-glycolic acid) nanoparticles containing fluorofenidone for the treatment of idiopathic pulmonary fibrosis. International Journal of Nanomedicine 12, pages 6687-6704.
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Fateme Bahram Yazdroudi & Alaeddin Malek. (2022) Optimal control of TGF-β to prevent formation of pulmonary fibrosis. PLOS ONE 17:12, pages e0279449.
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Evgeny Bazdyrev, Maria Panova, Valeria Zherebtsova, Alexandra Burdenkova, Ivan Grishagin, Fedor Novikov & Vladimir Nebolsin. (2022) The Hidden Pandemic of COVID-19-Induced Organizing Pneumonia. Pharmaceuticals 15:12, pages 1574.
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Hayder M. Al-kuraishy, Gaber El-Saber Batiha, Hani Faidah, Ali I. Al-Gareeb, Hebatallah M. Saad & Jesus Simal-Gandara. (2022) Pirfenidone and post-Covid-19 pulmonary fibrosis: invoked again for realistic goals. Inflammopharmacology 30:6, pages 2017-2026.
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Anna Birnhuber, Katharina Jandl, Valentina Biasin, Elisabeth Fließer, Francesco Valzano, Leigh M. Marsh, Christina Krolczik, Andrea Olschewski, Jochen Wilhelm, Wolfgang Toller, Akos Heinemann, Horst Olschewski, Malgorzata Wygrecka & Grazyna Kwapiszewska. (2022) Pirfenidone exacerbates Th2-driven vasculopathy in a mouse model of systemic sclerosis-associated interstitial lung disease. European Respiratory Journal 60:4, pages 2102347.
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Manas Sehgal, Sharayu Manish Jakhete, Amruta Ganesh Manekar & Satish Sasikumar. (2022) Specific epigenetic regulators serve as potential therapeutic targets in idiopathic pulmonary fibrosis. Heliyon 8:8, pages e09773.
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Martina Doubková. (2022) Antifibrotic therapy and its indications for interstitial pulmonary fibrosis. Vnitřní lékařství 68:4, pages 212-215.
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Henrik Jessen, Nils Hoyer, Thomas S. Prior, Peder Frederiksen, Sarah R. Rønnow, Morten A. Karsdal, Diana J. Leeming, Elisabeth Bendstrup, Jannie M. B. Sand & Saher B. Shaker. (2021) Longitudinal serological assessment of type VI collagen turnover is related to progression in a real-world cohort of idiopathic pulmonary fibrosis. BMC Pulmonary Medicine 21:1.
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David R. CassattAlex Gorovets, Banu Karimi-Shah, Rosemary Roberts, Paul W. Price, Merriline M. SatyamitraNushin Todd, Sue-Jane Wang & Libero Marzella. (2021) A Trans-Agency Workshop on the Pathophysiology of Radiation-Induced Lung Injury. Radiation Research 197:4.
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Yoshiki Seto, Gen Suzuki, Asako Aoki, Yuuki Kaneko, Masashi Kato, Hideyuki Sato & Satomi Onoue. (2021) Novel approach for attenuation of pirfenidone-induced digestive symptoms: a respirable powder formulation of pirfenidone. Therapeutic Delivery 12:7, pages 515-522.
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Ge Zhang, He Chen, Yifan Guo, Wei Zhang, Qiuyu Jiang, Si Zhang, Liping Han, She Chen & Ruyi Xue. (2021) Activation of Platelet NLRP3 Inflammasome in Crohn’s Disease. Frontiers in Pharmacology 12.
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Lili Ding, Juan Yang, Chunmei Zhang, Xiuna Zhang & Pujun Gao. (2021) Neutrophils Modulate Fibrogenesis in Chronic Pulmonary Diseases. Frontiers in Medicine 8.
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Ji Zhang, Tao Wang, Ashmita Saigal, Josephine Johnson, Jennifer Morrisson, Sahba Tabrizifard, Scott A. Hollingsworth, Michael J. Eddins, Wenxian Mao, Kim O’Neill, Margarita Garcia-Calvo, Ester Carballo-Jane, DingGang Liu, Taewon Ham, Qiong Zhou, Weifeng Dong, Hsien-Wei Meng, Jacqueline Hicks, Tian-Quan Cai, Taro Akiyama, Shirly Pinto, Alan C. Cheng, Thomas Greshock, John C. Marquis, Zhao Ren, Saswata Talukdar, Hussam Hisham Shaheen & Masahisa Handa. (2021) Discovery of a new class of integrin antibodies for fibrosis. Scientific Reports 11:1.
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Shankar J. Evani, S. L. Rajasekhar Karna, Janakiram Seshu & Kai P. Leung. (2020) Pirfenidone regulates LPS mediated activation of neutrophils. Scientific Reports 10:1.
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Maha H. Sharawy & Marwa S. Serrya. (2020) Pirfenidone attenuates gentamicin-induced acute kidney injury by inhibiting inflammasome-dependent NLRP3 pathway in rats. Life Sciences 260, pages 118454.
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Daniel S. Glass, David Grossfeld, Heather A. Renna, Priya Agarwala, Peter Spiegler, Lora J. Kasselman, Amy D. Glass, Joshua DeLeon & Allison B. Reiss. (2020) Idiopathic pulmonary fibrosis: Molecular mechanisms and potential treatment approaches. Respiratory Investigation 58:5, pages 320-335.
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Hamidreza Aboulkheyr Es, Sareh Zhand, Jean Paul Thiery & Majid Ebrahimi Warkiani. (2020) Pirfenidone reduces immune-suppressive capacity of cancer-associated fibroblasts through targeting CCL17 and TNF-beta. Integrative Biology 12:7, pages 188-197.
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Ixchel Lima-Posada, Francesco Fontana, Rosalba Pérez-Villalva, Nathan Berman-Parks & Norma A. Bobadilla. (2019) Pirfenidone prevents acute kidney injury in the rat. BMC Nephrology 20:1.
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Brandon Nokes, Eugene Golts & Kamyar Afshar. 2019. Interstitial Lung Diseases. Interstitial Lung Diseases.
C. Magnus Sköld, Lisen Arnheim-Dahlström, Karen Bartley, Christer Janson, Klaus-Uwe Kirchgaessler, Aaron Levine & Giovanni Ferrara. (2019) Patient journey and treatment patterns in adults with IPF based on health care data in Sweden from 2001 to 2015. Respiratory Medicine 155, pages 72-78.
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Amber Mortensen, Lauren Cherrier & Rajat Walia. (2018) Effect of pirfenidone on wound healing in lung transplant patients. Multidisciplinary Respiratory Medicine 13:1.
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Sally Ibbotson. (2020) Drug and chemical induced photosensitivity from a clinical perspective. Photochemical & Photobiological Sciences 17:12, pages 1885-1903.
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Yuzhen Hu, Miao Li, Mengmeng Zhang & Yiguang Jin. (2018) Inhalation treatment of idiopathic pulmonary fibrosis with curcumin large porous microparticles. International Journal of Pharmaceutics 551:1-2, pages 212-222.
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Yanwu Sun, Yiyi Zhang & Pan Chi. (2018) Pirfenidone suppresses TGF‑β1‑induced human intestinal fibroblasts activities by regulating proliferation and apoptosis via the inhibition of the Smad and PI3K/AKT signaling pathway. Molecular Medicine Reports.
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Chang Li, Veronika Rezov, Emmi Joensuu, Ville Vartiainen, Mikko Rönty, Miao Yin, Marjukka Myllärniemi & Katri Koli. (2018) Pirfenidone decreases mesothelioma cell proliferation and migration via inhibition of ERK and AKT and regulates mesothelioma tumor microenvironment in vivo. Scientific Reports 8:1.
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Dan Lei, Yingxue Huang, Hongfu Xie, Yuxin Yi, Juan Long, Shangqing Lin, Chuchu Huang, Dan Jian & Ji Li. (2018) Fluorofenidone inhibits UV-A induced senescence in human dermal fibroblasts via the mammalian target of rapamycin-dependent SIRT1 pathway. The Journal of Dermatology 45:7, pages 791-798.
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Yan-Wu Sun, Yi-Yi Zhang, Xin-Jie Ke, Xue-jing Wu, Zhi-Fen Chen & Pan Chi. (2018) Pirfenidone prevents radiation-induced intestinal fibrosis in rats by inhibiting fibroblast proliferation and differentiation and suppressing the TGF-β1/Smad/CTGF signaling pathway. European Journal of Pharmacology 822, pages 199-206.
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Rokhsana Rasooli, Fatemeh Pourgholamhosein, Younes Kamali, Fatemeh Nabipour & Ali Mandegary. (2017) Combination Therapy with Pirfenidone plus Prednisolone Ameliorates Paraquat-Induced Pulmonary Fibrosis. Inflammation 41:1, pages 134-142.
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Min-Young Park, Woo-Haing Shim, Jeong-Min Kim, Gun-Wook Kim, Hoon-Soo Kim, Hyun-Chang Ko, Moon-Bum Kim & Byung-Soo Kim. (2017) Pirfenidone-induced photo-allergic reaction in a patient with idiopathic pulmonary fibrosis. Photodermatology, Photoimmunology & Photomedicine 33:4, pages 209-212.
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