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Original Article

Auditory Neuropathy with Preserved Cochlear Microphonics and Secondary Loss of Otoacoustic Emissions

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Pages 187-195 | Received 13 Oct 1998, Accepted 18 Nov 1998, Published online: 07 Jul 2009

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Read on this site (12)

Ali A. Almishaal, Shaza Saleh, Hala Alferaih & Osamah Alhelo. (2022) Prevalence, risk factors, and audiological characteristics of auditory neuropathy. International Journal of Audiology 61:12, pages 1018-1026.
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Abeir Osman Dabbous. (2016) Cochlear microphonics recording during ABR threshold testing in children. Hearing, Balance and Communication 14:4, pages 163-182.
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Animesh Barman, Sujeet Kumar Sinha & Prashanth Prabhu. (2016) Amplification strategy to enhance speech perception in individuals with auditory neuropathy spectrum disorder. Hearing, Balance and Communication 14:1, pages 25-35.
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Emrah Can, Ayşegül Verim, Engin Başer & Nurkan İnan. (2015) Auditory neuropathy in late preterm infants treated with phototherapy for hyperbilirubinemia. International Journal of Audiology 54:2, pages 89-95.
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Vijaya Kumar Narne, Prashanth Prabhu, Hunsur Suresh Chandan & Mahadeva Deepthi. (2014) Audiological profiling of 198 individuals with auditory neuropathy spectrum disorder. Hearing, Balance and Communication 12:3, pages 112-120.
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H. S. Chandan, Prashanth Prabhu & Mahadeva Deepthi. (2013) Prevalence and characteristics of tinnitus in individuals with auditory neuropathy spectrum disorder. Hearing, Balance and Communication 11:4, pages 214-217.
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Anu Sharma, Garrett Cardon, Kathryn Henion & Peter Roland. (2011) Cortical maturation and behavioral outcomes in children with auditory neuropathy spectrum disorder. International Journal of Audiology 50:2, pages 98-106.
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Charles I. Berlin, Linda J. Hood, Thierry Morlet, Diane Wilensky, Li Li, Kelly Rose Mattingly, Jennifer Taylor-Jeanfreau, Bronya J.B. Keats, Patti St. John, Elizabeth Montgomery, Jon K. Shallop, Benjamin A. Russell & Stefan A. Frisch. (2010) Multi-site diagnosis and management of 260 patients with Auditory Neuropathy/Dys-synchrony (Auditory Neuropathy Spectrum Disorder*). International Journal of Audiology 49:1, pages 30-43.
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Gary Rance & Elizabeth Janet Barker. (2009) Speech and language outcomes in children with auditory neuropathy/dys-synchrony managed with either cochlear implants or hearing aids. International Journal of Audiology 48:6, pages 313-320.
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Joseph Kei, Rachel Gibson, David Tudehope & Marion Maurer. (2007) Audiologic Outcomes and Management of Infants with Hyperbilirubinemia. Asia Pacific Journal of Speech, Language and Hearing 10:2, pages 71-85.
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Wayne J. Wilson, Kathryn J. Sharp, Charlene Hansen, Poren Kwong & Andrea Kelly. (2007) Especially prominent cochlear microphonic activity in the auditory brainstem response. International Journal of Audiology 46:7, pages 362-373.
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Articles from other publishers (73)

Srikar Vijayasarathy & Hemanth Narayan Shetty. (2021) Perception of temporally enhanced and hearing aid processed speech in children with late-onset Auditory Neuropathy Spectrum Disorder. International Journal of Pediatric Otorhinolaryngology 148, pages 110813.
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Mustafa Yüksel & Ayça Çiprut. (2020) Music and psychoacoustic perception abilities in cochlear implant users with auditory neuropathy spectrum disorder. International Journal of Pediatric Otorhinolaryngology 131, pages 109865.
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Kyoko Kitao, Hideki Mutai, Kazunori Namba, Noriko Morimoto, Atsuko Nakano, Yukiko Arimoto, Tomoko Sugiuchi, Sawako Masuda, Yasuhide Okamoto, Noriko Morita, Hirokazu Sakamoto, Tomoko Shintani, Satoshi Fukuda, Kimitaka Kaga & Tatsuo Matsunaga. (2019) Deterioration in Distortion Product Otoacoustic Emissions in Auditory Neuropathy Patients With Distinct Clinical and Genetic Backgrounds. Ear & Hearing 40:1, pages 184-191.
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A. Farinetti, A. Raji, H. Wu, B. Wanna & C. Vincent. (2018) International consensus (ICON) on audiological assessment of hearing loss in children. European Annals of Otorhinolaryngology, Head and Neck Diseases 135:1, pages S41-S48.
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Prashanth Prabhu. 2018. Handbook of Research on Psychosocial Perspectives of Human Communication Disorders. Handbook of Research on Psychosocial Perspectives of Human Communication Disorders 1 11 .
Kyu-Hee Han, Doo-Yi Oh, Seungmin Lee, Chung Lee, Jin Hee Han, Min Young Kim, Hye-Rim Park, Moo Kyun Park, Nayoung K. D. Kim, Jaekwang Lee, Eunyoung Yi, Jong-Min Kim, Jeong-Whun Kim, Jong-Hee Chae, Seung Ha Oh, Woong-Yang Park & Byung Yoon Choi. (2017) ATP1A3 mutations can cause progressive auditory neuropathy: a new gene of auditory synaptopathy. Scientific Reports 7:1.
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Jijo Pottackal Mathai & Asha Yathiraj. (2017) Performance-Intensity Function and Aided Improvement in Individuals With Late-Onset Auditory Neuropathy Spectrum Disorder. Ear & Hearing 38:2, pages e109-e117.
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Pradeep Yuvaraj & Mannarukrishnaiah Jayaram. (2016) Audiological Profile of Adult Persons with Auditory Neuropathy Spectrum Disorders. Journal of Audiology and Otology 20:3, pages 158-167.
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Jin-Dong Kim. (2016) Assessment and Management of Auditory Neuropathy Spectrum Disorder. Journal of Clinical Otolaryngology Head and Neck Surgery 27:2, pages 246-261.
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Yusuf Kemal Kemaloğlu, Çağıl Gökdoğan, Bülent Gündüz, Eray Esra Önal, Canan Türkyılmaz & Yıldız Atalay. (2015) Newborn hearing screening outcomes during the first decade of the program in a reference hospital from Turkey. European Archives of Oto-Rhino-Laryngology 273:5, pages 1143-1149.
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K. N. Megha, Sugathan Adithya, K. P. Keerthana & Sreeraj Konadath. (2016) Coexistance of tinnitus and hyperacusis in individuals with auditory dys-synchrony: A single case study. Intractable & Rare Diseases Research 5:1, pages 50-55.
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Prashanth Prabhu. (2016) Evaluation of Depression, Anxiety, and Stress in Adolescents and Young Adults with Auditory Neuropathy Spectrum Disorder. Scientifica 2016, pages 1-8.
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Anu Sharma & Garrett Cardon. (2015) Cortical development and neuroplasticity in Auditory Neuropathy Spectrum Disorder. Hearing Research 330, pages 221-232.
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Hunsur Suresh Chandan & Prashanth Prabhu. (2015) Audiological changes over time in adolescents and young adults with auditory neuropathy spectrum disorder. European Archives of Oto-Rhino-Laryngology 272:7, pages 1801-1807.
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Luke Campbell, Arielle Kaicer, Robert Briggs & Stephen O’Leary. (2015) Cochlear Response Telemetry. Otology & Neurotology 36:3, pages 399-405.
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Min Kyu KwakJae Ho ChungChul Won ParkKyung Rae KimSun Wook KimSeung Hwan Lee. (2015) Role of Cochlear Microphonic in Newborn Hearing Test. Korean Journal of Otorhinolaryngology-Head and Neck Surgery 58:6, pages 389.
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Jayakumar Praveena, Hari Prakash & Thuruvas Mohan Rukmangathan. (2014) Language Outcomes Using Hearing Aids in Children with Auditory Dys-Synchrony. Audiology Research 4:1, pages 80.
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P. Prashanth Prabhu & Hunsur Suresh Chandan. (2014) Psychoacoustic Characteristics of Tinnitus in Individuals with Auditory Neuropathy Spectrum Disorder. Audiology Research 4:1, pages 108.
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Stefan Zirn, Julia Louza, Viktor Reiman, Natalie Wittlinger, John-Martin Hempel & Maria Schuster. (2014) Comparison between ABR with click and narrow band chirp stimuli in children. International Journal of Pediatric Otorhinolaryngology 78:8, pages 1352-1355.
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Vijaya Kumar Narne, P. Prashanth Prabhu & Suma Chatni. (2014) Time–frequency analysis of transient evoked-otoacoustic emissions in individuals with auditory neuropathy spectrum disorder. Hearing Research 313, pages 1-8.
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Amy Nash-Kille & Anu Sharma. (2014) Inter-trial coherence as a marker of cortical phase synchrony in children with sensorineural hearing loss and auditory neuropathy spectrum disorder fitted with hearing aids and cochlear implants. Clinical Neurophysiology 125:7, pages 1459-1470.
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Thierry MorletMindy R. RabinowitzLiesl R. LooneyTammy RiegnerL. Ashleigh GreenwoodEric A. ShermanNathan AchillyAnni ZhuEstelle YooRobert C. O'ReillyRobert N. JinksErik G. PuffenbergerAdam HeapsHolmes MortonKevin A. Strauss. (2013) A homozygous SLITRK6 nonsense mutation is associated with progressive auditory neuropathy in humans. The Laryngoscope 124:3.
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Bo Young KimWoo Yong BaeJae-Ryong KimTae Hoon Lee. (2014) Damage of Spiral Ganglion Cell Induced by Ouabain Application in Cat. Korean Journal of Otorhinolaryngology-Head and Neck Surgery 57:9, pages 589.
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P. Prabhu & P. Sneha. (2014) SELF-REPORTED TINNITUS HANDICAP IN INDIVIDUALS WITH AUDITORY NEUROPATHY SPECTRUM DISORDER. Journal of Hearing Science 4:3, pages 43-50.
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Cameron L. Budenz, Kelly Starr, Caroline Arnedt, Steven A. Telian, Henry Alexander Arts, Hussam K. El-Kashlan & Terry A. Zwolan. (2013) Speech and Language Outcomes of Cochlear Implantation in Children With Isolated Auditory Neuropathy Versus Cochlear Hearing Loss. Otology & Neurotology 34:9, pages 1615-1621.
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Hossam Sanyelbhaa Talaat, Lobna Hamed Khalil, Ahmed H. Khafagy, Mariyam M. Alkandari & Ahmed M. Zein. (2013) Persistence of otoacoustic emissions in children with auditory neuropathy spectrum disorders. International Journal of Pediatric Otorhinolaryngology 77:5, pages 703-706.
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Cameron L. Budenz, Steven A. Telian, Caroline Arnedt, Kelly Starr, Henry Alexander Arts, Hussam K. El-Kashlan & Terry A. Zwolan. (2013) Outcomes of Cochlear Implantation in Children With Isolated Auditory Neuropathy Versus Cochlear Hearing Loss. Otology & Neurotology 34:3, pages 477-483.
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H. Chandan & P. Prabhu. (2013) SPEECH PERCEPTION ABILITIES IN INDIVIDUALS WITH AUDITORY NEUROPATHY SPECTRUM DISORDER WITH PRESERVED TEMPORAL SYNCHRONY. Journal of Hearing Science 3:2, pages 16-21.
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P. Jijo & Asha Yathiraj. (2013) AUDIOLOGICAL FINDINGS AND AIDED PERFORMANCE IN INDIVIDUALS WITH AUDITORY NEUROPATHY SPECTRUM DISORDER (ANSD) – A RETROSPECTIVE STUDY. Journal of Hearing Science 3:1, pages 18-26.
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Vijaya Kumar Name & C. S. Vanaja. (2012) Speech Identification with Temporal and Spectral Modification in Subjects with Auditory Neuropathy. ISRN Otolaryngology 2012, pages 1-7.
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Ruchika Mittal, A.V. Ramesh, S.S. Panwar, Ajith Nilkanthan, Satish Nair & Poonam Raj Mehra. (2012) Auditory neuropathy spectrum disorder: Its prevalence and audiological characteristics in an Indian tertiary care hospital. International Journal of Pediatric Otorhinolaryngology 76:9, pages 1351-1354.
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Ming Zhang. (2012) Response Pattern Based on the Amplitude of Ear Canal Recorded Cochlear Microphonic Waveforms across Acoustic Frequencies in Normal Hearing Subjects. Trends in Amplification 16:2, pages 117-126.
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Garrett Cardon & Anu Sharma. (2011) Cortical Auditory Evoked Potentials in Auditory Neuropathy Spectrum Disorder: Clinical Implications. Perspectives on Hearing and Hearing Disorders in Childhood 21:1, pages 31-37.
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Joseph P. Roche, Benjamin Y. Huang, Mauricio Castillo, Marc K. Bassim, Oliver F. Adunka & Craig A. Buchman. (2010) Imaging Characteristics of Children With Auditory Neuropathy Spectrum Disorder. Otology & Neurotology 31:5, pages 780-788.
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Gabriela Ribeiro Ivo Rodrigues, Silvia Nápole Fichino & Dóris Ruthy Lewis. (2009) Presença de microfonismo coclear no peate-clique: diagnóstico diferencial entre espectro da neuropatia auditiva e perdas auditivas cocleares descendentes em crianças. Revista CEFAC 12:6, pages 1077-1083.
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Inger Uhlen & Duan Mao-li. (2009) Auditory neuropathy-a rare condition where CI provides improved hearing and speech development. Journal of Otology 4:1, pages 2-6.
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