Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration, Volume 20, Issue 5-6 (2019)

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Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration, Volume 20, Issue 5-6 (2019)

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Review Article

Review Article
Defining pre-symptomatic amyotrophic lateral sclerosis
Michael Benatar, Martin R. Turner & Joanne Wuu
Pages: 303-309
Published online: 20 Mar 2019
AbstractforDefining pre-symptomatic amyotrophic lateral sclerosis | Full Text | References | PDF (557.7 KB) | EPUB
  • 1012 Views
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Review Article
The C9orf72 hexanucleotide repeat expansion presents a challenge for testing laboratories and genetic counseling
Ashley Crook, Alison McEwen, Jennifer A. Fifita, Katharine Zhang, John B. Kwok, Glenda Halliday, Ian P. Blair & Dominic B. Rowe
Pages: 310-316
Published online: 23 Mar 2019
AbstractforThe C9orf72 hexanucleotide repeat expansion presents a challenge for testing laboratories and genetic counseling | Full Text | References | PDF (947.9 KB) | EPUB
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Original Articles

Article
The relationships between symptoms, disability, perceived health and quality of life in amyotrophic lateral sclerosis/motor neuron disease
Carolyn Anne Young, John Ealing, Christopher McDermott, Tim Williams, Ammar Al-Chalabi, Tahir Majeed, Georgina Burke, Ashwin Pinto, David Dick, Kevin Talbot, Timothy Harrower, Jannette Walsh, Siddharthan Chandran, C. Oliver Hanemann, Roger Mills & Alan Tennant
Pages: 317-327
Published online: 22 May 2019
AbstractforThe relationships between symptoms, disability, perceived health and quality of life in amyotrophic lateral sclerosis/motor neuron disease | Full Text | References | PDF (751.9 KB) | EPUB
  • 1297 Views
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Research Article

Article
A novel muscle cramp scale (MCS) in amyotrophic lateral sclerosis (ALS)
Hiroshi Mitsumoto, Codruta Chiuzan, Madison Gilmore, Yuan Zhang, Camila Ibagon, Brittany McHale, Jonathan Hupf & BjÖrn Oskarsson
Pages: 328-335
Published online: 22 Apr 2019
AbstractforA novel muscle cramp scale (MCS) in amyotrophic lateral sclerosis (ALS) | Full Text | References | PDF (1.1 MB) | EPUB
  • 347 Views
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Article
Incorporating self-reported questions for telemonitoring to optimize care of patients with MND on noninvasive ventilation (MND OptNIVent)
Hikari Ando, Helen Ashcroft-Kelso, Rob Halhead, Carolyn A. Young, Biswajit Chakrabarti, Peter Levene, Rosanna Cousins & Robert M. Angus
Pages: 336-347
Published online: 26 Mar 2019
AbstractforIncorporating self-reported questions for telemonitoring to optimize care of patients with MND on noninvasive ventilation (MND OptNIVent) | Full Text | References | PDF (962.3 KB) | EPUB | Supplemental
  • 511 Views
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Article
Evaluation of remote pulmonary function testing in motor neuron disease
Andrew Geronimo & Zachary Simmons
Pages: 348-355
Published online: 07 Apr 2019
AbstractforEvaluation of remote pulmonary function testing in motor neuron disease | Full Text | References | PDF (453.2 KB) | EPUB | Supplemental
  • 596 Views
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Article
Systematic review of the prognostic role of body mass index in amyotrophic lateral sclerosis
Pingping Ning, Baiyuan Yang, Shuangjiang Li, Xin Mu, Qiuyan Shen, Fayun Hu, Yao Tang, Xinglong Yang & Yanming Xu
Pages: 356-367
Published online: 01 Apr 2019
AbstractforSystematic review of the prognostic role of body mass index in amyotrophic lateral sclerosis | Full Text | References | PDF (505.7 KB) | EPUB | Supplemental
  • 400 Views
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Article
The split hand in amyotrophic lateral sclerosis: a possible role for the neuromuscular junction
Mamede de Carvalho & Michael Swash
Pages: 368-375
Published online: 06 May 2019
AbstractforThe split hand in amyotrophic lateral sclerosis: a possible role for the neuromuscular junction | Full Text | References | PDF (384.5 KB) | EPUB
  • 315 Views
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Original Articles

Article
A neuropsychological and behavioral study of PLS
Bálint S. de Vries, Lauriane A. Spreij, Laura M.M. Rustemeijer, Leonhard A. Bakker, Jan H. Veldink, Leonard H. van den Berg, Tanja C.W. Nijboer & Michael A. van Es
Pages: 376-384
Published online: 28 May 2019
AbstractforA neuropsychological and behavioral study of PLS | Full Text | References | PDF (937.6 KB) | EPUB | Supplemental
  • 2558 Views
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Open Access

Review Article

Article
Speech network regional involvement in bulbar ALS: a multimodal structural MRI study
Sanjana Shellikeri, Matthew Myers, Sandra E. Black, Agessandro Abrahao, Lorne Zinman & Yana Yunusova
Pages: 385-395
Published online: 14 May 2019
AbstractforSpeech network regional involvement in bulbar ALS: a multimodal structural MRI study | Full Text | References | PDF (948.9 KB) | EPUB | Supplemental
  • 283 Views
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Original Articles

Article
Quantifying changes on susceptibility weighted images in amyotrophic lateral sclerosis using MRI texture analysis
Scott L.M. Johns, Abdullah Ishaque, Muhammad Khan, Yee-Hong Yang, Alan H. Wilman & Sanjay Kalra
Pages: 396-403
Published online: 26 Apr 2019
AbstractforQuantifying changes on susceptibility weighted images in amyotrophic lateral sclerosis using MRI texture analysis | Full Text | References | PDF (738.8 KB) | EPUB
  • 404 Views
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Article
Amyotrophic lateral sclerosis mortality rates among ethnic groups in a predominant admixed population in Latin America: a population-based study in Ecuador
Jaime Luna, Pierre-Marie Preux, Giancarlo Logroscino, Daniells Erazo, Oscar H. Del Brutto, Farid Boumediene, Philippe Couratier & Benoit Marin
Pages: 404-412
Published online: 02 Apr 2019
AbstractforAmyotrophic lateral sclerosis mortality rates among ethnic groups in a predominant admixed population in Latin America: a population-based study in Ecuador | Full Text | References | PDF (596.3 KB) | EPUB | Supplemental
  • 185 Views
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Article
Clinical characteristics of a large cohort of US participants enrolled in the National Amyotrophic Lateral Sclerosis (ALS) Registry, 2010–2015
Jaime Raymond, BjÖrn Oskarsson, Paul Mehta & Kevin Horton
Pages: 413-420
Published online: 26 May 2019
AbstractforClinical characteristics of a large cohort of US participants enrolled in the National Amyotrophic Lateral Sclerosis (ALS) Registry, 2010–2015 | Full Text | References | PDF (420.3 KB) | EPUB | Supplemental
  • 11870 Views
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Open Access

Research Article

Article
Post-hoc analyses of the edaravone clinical trials Study 16 and Study 19: a step toward more efficient clinical trial designs in amyotrophic lateral sclerosis
Joseph M. Palumbo, Jean Hubble, Stephen Apple, Koji Takei, Kikumi Tsuda, Shawn Liu, Jeffrey Zhang & Wendy Agnese
Pages: 421-431
Published online: 13 Apr 2019
AbstractforPost-hoc analyses of the edaravone clinical trials Study 16 and Study 19: a step toward more efficient clinical trial designs in amyotrophic lateral sclerosis | Full Text | References | PDF (1.9 MB) | EPUB
  • 3692 Views
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Open Access
Article
The project MinE databrowser: bringing large-scale whole-genome sequencing in ALS to researchers and the public
Rick A.A. van der Spek, Wouter van Rheenen, Sara L. Pulit, Kevin P. Kenna, Leonard H. van den Berg, Jan H. Veldink & on behalf of the Project MinE ALS Sequencing Consortium¶
Pages: 432-440
Published online: 08 Jul 2019
AbstractforThe project MinE databrowser: bringing large-scale whole-genome sequencing in ALS to researchers and the public | Full Text | References | PDF (1.5 MB) | EPUB | Supplemental
  • 3710 Views
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Open Access

Short Report

Report
Ferritin and LDL-cholesterol as biomarkers of fat-free mass loss in ALS
Pierre Jésus, Hélène Blasco, Franck Patin, Salah Eddine Bakkouche, Stéphane Beltran, Christian R. Andrés, Patrick Vourc’h, François Maillot & Philippe Corcia
Pages: 441-444
Published online: 03 Apr 2019
AbstractforFerritin and LDL-cholesterol as biomarkers of fat-free mass loss in ALS | Full Text | References | PDF (149.1 KB) | EPUB
  • 199 Views
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Report

Report
Assessing upper limb function with ALSFRS-R in amyotrophic lateral sclerosis patients
Susana Pinto, Marta Gromicho & Mamede de Carvalho
Pages: 445-448
Published online: 28 Apr 2019
AbstractforAssessing upper limb function with ALSFRS-R in amyotrophic lateral sclerosis patients | Full Text | References | PDF (220.5 KB) | EPUB
  • 252 Views
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Report
Concurrence of NMOSD and ALS in a patient with hexanucleotide repeat expansions of C9orf72
Yuri Matteo Falzone, Marta Radaelli, Federica Agosta, Teuta Domi, Simone Guerrieri, Edoardo Gioele Spinelli, Laura Pozzi, Paola Carrera, Maurizio Ferrari, Giancarlo Comi, Massimo Filippi, Angelo Quattrini & Nilo Riva
Pages: 449-452
Published online: 22 Apr 2019
AbstractforConcurrence of NMOSD and ALS in a patient with hexanucleotide repeat expansions of C9orf72 | Full Text | References | PDF (727.1 KB) | EPUB | Supplemental
  • 182 Views
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Research Article

ALSUntangled 48: Perampanel (Fycompa)
Rick Bedlack
Pages: 453-456
Published online: 20 Feb 2019
First Page PreviewforALSUntangled 48: Perampanel (Fycompa) | Full Text | References | PDF (142.1 KB) | EPUB
  • 3161 Views
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Free Access

Correction

Correction
Correction
Page: (457)
Published online: 11 Jun 2019
CitationforCorrection | Full Text | PDF (171.7 KB) | EPUB
  • 482 Views
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Free Access

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