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Original Research

Alpha-1-antitrypsin augmentation therapy in deficient individuals enrolled in the Alpha-1 Foundation DNA and Tissue Bank

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Pages 443-452 | Published online: 08 Dec 2009

References

  • BrantlyMNukiwaTCrystalRGMolecular basis of alpha-1-antitrypsin deficiencyAm J Med19888413313289385
  • GadekJEFellsGAZimmermanRLRennardSICrystalRGAntielastases of the human alveolar structures. Implications for the protease-antiprotease theory of emphysemaJ Clin Invest1981688898986169740
  • StockleyRAThe pathogenesis of chronic obstructive lung diseases: implications for therapyQJM1995881411467704565
  • American Thoracic SocietyEuropean Respiratory SocietyAmerican Thoracic Society/European Respiratory Society statement: standards for the diagnosis and management of individuals with alpha-1-antitrypsin deficiencyAm J Respir Crit Care Med200316881890014522813
  • The Alpha-1-Antitrypsin Deficiency Registry Study GroupSurvival and FEV1 decline in individuals with severe deficiency of alpha-1-antitrypsin. The Alpha-1-Antitrypsin Deficiency Registry Study GroupAm J Respir Crit Care Med199815849599655706
  • EvaldTDirksenAKeittelmannSViskumKKok-JensenADecline in pulmonary function in patients with alpha-1-antitrypsin deficiencyLung19901685795852117166
  • SeersholmNKok-JensenADirksenADecline in FEV1 among patients with severe hereditary alpha-1-antitrypsin deficiency type PiZAm J Respir Crit Care Med1995152192219258520756
  • PiitulainenEErikssonSDecline in FEV1 related to smoking status in individuals with severe alpha-1-antitrypsin deficiency (PiZZ)Eur Respir J19991324725110065663
  • JanusEDPhillipsNTCarrellRWSmoking, lung function, and alpha-1-antitrypsin deficiencyLancet198511521542857224
  • DawkinsPADawkinsCLWoodAMNightingalePGStockleyJAStockleyRARate of progression of lung function impairment in alpha-1-antitrypsin deficiencyEur Respir J2009331338134419164359
  • WuMCErikssonSLung function, smoking and survival in severe alpha 1-antitrypsin deficiency, PiZZJ Clin Epidemiol198841115711653264848
  • PiitulainenETornlingGErikssonSEffect of age and occupational exposure to airway irritants on lung function in non-smoking individuals with alpha 1-antitrypsin deficiency (PiZZ)Thorax1997522442489093340
  • DowsonLJGuestPJStockleyRALongitudinal changes in physiological, radiological, and health status measurements in alpha(1)-antitrypsin deficiency and factors associated with declineAm J Respir Crit Care Med20011641805180911734427
  • EdenEHammelJRouhaniFNAsthma features in severe alpha-1-antitrypsin deficiency: experience of the National Heart, Lung, and Blood Institute RegistryChest200312376577112628876
  • SeersholmNWenckerMBanikNDoes alpha-1-antitrypsin augmentation therapy slow the annual decline in FEV1 in patients with severe hereditary alpha-1-antitrypsin deficiency?Eur Respir J199710226022639387950
  • WenckerMFuhrmannBBanikNKonietzkoNLongitudinal follow-up of patients with alpha(1)-protease inhibitor deficiency before and during therapy with IV alpha(1)-protease inhibitorChest200111973774411243951
  • DirksenADijkmanJHMadsenFA randomized clinical trial of alpha(1)-antitrypsin augmentation therapyAm J Respir Crit Care Med19991601468147210556107
  • PiitulainenETornlingGErikssonSEnvironmental correlates of impaired lung function in non-smokers with severe alpha-1-antitrypsin deficiency (PiZZ)Thorax19985393994310193391
  • LiebermanJAugmentation therapy reduces frequency of lung infections in antitrypsin deficiency: a new hypothesis with supporting dataChest20001181480148511083705
  • SilvermanEKProvinceMARaoDCPierceJACampbellEJA family study of the variability of pulmonary function in alpha-1-antitrypsin deficiency. Quantitative phenotypesAm Rev Respir Dis1990142101510212240821
  • SilvermanEKProvinceMACampbellEJPierceJARaoDCVariability of pulmonary function in alpha-1-antitrypsin deficiency: residual family resemblance beyond the effect of the Pi locusHum Hered1990403403552083948
  • DirksenAPiitulainenEParrDGExploring the role of CT densitometry: a randomised study of augmentation therapy in alpha-1-antitrypsin deficiencyEur Respir J2009331345135319196813