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Ultrastructural Pathology Volume 34, 2010 - Issue 6
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Research Article

Ultrastructural Characteristics (or Evaluation) of Creutzfeldt-Jakob Disease and Other Human Transmissible Spongiform Encephalopathies or Prion Diseases

Paweł P. Liberski Department of Molecular Pathology and Neuropathology, Chair of Oncology, Medical University of Lodz, Lodz, PolandCorrespondence[email protected]
, MD, PhD,
Beata Sikorska Department of Molecular Pathology and Neuropathology, Chair of Oncology, Medical University of Lodz, Lodz, Poland
, MD, PhD,
Jean-Jacques Hauw APHP, Hôpital de la Salpêtrière, Laboratoire de Neuropathologie Raymond Escourolle, Paris VI University and InVS, Centre National de Référence des ATNC, Paris, France
, MD, PhD,
Nicolas Kopp Hôpital Neurologique et Neuro-chirurgical Pierre Wertheimer, Laboratoire d'Anatomie Pathologique et de Neuropathologique, Lyon, France
, MD, PhD,
Nathalie Streichenberger Hôpital Neurologique et Neuro-chirurgical Pierre Wertheimer, Laboratoire d'Anatomie Pathologique et de Neuropathologique, Lyon, France
, MD, PhD,
Pierrie Giraud Hôpital Neurologique et Neuro-chirurgical Pierre Wertheimer, Laboratoire d'Anatomie Pathologique et de Neuropathologique, Lyon, France
, MD, PhD,
Jan Boellaard Tübingen, Federal Republic of Germany, retired
, MD, PhD,
Herbert Budka Institute of Neurology, Medical University of Vienna, and Austrian Reference Centre for Human Prion Diseases, Vienna, Austria
, MD, PhD,
Gabor G. Kovacs Institute of Neurology, Medical University of Vienna, and Austrian Reference Centre for Human Prion Diseases, Vienna, Austria
, MD PhD,
James Ironside National CJD Surveillance Unit, Western General Hospital, Edinburgh, UK
, FRCPath &
Paul Brown CEA/DSV/iMETI/SEPIA, Fontenay-aux-Roses, France
, MD, PhD show all
Pages 351-361 | Received 16 Apr 2010, Accepted 04 May 2010, Published online: 11 Nov 2010

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Paweł P. Liberski. (2019) Axonal changes in experimental prion diseases recapitulate those following constriction of postganglionic branches of the superior cervical ganglion: a comparison 40 years later. Prion 13:1, pages 83-93.
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Beata Sikorska, Agata Gajos, Andrzej Bogucki, Emil Zielonka, Christina Sigurdson & Pawel P. Liberski. (2017) Electron microscopic and confocal laser microscopy analysis of amyloid plaques in chronic wasting disease transmitted to transgenic mice. Prion 11:6, pages 431-439.
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Rosario Alberto Caruso, Antonino Parisi, Costantino Crisafulli, Anna Bonanno, Roberta Lucianò, Giovanni Branca, Marco Scardigno & Francesco Fedele. (2011) Intraepithelial Infiltration by Mast Cells in Human Helicobacter pylori Active Gastritis. Ultrastructural Pathology 35:6, pages 251-255.
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Articles from other publishers (23)

Hash Brown Taha. (2023) The ESCRT Pathway's Role in Prion Diseases and Beyond. The Journal of Neuroscience 43:46, pages 7727-7729.
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Jessica A. Lawrence, Patricia Aguilar-Calvo, Daniel Ojeda-Juárez, Helen Khuu, Katrin Soldau, Donald P. Pizzo, Jin Wang, Adela Malik, Timothy F. Shay, Erin E. Sullivan, Brent Aulston, Seung Min Song, Julia A. Callender, Henry Sanchez, Michael D. Geschwind, Subhojit Roy, Robert A. Rissman, JoAnn Trejo, Nobuyuki Tanaka, Chengbiao Wu, Xu Chen, Gentry N. Patrick & Christina J. Sigurdson. (2023) Diminished Neuronal ESCRT-0 Function Exacerbates AMPA Receptor Derangement and Accelerates Prion-Induced Neurodegeneration. The Journal of Neuroscience 43:21, pages 3970-3984.
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Romana Wimmer, Milena Steiner, Karl Matz & Peter Stöger. (2023) Creutzfeldt-Jakob-Krankheit – eine mögliche Differentialdiagnose an einer PsychiatrieCreutzfeldt-Jacob Disease: a Possible Differential Diagnosis in a Psychiatric Hospital. psychopraxis. neuropraxis 26:1, pages 31-37.
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Stefano Thellung, Alessandro Corsaro, Irene Dellacasagrande, Mario Nizzari, Martina Zambito & Tullio Florio. (2022) Proteostasis unbalance in prion diseases: Mechanisms of neurodegeneration and therapeutic targets. Frontiers in Neuroscience 16.
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Anirban Basu, Adil Mahammad & Arindam Das. (2022) Inhibition of the formation of lysozyme fibrillar assemblies by the isoquinoline alkaloid coralyne. New Journal of Chemistry 46:7, pages 3258-3269.
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Muhammad Elsadany, Reem A. Elghaish, Aya S. Khalil, Alaa S. Ahmed, Rana H. Mansour, Eman Badr & Menattallah Elserafy. (2021) Transcriptional Analysis of Nuclear-Encoded Mitochondrial Genes in Eight Neurodegenerative Disorders: The Analysis of Seven Diseases in Reference to Friedreich’s Ataxia. Frontiers in Genetics 12.
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Charles R. Hutti, Kevin A. Welle, Jennifer R. Hryhorenko & Sina Ghaemmaghami. (2020) Global analysis of protein degradation in prion infected cells. Scientific Reports 10:1.
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Su-Chun How, Ai Hsin, Guan-Yu Chen, Wei-Tse Hsu, Szu-Ming Yang, Wei-Lung Chou, Shiu-Huey Chou & Steven S.-S. Wang. (2019) Exploring the influence of brilliant blue G on amyloid fibril formation of lysozyme. International Journal of Biological Macromolecules 138, pages 37-48.
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Anna Bartoletti-Stella, Patrizia Corrado, Nicola Mometto, Simone Baiardi, Pascal F. Durrenberger, Thomas Arzberger, Richard Reynolds, Hans Kretzschmar, Sabina Capellari & Piero Parchi. (2018) Analysis of RNA Expression Profiles Identifies Dysregulated Vesicle Trafficking Pathways in Creutzfeldt-Jakob Disease. Molecular Neurobiology 56:7, pages 5009-5024.
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Joanna E. Pankiewicz, Sandrine Sanchez, Kent Kirshenbaum, Regina B. Kascsak, Richard J. Kascsak & Martin J. Sadowski. (2018) Anti-prion Protein Antibody 6D11 Restores Cellular Proteostasis of Prion Protein Through Disrupting Recycling Propagation of PrPSc and Targeting PrPSc for Lysosomal Degradation. Molecular Neurobiology 56:3, pages 2073-2091.
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Patricia Aguilar-Calvo, Cyrus Bett, Alejandro M. Sevillano, Timothy D. Kurt, Jessica Lawrence, Katrin Soldau, Per Hammarström, K. Peter R. Nilsson & Christina J. Sigurdson. (2018) Generation of novel neuroinvasive prions following intravenous challenge. Brain Pathology 28:6, pages 999-1011.
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Belén Ansoleaga, Paula Garcia-Esparcia, Franc Llorens, Karina Hernández-Ortega, Margarita Carmona, José Antonio del Rio, Inga Zerr & Isidro Ferrer. (2016) Altered Mitochondria, Protein Synthesis Machinery, and Purine Metabolism Are Molecular Contributors to the Pathogenesis of Creutzfeldt–Jakob Disease. Journal of Neuropathology & Experimental Neurology 75:8, pages 755-769.
Crossref
Zareen Amtul. (2016) Why therapies for Alzheimer’s disease do not work: Do we have consensus over the path to follow?. Ageing Research Reviews 25, pages 70-84.
Crossref
Jack C. de la TorreJack C. de la Torre. 2016. Alzheimer’s Turning Point. Alzheimer’s Turning Point 39 48 .
Jack C. de la TorreJack C. de la Torre. 2016. Alzheimer’s Turning Point. Alzheimer’s Turning Point 1 20 .
Ilaria Mirabile, Parmjit S. Jat, Sebastian Brandner & John Collinge. (2015) Identification of clinical target areas in the brainstem of prion-infected mice. Neuropathology and Applied Neurobiology 41:5, pages 613-630.
Crossref
Rob Goold, Chris McKinnon & Sarah J. Tabrizi. (2015) Prion degradation pathways: Potential for therapeutic intervention. Molecular and Cellular Neuroscience 66, pages 12-20.
Crossref
Hermann C Altmeppen, Johannes Prox, Susanne Krasemann, Berta Puig, Katharina Kruszewski, Frank Dohler, Christian Bernreuther, Ana Hoxha, Luise Linsenmeier, Beata Sikorska, Pawel P Liberski, Udo Bartsch, Paul Saftig & Markus Glatzel. (2015) The sheddase ADAM10 is a potent modulator of prion disease. eLife 4.
Crossref
Josephine W. Wu, Kuan-Nan Liu, Su-Chun How, Wei-An Chen, Chia-Min Lai, Hwai-Shen Liu, Chaur-Jong Hu & Steven S. -S. Wang. (2013) Carnosine's Effect on Amyloid Fibril Formation and Induced Cytotoxicity of Lysozyme. PLoS ONE 8:12, pages e81982.
Crossref
Lilla Reiniger, Ilaria Mirabile, Ana Lukic, Jonathan DF Wadsworth, Jacqueline M Linehan, Michael Groves, Jessica Lowe, Ronald Druyeh, Peter Rudge, John Collinge, Simon Mead & Sebastian Brandner. (2013) Filamentous white matter prion protein deposition is a distinctive feature of multiple inherited prion diseases. Acta Neuropathologica Communications 1:1.
Crossref
Frederik H Aidt, Lis F Hasholt, Michael Christiansen & Henning Laursen. (2013) Localization of A11‐reactive oligomeric species in prion diseases. Histopathology 62:7, pages 994-1001.
Crossref
Leo H. Wang, Robert C. Bucelli, Erica Patrick, Dhanashree Rajderkar, Enrique Alvarez III, Miranda M. Lim, Gabriela DeBruin, Victoria Sharma, Sonika Dahiya, Robert E. Schmidt, Tammie S. Benzinger, Beth A. Ward & Beau M. Ances. (2012) Role of magnetic resonance imaging, cerebrospinal fluid, and electroencephalogram in diagnosis of sporadic Creutzfeldt-Jakob disease. Journal of Neurology 260:2, pages 498-506.
Crossref
Beata Sikorska & Pawel P. Liberski. 2012. Protein Aggregation and Fibrillogenesis in Cerebral and Systemic Amyloid Disease. Protein Aggregation and Fibrillogenesis in Cerebral and Systemic Amyloid Disease 457 496 .

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