Citations (42)
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Kenneth R Chapman, Joanna Chorostowska-Wynimko, A Rembert Koczulla, Ilaria Ferrarotti & Noel G McElvaney. (2018) Alpha 1 antitrypsin to treat lung disease in alpha 1 antitrypsin deficiency: recent developments and clinical implications. International Journal of Chronic Obstructive Pulmonary Disease 13, pages 419-432.
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David G Parr & Beatriz Lara. (2017) Clinical utility of alpha-1 proteinase inhibitor in the management of adult patients with severe alpha-1 antitrypsin deficiency: a review of the current literature. Drug Design, Development and Therapy 11, pages 2149-2162.
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Ross G Edgar, Mitesh Patel, Susan Bayliss, Diana Crossley, Elizabeth Sapey & Alice M Turner. (2017) Treatment of lung disease in alpha-1 antitrypsin deficiency: a systematic review. International Journal of Chronic Obstructive Pulmonary Disease 12, pages 1295-1308.
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Maria Paula Henao & Timothy J. Craig. (2016) Recent advances in understanding and treating COPD related to α1-antitrypsin deficiency. Expert Review of Respiratory Medicine 10:12, pages 1281-1294.
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Sanjay H Chotirmall, Mazen Al-Alawi, Thomas McEnery & Noel G McElvaney. (2015) Alpha-1 proteinase inhibitors for the treatment of alpha-1 antitrypsin deficiency: safety, tolerability, and patient outcomes. Therapeutics and Clinical Risk Management 11, pages 143-151.
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Robert A. Sandhaus, James Stocks, Farshid N. Rouhani, Mark Brantly & Pnina Strauss. (2014) Biochemical Efficacy and Safety of a New, Ready-to-Use, Liquid Alpha-1-Proteinase Inhibitor, GLASSIA (Alpha1-Proteinase Inhibitor (Human), Intravenous). COPD: Journal of Chronic Obstructive Pulmonary Disease 11:1, pages 17-25.
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Manish Mohanka, Danai Khemasuwan & James K Stoller. (2012) A review of augmentation therapy for alpha-1 antitrypsin deficiency. Expert Opinion on Biological Therapy 12:6, pages 685-700.
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Catherine M Greene, Tidi Hassan, Kevin Molloy & Noel G McElvaney. (2011) The role of proteases, endoplasmic reticulum stress and SERPINA1 heterozygosity in lung disease and α-1 anti-trypsin deficiency. Expert Review of Respiratory Medicine 5:3, pages 395-411.
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Jennifer A Dickens & David A Lomas. (2011) Why has it been so difficult to prove the efficacy of alpha-1-antitrypsin replacement therapy? Insights from the study of disease pathogenesis. Drug Design, Development and Therapy 5, pages 391-405.
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Articles from other publishers (33)
J.-F. Mornex, M. Balduyck, M. Bouchecareilh, A. Cuvelier, R. Epaud, M. Kerjouan, O. Le Rouzic, C. Pison, L. Plantier, M.-C. Pujazon, M. Reynaud-Gaubert, A. Toutain, B. Trumbic, M.-C. Willemin, M. Zysman, O. Brun, M. Campana, F. Chabot, V. Chamouard, M. Dechomet, J. Fauve, B. Girerd, C. Gnakamene, S. Lefrançois, J.-N. Lombard, B. Maitre, C. Maynié-François, A. Moerman, A. Payancé, P. Reix, D. Revel, M.-P. Revel, M. Schuers, P. Terrioux, D. Theron, F. Willersinn, V. Cottin & H. Mal. (2022) Atteinte pulmonaire du déficit en alpha-1 antitrypsine. Recommandations pratiques pour le diagnostic et la prise en charge. Revue des Maladies Respiratoires 39:7, pages 633-656.
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Manuel Izquierdo, Himanshu Rawal, Michael Armstrong & Chad R. Marion. (2022) Alpha-1 Asthma Overlap Syndrome: a Clinical Overview. Current Allergy and Asthma Reports 22:9, pages 101-111.
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Jan Sieluk, Julia F. Slejko, Henry Silverman, Eleanor Perfetto & C. Daniel Mullins. (2020) Medical costs of Alpha-1 antitrypsin deficiency-associated COPD in the United States. Orphanet Journal of Rare Diseases 15:1.
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Reka Lorincz & David T. Curiel. (2020) Advances in Alpha-1 Antitrypsin Gene Therapy. American Journal of Respiratory Cell and Molecular Biology 63:5, pages 560-570.
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Crossref
José Luis López-Campos, Laura Carrasco Hernandez & Candelaria Caballero Eraso. (2020) Implications of a Change of Paradigm in Alpha1 Antitrypsin Deficiency Augmentation Therapy: From Biochemical to Clinical Efficacy. Journal of Clinical Medicine 9:8, pages 2526.
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Jack Dummer, Claudia C. Dobler, Mark Holmes, Daniel Chambers, Ian A. Yang, Lianne Parkin, Sheree Smith, Peter Wark, Anouk Dev, Sandra Hodge, Eli Dabscheck, Julian Gooi, Sameh Samuel, Steven Knowles & Anne E. Holland. (2020) Diagnosis and treatment of lung disease associated with alpha one‐antitrypsin deficiency: A position statement from the Thoracic Society of Australia and New Zealand*. Respirology 25:3, pages 321-335.
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María Torres-Durán, José Luis Lopez-Campos, Miriam Barrecheguren, Marc Miravitlles, Beatriz Martinez-Delgado, Silvia Castillo, Amparo Escribano, Adolfo Baloira, María Mercedes Navarro-Garcia, Daniel Pellicer, Lucía Bañuls, María Magallón, Francisco Casas & Francisco Dasí. (2018) Alpha-1 antitrypsin deficiency: outstanding questions and future directions. Orphanet Journal of Rare Diseases 13:1.
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Crossref
A.P. Lopes, M.A. Mineiro, F. Costa, J. Gomes, C. Santos, C. Antunes, D. Maia, R. Melo, M. Canotilho, E. Magalhães, I. Vicente, C. Valente, B.G. Gonçalves, B. Conde, C. Guimarães, C. Sousa, J. Amado, M.E. Brandão, M. Sucena, M.J. Oliveira, S. Seixas, V. Teixeira & L. Telo. (2018) Portuguese consensus document for the management of alpha-1-antitrypsin deficiency. Pulmonology 24, pages 1-21.
Crossref
Crossref
Timothy J. Craig & Maria Paula Henao. (2018)
Advances in managing COPD related to α
1
-antitrypsin deficiency: An under-recognized genetic disorder
. Allergy 73:11, pages 2110-2121.
Crossref
Crossref
Minsun Kim, Qing Cai & Youngman Oh. (2018) Therapeutic potential of alpha-1 antitrypsin in human disease. Annals of Pediatric Endocrinology & Metabolism 23:3, pages 131-135.
Crossref
Crossref
Article Editorial. (2018) Diagnosis and treatment of pulmonarydisease in α1-antitrypsin deficiency: a statement of European Respiratory Society. Russian Pulmonology 28:3, pages 273-295.
Crossref
Crossref
Ilaria Ferrarotti, Stefania Ottaviani, Annalisa De Silvestri & Angelo G. Corsico. (2018)
Update on α
1
-antitrypsin deficiency
. Breathe 14:2, pages e17-e24.
Crossref
Crossref
Mercedes Susan Mandell & Masahiko Taniguchi. 2018. Liver Anesthesiology and Critical Care Medicine. Liver Anesthesiology and Critical Care Medicine
293
305
.
Marc Miravitlles, Asger Dirksen, Ilaria Ferrarotti, Vladimir Koblizek, Peter Lange, Ravi Mahadeva, Noel G. McElvaney, David Parr, Eeva Piitulainen, Nicolas Roche, Jan Stolk, Gabriel Thabut, Alice Turner, Claus Vogelmeier & Robert A. Stockley. (2017)
European Respiratory Society statement: diagnosis and treatment of pulmonary disease in α
1
-antitrypsin deficiency
. European Respiratory Journal 50:5, pages 1700610.
Crossref
Crossref
Tidi Hassan, Chiara de Santi, Catherine Mooney, Noel G. McElvaney & Catherine M. Greene. (2017) Alpha-1 antitrypsin augmentation therapy decreases miR-199a-5p, miR-598 and miR-320a expression in monocytes via inhibition of NFκB. Scientific Reports 7:1.
Crossref
Crossref
Ignacio Blanco. 2017. Blanco's Overview of Alpha-1 Antitrypsin Deficiency. Blanco's Overview of Alpha-1 Antitrypsin Deficiency
175
191
.
Umur Hatipoğlu & James K. Stoller. (2016) α1-Antitrypsin Deficiency. Clinics in Chest Medicine 37:3, pages 487-504.
Crossref
Crossref
Catherine M. Greene, Stefan J. Marciniak, Jeffrey Teckman, Ilaria Ferrarotti, Mark L. Brantly, David A. Lomas, James K. Stoller & Noel G. McElvaney. (2016) α1-Antitrypsin deficiency. Nature Reviews Disease Primers 2:1.
Crossref
Crossref
Chao Wang & William E. Balch. 2016. Alpha-1 Antitrypsin. Alpha-1 Antitrypsin
53
83
.
James K. Stoller, Loutfi S. Aboussouan, Richard E. Kanner, Laura A. Wilson, Phil Diaz & Robert Wise. (2015) Characteristics of Alpha-1 Antitrypsin–Deficient Individuals in the Long-term Oxygen Treatment Trial and Comparison with Other Subjects with Chronic Obstructive Pulmonary Disease. Annals of the American Thoracic Society 12:12, pages 1796-1804.
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Crossref
Amit Banga, Haala Rokadia & James K. Stoller. (2015) A Review of Lung Transplantation for Patients With α-1 Antitrypsin Deficiency. Clinical Pulmonary Medicine 22:5, pages 239-245.
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Crossref
J. Traclet, P. Delaval, P. Terrioux & J.-F. Mornex. (2015) Augmentation therapy of alpha-1 antitrypsin deficiency associated emphysema. Revue des Maladies Respiratoires 32:4, pages 435-446.
Crossref
Crossref
Francisco Casas, Ignacio Blanco, María Teresa Martínez, Ana Bustamante, Marc Miravitlles, Sergio Cadenas, José M. Hernández, Lourdes Lázaro, Esther Rodríguez, Francisco Rodríguez-Frías, María Torres & Beatriz Lara. (2015) Actualización sobre indicaciones de búsqueda activa de casos y tratamiento con alfa-1 antitripsina por vía intravenosa en pacientes con enfermedad pulmonar obstructiva crónica asociada a déficit de alfa-1 antitripsina. Archivos de Bronconeumología 51:4, pages 185-192.
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Francisco Casas, Ignacio Blanco, María Teresa Martínez, Ana Bustamante, Marc Miravitlles, Sergio Cadenas, José M. Hernández, Lourdes Lázaro, Esther Rodríguez, Francisco Rodríguez-Frías, María Torres & Beatriz Lara. (2015) Indications for Active Case Searches and Intravenous Alpha-1 Antitrypsin Treatment for Patients With Alpha-1 Antitrypsin Deficiency Chronic Pulmonary Obstructive Disease: An Update. Archivos de Bronconeumología (English Edition) 51:4, pages 185-192.
Crossref
Crossref
F. de Serres & I. Blanco. (2014) Role of alpha-1 antitrypsin in human health and disease. Journal of Internal Medicine 276:4, pages 311-335.
Crossref
Crossref
Amit Banga, Thomas Gildea, Jeevanantham Rajeswaran, Haala Rokadia, Eugene H. Blackstone & James K. Stoller. (2014)
The Natural History of Lung Function after Lung Transplantation for α
1
-Antitrypsin Deficiency
. American Journal of Respiratory and Critical Care Medicine 190:3, pages 274-281.
Crossref
Crossref
Jean-François Mornex. (2014) Le déficit en alpha-1 antitrypsine 50 ans après sa découverte. Bulletin de l'Académie Nationale de Médecine 198:4-5, pages 757-766.
Crossref
Crossref
Leslie J. Donato, Sarah M. Jenkins, Carin Smith, Jerry A. Katzmann & Melissa R. Snyder. (2012)
Reference and Interpretive Ranges for α
1
-Antitrypsin Quantitation by Phenotype in Adult and Pediatric Populations
. American Journal of Clinical Pathology 138:3, pages 398-405.
Crossref
Crossref
David A. Bergin, Killian Hurley, Noel G. McElvaney & Emer P. Reeves. (2012) Alpha-1 Antitrypsin: A Potent Anti-Inflammatory and Potential Novel Therapeutic Agent. Archivum Immunologiae et Therapiae Experimentalis 60:2, pages 81-97.
Crossref
Crossref
James K. Stoller & Loutfi S. Aboussouan. (2012)
A Review of α
1
-Antitrypsin Deficiency
. American Journal of Respiratory and Critical Care Medicine 185:3, pages 246-259.
Crossref
Crossref
Mercedes Susan Mandell & Masahiko Taniguchi. 2012. Liver Anesthesiology and Critical Care Medicine. Liver Anesthesiology and Critical Care Medicine
255
266
.
Theresa Lindhout, Umar Iqbal, Lisa M. Willis, Anne N. Reid, Jianjun Li, Xin Liu, Maria Moreno & Warren W. Wakarchuk. (2011) Site-specific enzymatic polysialylation of therapeutic proteins using bacterial enzymes. Proceedings of the National Academy of Sciences 108:18, pages 7397-7402.
Crossref
Crossref
Adriano R. Tonelli & Mark L. Brantly. (2010) Augmentation therapy in alpha-1 antitrypsin deficiency: advances and controversies. Therapeutic Advances in Respiratory Disease 4:5, pages 289-312.
Crossref
Crossref