Limitations of the dichotomized 6-minute walk distance when computing lung allocation score for cystic fibrosis: a 16-year retrospective cohort study

References

• Castellani C, Duff AJA, Bell SC, et al. ECFS best practice guidelines: the 2018 revision. J Cyst Fibros. 2018;17(2):153–178.
   PubMed Web of Science ®Google Scholar
• Gottlieb J. Lung allocation. J Thorac Dis. 2017;9(8):2670–2674.
   PubMed Web of Science ®Google Scholar
• Palleschi A, Benazzi E, Rossi CF, et al. Lung allocation score system: first Italian experience. Transplant Proc. 2019;51(1):190–193.
   PubMed Web of Science ®Google Scholar
• Singh SJ, Puhan MA, Andrianopoulos V, et al. An official systematic review of the european respiratory society/American thoracic society: measurement properties of field walking tests in chronic respiratory disease. Eur Respir J. 2014;44(6):1447–1478.
   PubMed Web of Science ®Google Scholar
• Martin C, Chapron J, Hubert D, et al. Prognostic value of six minute walk test in cystic fibrosis adults. Respir Med. 2013;107(12):1881–1887.
   PubMed Web of Science ®Google Scholar
• Stollar F, Rodrigues JC, Cunha MT, et al. Six minute walk test Z score: correlations with cystic fibrosis severity markers. J Cyst Fibros. 2012;11(3):253–256.
   PubMed Web of Science ®Google Scholar
• Donadio MVF, Heinzmann-filho JP, Vendrusculo FM, et al. Six-Minute walk test results predict risk of hospitalization for youths with cystic fibrosis: a 5-Year Follow-Up study. J Pediatr. 2017;182:204–209.e1.
   PubMed Web of Science ®Google Scholar
• Colombo C, Littlewood J. The implementation of standards of care in Europe: state of the art. J Cyst Fibros. 2011;10:S7–S15.
   PubMed Web of Science ®Google Scholar
• Hebestreit H, Arets HGM, Aurora P, European Cystic Fibrosis Exercise Working Group, et al. Statement on exercise testing in cystic fibrosis. Respiration. 2015;90(4):332–351.
   PubMed Web of Science ®Google Scholar
• Crapo RO, Casaburi R, Coates AL, et al. ATS statement: guidelines for the six-minute walk test. Am J Respir Crit Care Med. 2002;166:111–117.
   PubMed Web of Science ®Google Scholar
• Holland AE, Spruit MA, Troosters T, et al. An official European respiratory society/American thoracic society technical standard: field walking tests in chronic respiratory disease. Eur Respir J. 2014;44(6):1428–1446.
   PubMed Web of Science ®Google Scholar
• Piaggi G, Gambazza S, Guarise R, et al. Pulse oximetry oxygen saturation during the 6-min walk test: a limit for stopping the test without resuming it. Eur Respir J. 2015;46(4):1222–1223.
   PubMed Web of Science ®Google Scholar
• Cacciari E, Milani S, Balsamo A, et al. Italian cross-sectional growth charts for height, weight and BMI (2 to 20 yr). J Endocrinol Invest. 2006;29(7):581–593.
   PubMed Web of Science ®Google Scholar
• Quanjer PH, Stanojevic S, Cole TJ, ERS Global Lung Function Initiative, et al. Multi-ethnic reference values for spirometry for the 3–95-yr age range: the global lung function 2012 equations. Eur Respir J. 2012;40(6):1324–1343.
   PubMed Web of Science ®Google Scholar
• Andrinopoulou ER, Rizopoulos D, Jin R, et al. An introduction to mixed models and joint modeling: Analysis of valve function over time. Ann Thorac Surg. 2012;93(6):1765–1772.
   PubMed Web of Science ®Google Scholar
• Rizopoulos D. The R package JMbayes for fitting joint models for longitudinal and time-to-Event data using MCMC. J Stat Softw. 2016;72(7):1–46.
   Web of Science ®Google Scholar
• Castleberry AW, Englum BR, Snyder LD, et al. The utility of preoperative Six-Minute-Walk distance in lung transplantation. Am J Respir Crit Care Med. 2015;192(7):843–852.
   PubMed Web of Science ®Google Scholar
• Castleberry A, Mulvihill MS, Yerokun BA, et al. The utility of 6-minute walk distance in predicting waitlist mortality for lung transplant candidates. J Heart Lung Transplant. 2017;36(7):780–786.
   PubMed Web of Science ®Google Scholar
• Lynch J, Sayah D. Lung transplantation for cystic fibrosis: results, indications, complications, and controversies. Semin Respir Crit Care Med. 2016;36:299–320.
   Web of Science ®Google Scholar
• Krivchenia K, Tumin D, Tobias JD, et al. Increased mortality in adult cystic fibrosis patients with medicaid insurance awaiting lung transplantation. Lung. 2016;194(5):799–806.
   PubMed Web of Science ®Google Scholar
• Colombo C, Alicandro G, Gambazza S, et al. Ventilation inhomogeneity is associated with OGTT-derived insulin secretory defects in cystic fibrosis. Pediatr Pulmonol. 2019;54(2):141–149.
   PubMed Web of Science ®Google Scholar
• Tomlinson OW, Stoate ALE, Dobson L, et al. The effect of dysglycaemia on changes in pulmonary and aerobic function in cystic fibrosis. Front Physiol. 2022;13:834664.
   PubMed Web of Science ®Google Scholar
• Causer AJ, Shute JK, Cummings MH, et al. The implications of dysglycaemia on aerobic exercise and ventilatory function in cystic fibrosis. J Cyst Fibros. 2020;19(3):427–433.
   PubMed Web of Science ®Google Scholar
• Ramos KJ, Smith PJ, McKone EF, CF Lung Transplant Referral Guidelines Committee, et al. Lung transplant referral for individuals with cystic fibrosis: cystic fibrosis foundation consensus guidelines. J Cyst Fibros. 2019;18(3):321–333.
   PubMed Web of Science ®Google Scholar
• Volkova N, Moy K, Evans J, et al. Disease progression in patients with cystic fibrosis treated with ivacaftor: Data from national US and UK registries. J Cyst Fibros. 2020;19(1):68–79.
   PubMed Web of Science ®Google Scholar
• Konstan MW, McKone EF, Moss RB, et al. Assessment of safety and efficacy of long-term treatment with combination lumacaftor and ivacaftor therapy in patients with cystic fibrosis homozygous for the F508del-CFTR mutation (PROGRESS): a phase 3, extension study. Lancet Respir Med. 2016;2600:1–12.
   Google Scholar
• Taylor-Cousar JL, Munck A, McKone EF, et al. Tezacaftor–ivacaftor in patients with cystic fibrosis homozygous for Phe508del. N Engl J Med. 2017;377(21):2013–2023.
   PubMed Web of Science ®Google Scholar
• Middleton PG, Mall MA, Dřevínek P, et al. Elexacaftor–tezacaftor–ivacaftor for cystic fibrosis with a single Phe508del allele. N Engl J Med. 2019;381(19):1809–1819.
   PubMed Web of Science ®Google Scholar
• Hebestreit H, Hulzebos EHJ, Schneiderman JE, Prognostic Value of CPET in CF Study Group, et al. Cardiopulmonary exercise testing provides additional prognostic information in cystic fibrosis. Am J Respir Crit Care Med. 2019;199(8):987–995.
   PubMed Web of Science ®Google Scholar
• Lehr CJ, Skeans M, Dasenbrook E, et al. Effect of including important clinical variables on accuracy of the lung allocation score for cystic fibrosis and chronic obstructive pulmonary disease. Am J Respir Crit Care Med. 2019;200(8):1013–1021.
   PubMed Web of Science ®Google Scholar
• Chen Y, Postmus D, Cowie MR, et al. Using joint modelling to assess the association between a time-varying biomarker and a survival outcome: an illustrative example in respiratory medicine. Eur Respir J. 2021;57(2):2003206.
   PubMed Web of Science ®Google Scholar