Semantic knowledge fractionations: verbal propositions vs. perceptual input? Evidence from a child with Klinefelter syndrome

REFERENCES

• Abramsky , L. and Chapple , J. 1997 . 47,XXY (Klinefelter syndrome) and 47,XYY: Estimated rates of and indication for postnatal diagnosis with implications for prenatal counselling . Prenatal Diagnosis , 17 : 363 – 368 .
   PubMed Web of Science ®Google Scholar
• BBC Key Stage 2 Revisewise (2004). Available atvisited March 2004 http://www.bbc.co.uk/schools/revisewise.html (http://www.bbc.co.uk/schools/revisewise.html)
   Google Scholar
• Bell , B. D. , Davies , K. G. , Hermann , B. P. and Walters , G. 1999 . Confrontation naming after anterior temporal lobectomy is related to age of acquisition of the object names . Neuropsychologia , 38 ( 1 ) : 83 – 92 .
   Web of Science ®Google Scholar
• Bojesen , C. H. , Juul , S. and Gravholt , C. H. 2003 . Prenatal and postnatal prevalence of Klinefelter syndrome: A national registry study . Journal of Clinical Endocrinology and Metabolism , 88 ( 2 ) : 622 – 626 .
   PubMed Web of Science ®Google Scholar
• Boone , K. B. , Swerdloff , R. S. , Miller , B. L. , Geschwind , D. H. , Razani , J. , Lee , A. , Gonzalo , I. G. , Haddal , A. , Rankin , K. , Lu , P. and Paul , L. 2001 . Neuropsychological profile of adults with Klinefelter syndrome . Journal of the International Neuropsychological Society , 7 : 446 – 456 .
   PubMed Web of Science ®Google Scholar
• Breedin , S. D. , Saffran , E. M. and Coslett , H. B. 1994 . Reversal of the concreteness effect in a patient with semantic dementia . Cognitive Neuropsychology , 11 ( 6 ) : 617 – 660 .
   Web of Science ®Google Scholar
• Butterworth , B. 1999 . The mathematical brain , London , , UK : Macmillan .
   Google Scholar
• 2004 . Cambridge Advanced Learner's Dictionary , Cambridge University Press .
   Google Scholar
• 2004 . Cambridge Learner's Dictionary , Cambridge University Press .
   Google Scholar
• Cappelletti , M. , Butterworth , B. and Kopelman , M. D. 2001 . Spared numerical abilities in a case of semantic dementia . Neuropsychologia , 39 : 1224 – 1239 .
   PubMed Web of Science ®Google Scholar
• Cappelletti , M. , Kopelman , M. D. and Butterworth , B. 2002 . Why semantic dementia drives you to the dogs (but not the horses): A theoretical account . Cognitive Neuropsychology , 19 : 483 – 503 .
   PubMed Web of Science ®Google Scholar
• Cappelletti , M. , Kopelman , M. D. and Butterworth , B. 2005 . Dissociations in numerical abilities reveals by progressive cognitive decline in a patient with semantic dementia . Cognitive Neuropsychology , 22 ( 7 ) : 771 – 793 .
   PubMed Web of Science ®Google Scholar
• Caramazza , A. and Shelton , J. R. 1998 . Domain-specific knowledge systems in the brain: The animate-inanimate distinction . Journal of Cognitive Neuroscience , 10 : 1 – 34 .
   PubMed Web of Science ®Google Scholar
• Cedrus Corporation . 1997 . SuperlLab Pro 1.75. ,
   Google Scholar
• Cipolotti , L. and Butterworth , B. 1995 . Toward a multi route model of number processing: Impaired number transcending with preserved calculation skills . Journal of Experimental Psychology: General , 124 : 375 – 390 .
   Web of Science ®Google Scholar
• Cipolotti , L. , Butterworth , B. and Denes , G. 1991 . A specific deficits for numbers in a case of dense acalulia . Brain , 114 : 2619 – 2637 .
   PubMed Web of Science ®Google Scholar
• Crawford , J. R. and Garthwaite , P. H. 2002 . Investigation of the single case in neuropsychology: Confidence limits on the abnormality of test scores and test score differences . Neuropsychologia , 40 : 1196 – 1208 .
   PubMed Web of Science ®Google Scholar
• Crawford , J. R. and Howell , D. C. 1998 . Comparing an individual's test score against norms derived from small samples . The Clinical Neruopsychologist , 12 : 482 – 486 .
   Web of Science ®Google Scholar
• Crutch , S. J. and Warrington , E. K. 2003 . The selective impairment of fruit & vegetable knowledge: A multiple processing channels account of fine-grain category specificity . Cognitive Neuropsychology , 20 ( 3/4/5/6 ) : 355 – 372 .
   PubMed Web of Science ®Google Scholar
• Damasio , A. R. 1989 . The brain binds entities and events by multiregional activation from convergence zones . Neural Computation , 1 : 123 – 132 .
   Web of Science ®Google Scholar
• Dehaene , S. 1992 . Varieties of numerical abilities . Cognition , 44 : 1 – 42 .
   PubMed Web of Science ®Google Scholar
• Dehaene , S. and Cohen , L. 1995 . Towards an anatomical and functional model of number processing . Mathematical Cognition , 1 : 83 – 120 .
   Google Scholar
• Dehaene , S. and Cohen , L. 1997 . Cerebral pathways for calculation: Double dissociation between rote verbal and quantitative knowledge of arithmetic . Cortex , 33 : 219 – 250 .
   PubMed Web of Science ®Google Scholar
• Dehaene , S. , Piazza , M. , Pinel , P. and Cohen , L. 2003 . Three parietal circuits for number processing . Cognitive Neuropsychology , 20 : 487 – 506 .
   PubMed Web of Science ®Google Scholar
• Delazer , M. , Karner , E. , Zamarian , L. , Donnemiller , E. and Benke , T. 2006 . Number processing in posterior cortical atrophy – A neuropsychological case study . Neuropsychologia , 44 ( 1 ) : 36 – 51 .
   PubMed Web of Science ®Google Scholar
• Devlin , J. T. , Gonnerman , L. M. , Anderson , E. S. and Seidenberg , M. S. 1998 . Category-specific semantic deficits in focal and widespread brain damage: A computational account . Journal of Cognitive Neuroscience , 10 : 77 – 94 .
   PubMed Web of Science ®Google Scholar
• Dixon , M. J. 1999 . Tool and bird identification in a patient with category-specific agnosia . Brain and Cognition , 40 : 97 – 100 .
   Web of Science ®Google Scholar
• Duchaine , B. C. , Yovel , G. , Butterworth , E. J. and Nakayama , K. 2006 . Prosopagnosia as an impairment to face-specific mechanisms: Elimination of the alternative hypotheses in a developmental case . Cognitive Neuropsychology , 23 : 714 – 747 .
   PubMed Web of Science ®Google Scholar
• Dunn , L., M. and Dunn , L. M. 1981 . Peabody Picture Vocabulary Test-Revised manual for Forms L and M , Circle Pines , MN : American Guidance Service .
   Google Scholar
• Dunn , L. M. , Dunn , L. M. , Whetton , C. and Burley , J. 1997 . The British Picture Vocabulary Scale: Second Edition – BPVS II , Windsor , UK : NFER-Nelson .
   Google Scholar
• Elliot , C. D. , Smith , P. and McCulloch , K. 1996 . British Ability Scales , Windsor , UK : NFER- Nelson .
   Google Scholar
• Farah , M. J. , Rabinowitz , C. , Quinn , G. and Liu , G. T. 2000 . Early commitment of neural substrates for face recognition . Cognitive Neuropsychology , 1–3 : 117 – 123 .
   Google Scholar
• Geschwind , D. H. , Boone , K. B. , Miller , B. L. and Swerdloff , R. S. 2000 . Neurobehavioural phenotypes of Klinefelter syndrome . Mental Retardation and Developmental Disabilities Research Reviews , 6 : 107 – 116 .
   PubMedGoogle Scholar
• Geschwind , D. H. and Dykens , E. 2004 . Neurobehavioral and psychosocial issues in Klinefelter syndrome . Learning Disabilities Research & Practice , 19 : 166 – 173 .
   Google Scholar
• Goodglass , H. and Kaplan , E. 2000 . The Assessment of Aphasia and Related Disorders , London , , UK : Lea and Fediger .
   Google Scholar
• Graham , J. , Bashir , A. , Stark , R. , Silbert , A. and Walzer , S. 1988 . Oral and written language abilities of XXY boys: Implications for anticipatory guidance . Paediatrics , 81 : 795 – 806 .
   PubMed Web of Science ®Google Scholar
• Henderson Publishing Ltd . 1995 . Trivia Quiz , Woodbridge , , UK : Author .
   Google Scholar
• Hillis , A. E. and Caramazza , A. 1991 . Mechanisms for accessing lexical representations for output: Evidence from a category-specific semantic deficit . Brain and Language , 40 : 106 – 144 .
   PubMed Web of Science ®Google Scholar
• Humphreys , G. W. and Forde , E. M. 2001 . Hierarchies, similarity, and interactivity in object recognition. On the multiplicity of ‘category-specific’ deficits in neuropsychological populations . Behavioural and Brain Sciences , 24 : 453 – 509 .
   PubMed Web of Science ®Google Scholar
• Jastak , S. and Wilkinson , G. 1984 . Wide range achievement test – Revised , Wilmington , DE : Jastak .
   Google Scholar
• Khalifa , M. M. and Struthers , J. L. 2002 . Klinefelter syndrome is a common cause for mental retardation of unknown etiology among prepubertal males . Medical Genetics , 61 : 49 – 53 .
   Google Scholar
• Kremin , H. , Perrier , D. , De Wilde , M. , Dordain , M. , Le Bayon , A. , Gatignol , P. , Rabine , C. , Corbinau , M. , Lehoux , E. and Arabia , C. 2001 . Factors predicting success in picture naming in Alzheimer's disease and primary progressive aphasia . Brain and Cognition , 46 : 180 – 183 .
   PubMed Web of Science ®Google Scholar
• Lambon Ralph , M. A. , Howard , D. , Nightingale , G. and Ellis , A. W. 1998 . Are living and non-living category-specific deficits causally linked to impaired perceptual or associative knowledge? Evidence from a category-specific double dissociation . Neurocase , 4 : 311 – 338 .
   Web of Science ®Google Scholar
• Leonard , M. and Sparrow , S. 1986 . “ Prospective study of development of children with sex chromosome anomalies: New Haven study IV. Adolescence ” . In Prospective studies on children with sex chromosome aneuploidy , Edited by: Ratcliffe , S. and Paul , N. 221 – 249 . New York , NY : Alan R Liss .
   Google Scholar
• Leonard , M. , Sparrow , S. and Schowalter , J. 1982 . “ A prospective study of development of children with sex chromosomes anomalies – New Haven study III. The middle years ” . In Children with sex chromosome aneuploidy. Follow-up studies , Edited by: Stewart , D. , Bailey , J. , Netley , C. and Park , E. Vol. 18 , 193 – 218 . New York , NY : Alan R. Liss .
   Google Scholar
• Lowe , C. , Knapp , S. and Lambon Ralph , M. A. 2005 . Relative preservation of ‘animate’ knowledge in an atypical presentation of herpes simplex virus encephalitis . Neurocase , 11 : 157 – 166 .
   PubMed Web of Science ®Google Scholar
• McCarthy , R. A. and Warrington , E. K. 1988 . Evidence for modality-specific meaning systems in the brain . Nature , 334 : 428 – 430 .
   PubMed Web of Science ®Google Scholar
• McCarthy , R. and Warrington , E. K. 1990 . Cognitive neuropsychology: A clinical introduction , London/New York : Academic Press .
   Google Scholar
• McCloskey , M. 1992 . Cognitive mechanisms in numerical processing: Evidence from acquired dyscalculia . Cognition , 44 : 107 – 157 .
   PubMed Web of Science ®Google Scholar
• McCloskey , M. , Caramazza , A. and Basili , A. 1985 . Cognitive mechanisms in number processing and calculation: Evidence from dyscalculia . Brain and Cognition , 4 : 171 – 176 .
   PubMed Web of Science ®Google Scholar
• McGregor , K. K. , Friedman , R. M. , Reilly , R. M. and Newman , R. M. 2002 . Semantic representation and naming in young children . Journal of Speech, Language and Hearing Research , 45 : 332 – 346 .
   PubMed Web of Science ®Google Scholar
• McRae , K. , de Sa , V. R. and Seidenberg , M. S. 1997 . On the nature and scope of featural representations of word meaning . Journal of Experimental Psychology – General , 126 ( 2 ) : 99 – 130 .
   PubMed Web of Science ®Google Scholar
• Morris , J. K. , Alberman , E. , Scott , C. and Jacobs , P. 2008 . Is the prevalence of Klinefelter syndrome increasing? . European Journal of Human Genetics , 16 : 163 – 170 .
   PubMed Web of Science ®Google Scholar
• Morrison , C. M. and Ellis , A. W. 1995 . Roles of word frequency and age of acquisition in word naming and lexical decision . Journal of Experimental Psychology: Learning, Memory and Cognition , 21 : 116 – 123 .
   Web of Science ®Google Scholar
• Morrison , C. M. and Ellis , A. W. 2000 . Real age of acquisition effects in word naming and lexical decision . British Journal of Psychology , 91 ( 2 ) : 167 – 180 .
   PubMedGoogle Scholar
• Morrison , C. M. , Hirsh , K. W. , Chappell , T. D. and Ellis , A. W. 2002 . Age of acquisition: An evaluation of the cuimulative frequency hypothesis . European Journal of Cognitive Psychology , 14 : 435 – 459 .
   Web of Science ®Google Scholar
• Moss , H. E. and Tyler , L. K. 1997 . A category-specific semantic deficit for nonliving things in a case of progressive aphasia . Brain and Language , 60 : 55 – 58 .
   Web of Science ®Google Scholar
• Moss , H. E. and Tyler , L. K. 2000 . A progressive category-specific deficit for non-living things . Neuropsychologia , 38 : 60 – 82 .
   PubMed Web of Science ®Google Scholar
• Neilsen , J. , Sorensen , A. and Sorensen , K. 1982 . “ Follow-up until age 7 to 11 of 25 unselected children with sex chromosome abnormalities ” . In Children with sex chromosome aneuploidy: Follow-up studies , Edited by: Stewart , D. , Bailey , J. , Netley , C. and Park , E. Vol. 18 , 6198 New York , NY : Alan R. Liss .
   Google Scholar
• Peerman , R. and Content , A. 1995 . Neighbourhood soze in naming: Lexical activation or sublexical correspodences? . Journal of Experimental Psychology: Learning, Memory and Cognition , 21 : 409 – 421 .
   Web of Science ®Google Scholar
• Perneger , T. V. 1998 . What's wrong with Bonferroni adjustments . British Medical Journal , 18 : 1236 – 1238 .
   Google Scholar
• Porter , M. E. , Gardener , H. A. , DeFeudis , P. and Endler , N. S. 1988 . Verbal deficits in Klinefelter (XXY) adults living in the community . Clinical Genetics , 33 : 246 – 253 .
   PubMed Web of Science ®Google Scholar
• Qingfang , Z. and Yufang , Y. 2003 . The determiners of picture naming latency . Acta Psychologica Sinica , 35 ( 4 ) : 447 – 454 .
   Google Scholar
• Ratcliffe , S. G. 1999 . Long term outcome in children of sex chromosome abnormalities . Archives of Disease in Childhood , 80 : 192 – 195 .
   PubMed Web of Science ®Google Scholar
• Ratcliffe , S. , Bancroft , J. , Axworthy , D. and McLaren , W. 1982 . Klinefelter's syndrome in adolescence . Archives of Diseases of Childhood , 57 : 6 – 12 .
   PubMed Web of Science ®Google Scholar
• Ratcliffe , S. , Butler , G. E. and Jones , M. 1991 . “ Edinburgh study of growth and development of children with sex chromosome abnormalities ” . In Children and young adults with sex chromosome aneuploidy , Edited by: Evans , J. , Hamerton , J. and Robinson , A. Vol. 26 , 1 – 44 . New York , NY : Alan R. Liss .
   Google Scholar
• Ratcliffe , S. G. and Paul , N. , eds. 1986 . Prospective studies on children with sex chromosomeaneuploidy , Vol. 22 , New York , NY : Alan R. Liss .
   Google Scholar
• Robinson , S. J. and Temple , C. M. 2009 . The representation of semantic knowledge in a child with Williams Syndrome . Cognitive Neuropsychology , 26 : 307 – 337 .
   PubMed Web of Science ®Google Scholar
• Robinson , S. J. and Temple , C. M. 2010 . Atypical semantic knowledge and autobiographical memory disorder in a young adult with Downs syndrome . Neurocase , 16 ( 5 ) : 377 – 396 .
   PubMed Web of Science ®Google Scholar
• Robinson , S. J. and Temple , C. M. in preparation . Atypical semantic knowledge representation in a child with Turners syndrome. ,
   Google Scholar
• Robinson , S. J. and Temple , C. M. Dissociations in mathematical knowledge: Case studies in Downs syndrome and Williams syndrome . Cortex , accepted for publication
   Google Scholar
• Rogers , T. T. , Lambon-Ralph , M. A. , Garrard , P. , Bozeat , S. , McClelland , J. L. , Hidges , J. R. and Patterson , K. 2004 . Structure and deterioration of semantic memory: A neuropsychological and computational investigation . Psychological Review , 111 : 205 – 235 .
   PubMed Web of Science ®Google Scholar
• Rovet , J. , Netley , C. , Keenan , M. , Bailey , J. and Stweart , D. 1996 . The psychoeducational profile of boys with Klinefelter syndrome . Journal of Learning Disabilities , 29 : 180 – 196 .
   PubMed Web of Science ®Google Scholar
• Samango-Sprouse , C. 2001 . Mental development in polysomy X Klinefelter syndrome (47,XXY; 48,XXXY): Effects of incomplete X inactivation . Seminars in Reproductive Medicine , 19 ( 2 ) : 193 – 202 .
   PubMed Web of Science ®Google Scholar
• Santos , L. R. and Caramazza , A. 2002 . “ The domain specific hypothesis: A developmental and comparative perspective on category-specific deficits ” . In Category-specificity in brain and mind , Edited by: Forde , E. M. E. and Humphreys , G. W. 1 – 23 . Hove , , UK : Psychology Press .
   Google Scholar
• Shelton , J. R. and Caramazza , A. 2001 . “ The organisation of semantic memory ” . In Handbook of Cognitive Neuropsychology: What deficits reveal about the human mind , Edited by: Rapp , B. Hove , , UK : Psychology Press .
   Google Scholar
• Simmons , W. K. and Barsalou , L. W. 2003 . The similarity-in-topography principles: Reconciling theories of conceptual deficits . Cognitive Neuropsychology , 20 ( 3/4/5/6 ) : 451 – 486 .
   PubMed Web of Science ®Google Scholar
• Sorensen , K. 1992 . Physical and mental-development of adolescent males with Klinefelter syndrome . Hormone Research , 37 : 55 – 61 .
   PubMed Web of Science ®Google Scholar
• Stewart , D. , Bailey , J. , Netley , C. and Park , E. 1986 . “ Growth and development of midadolescent children with X and Y chromosome aneuploidy: The Toronto study ” . In Sex chromosome aneuploidy. Follow-up studies , Edited by: Ratcliffe , S. and Paul , N. Vol. 22 , 119 – 182 . New York , NY : Alan R. Liss .
   Google Scholar
• Stewart , D. , Bailey , J. , Netley , C. and Park , E. 1991 . “ Growth, development, and behavioural outcome from mid-adolescence to adulthood in subjects with chromosome aneuploidy: The Toronto study ” . In Children and young adults with sex chromosome aneuploidy , Edited by: Evans , J. , Hamerton , J. and Robinson , A. Vol. 26 , 131 – 188 . New York , NY : Alan R. Liss .
   Google Scholar
• Stewart , D. , Bailey , J. , Netley , C. , Park , M. E. , Curtiss , J. and Cripps , M. 1982 . “ Groth and development of children with X and Y aneuploidy from infancy to puberty ” . In Sex chromosome aneuploidy. Follow-up studies , Edited by: Stewart , D. , Bailey , J. , Netley , C. and Park , E. Vol. 18 , 99 – 154 . New York , NY : Alan R. Liss .
   Google Scholar
• Stemkens , D. , Roza , T. , Verrij , L. , Swaab , H. , Werkhoven , M. K. , Alizadeh , B. Z. , Sinke , R. J. and Giltay , J. C. 2006 . Is there an influence of X-chromosomal imprinting on the phenotype in Klinefelter syndrome? A clinical and molecular genetic study of 61 cases . Clinical Genetics , 70 : 43 – 48 .
   PubMed Web of Science ®Google Scholar
• Temple , C. M. 1986 . Anomia for animals in a child . Brain , 109 : 1225 – 1242 .
   PubMed Web of Science ®Google Scholar
• Temple , C. M. 1989 . Digit dyslexia: A category-specific disorder in developmental dyscalculia . Cognitive Neuropsychology , 6 : 93 – 116 .
   Web of Science ®Google Scholar
• Temple , C. M. 1992 . “ Developmental memory impairment: Faces and patterns ” . In Mental lives: Case studies in cognition , Edited by: Campbell , R. Oxford , UK : Blackwell .
   Google Scholar
• Temple , C. M. 1994 . Developmental dyscalculias: Dissociations and parallels . ANAE , 6 ( Suppl. 30 ) : 1 – 5 .
   Google Scholar
• Temple , C. M. 1997 . Developmental cognitive neuropsychology , Hove , UK : Psychology Press .
   Google Scholar
• Temple , C. M. and Carney , R. A. 1993 . Intellectual functioning of children with Turner syndrome: A comparison of behavioural phenotypes . Developmental Medicine and Child Neurology , 35 : 691 – 698 .
   PubMed Web of Science ®Google Scholar
• Temple , C. M. and Martin Sanfilippo , P. 2003 . Executive skills in Klinefelter's syndrome . Neuropsychologia , 41 : 1547 – 1559 .
   PubMed Web of Science ®Google Scholar
• Temple , C. M. and Richardson , P. 2004 . Developmental amnesia: A new pattern of dissociation with intact episodic memory . Neuropsychologia , 42 : 764 – 781 .
   PubMed Web of Science ®Google Scholar
• Temple , C. M. and Richardson , P. 2006 . Developmental amnesia: Fractionation of developing memory systems . Cognitive Neuropsychology , 23 : 762 – 788 .
   PubMed Web of Science ®Google Scholar
• Tyler , L. , Moss , H. E. , Durrant-Peatfield , M. R. and Levy , J. P. 2000 . Conceptual structure and the structure of concepts: A distributed accounts of category-specific deficits . Brain and Language , 75 : 195 – 231 .
   PubMed Web of Science ®Google Scholar
• Visootsak , J. and Graham , J. M. 2006 . Kleinfelter syndrome and other sex chromosomal aneuploidies . Orphanet Journal of Rare Diseases , 1 : 42
   PubMed Web of Science ®Google Scholar
• Warrington , E. K. 1982 . The fractionation of arithmetical skills: A single case study . Quarterly Journal of Experimental Psychology , 34A : 31 – 51 .
   Web of Science ®Google Scholar
• Warrington , E. K. and McCarthy , R. A. 1983 . Category-specific access dysphasia . Brain , 106 : 859 – 878 .
   PubMed Web of Science ®Google Scholar
• Warrington , E. K. and McCarthy , R. A. 1987 . Categories of knowledge: Further fractionation and an attempted integration . Brain , 110 : 1273 – 1296 .
   PubMed Web of Science ®Google Scholar
• Warrington , E. K. and Shallice , T. 1984 . Category specific semantic impairments . Brain , 107 : 829 – 854 .
   PubMed Web of Science ®Google Scholar
• Wechsler , D. 1992 . Wechsler intelligence scales for children. Third UK edition (WISC-III) , London , , UK : Psychological Corporation .
   Google Scholar
• Wechsler , D. 1999 . Wechsler Abbreviated Scale of Intelligence , London , , UK : Psychological Corporation .
   Google Scholar
• Woodcock , R. W. and Johnson , M. B. 1977 . Woodcock Johnson Psychoeducational Battery , Boston , MA : DLM Teaching Resources Corporation .
   Google Scholar