Prion, Volume 14, Issue 1 (2020)

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Prion, Volume 14, Issue 1 (2020)

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Research Article

Article
Chronic wasting disease associated with prion protein gene (PRNP) variation in Norwegian wild reindeer (Rangifer tarandus)
Mariella E. Güere, Jørn Våge, Helene Tharaldsen, Sylvie L. Benestad, Turid Vikøren, Knut Madslien, Petter Hopp, Christer M. Rolandsen, Knut H. Røed & Michael A. Tranulis
Pages: 1-10
Published online: 18 Dec 2019
AbstractforChronic wasting disease associated with prion protein gene (PRNP) variation in Norwegian wild reindeer (Rangifer tarandus) | Full Text | References | PDF (3.2 MB) | EPUB | Supplemental
  • 2738 Views
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Open Access

Back Matter

Understanding Creutzfeldt-Jackob disease from a viewpoint of amyloidogenic evolvability
Makoto Hashimoto, Gilbert Ho, Yoshiki Takamatsu, Ryoko Wada, Shuei Sugama, Masaaki Waragai, Eliezer Masliah & Takato Takenouchi
Pages: 1-8
Published online: 07 May 2020
AbstractforUnderstanding Creutzfeldt-Jackob disease from a viewpoint of amyloidogenic evolvability | Full Text | References | PDF (2.6 MB) | EPUB
  • 1843 Views
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Open Access

Review

Proteinase K resistant cores of prions and amyloids
Vitaly V. Kushnirov, Alexander A. Dergalev & Alexander I. Alexandrov
Pages: 11-19
Published online: 26 Dec 2019
AbstractforProteinase K resistant cores of prions and amyloids | Full Text | References | PDF (1 MB) | EPUB
  • 3147 Views
  • 25 CrossRef citations
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Open Access

Back Matter

Cloning and analysis of PRNP gene of Vulpes corsac in Qinghai plateau, China
Xue-Hua Yang, Kang Xiao, Yuezhang Wu, Liping Gao, Dongdong Chen, Xiao-Ping Dong & Qi Shi
Pages: 20-23
Published online: 27 Dec 2019
AbstractforCloning and analysis of PRNP gene of Vulpes corsac in Qinghai plateau, China | Full Text | References | PDF (1.9 MB) | EPUB
  • 1047 Views
  • 1 CrossRef citations
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Open Access

Report

An enigmatic case of cortical anopsia: Antemortem diagnosis of a 14-3-3 negative Heidenhain-variant MM1-sCJD
Julius Obergassel, Lisa Lohmann, Sven G. Meuth, Heinz Wiendl, Oliver Grauer & Christopher Nelke
Pages: 24-28
Published online: 27 Dec 2019
AbstractforAn enigmatic case of cortical anopsia: Antemortem diagnosis of a 14-3-3 negative Heidenhain-variant MM1-sCJD | Full Text | References | PDF (1 MB) | EPUB | Supplemental
  • 1513 Views
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Open Access
25 years of yeast prions
Symposium honouring the 25-year anniversary of Reed Wickner’s discovery of yeast prions
Frank Shewmaker & Dan Masison
Pages: 29-30
Published online: 06 Jan 2020
Citationfor25 years of yeast prions | Full Text | References | PDF (397.1 KB) | EPUB
  • 992 Views
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Open Access

Research Article

Article
The cellular prion protein promotes neuronal regeneration after acute nasotoxic injury
Lindsay E. Parrie, Jenna A.E. Crowell, Julie A. Moreno, Stephanie S. Suinn, Glenn C. Telling & Richard A. Bessen
Pages: 31-41
Published online: 17 Jan 2020
AbstractforThe cellular prion protein promotes neuronal regeneration after acute nasotoxic injury | Full Text | References | PDF (2.6 MB) | EPUB
  • 1402 Views
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Open Access

Back Matter

Discovery of a multipotent chaperone, 1-(2,6-Difluorobenzylamino)-3-(1,2,3,4-tetrahydrocarbazol-9-yl)-propan-2-ol with the inhibitory effects on the proliferation of prion, cancer as well as influenza virus
Satoshi Yamashita, Ryo Honda, Mayuko Fukuoka, Tsutomu Kimura, Junji Hosokawa-Muto & Kazuo Kuwata
Pages: 42-46
Published online: 23 Jan 2020
AbstractforDiscovery of a multipotent chaperone, 1-(2,6-Difluorobenzylamino)-3-(1,2,3,4-tetrahydrocarbazol-9-yl)-propan-2-ol with the inhibitory effects on the proliferation of prion, cancer as well as influenza virus | Full Text | References | PDF (953.6 KB) | EPUB
  • 1237 Views
  • 2 CrossRef citations
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Open Access

Research Article

Article
Cross-validation of the RT-QuIC assay for the antemortem detection of chronic wasting disease in elk
N.J. Haley, R. Donner, D.M. Henderson, J. Tennant, E.A. Hoover, M. Manca, B. Caughey, N. Kondru, S. Manne, A. Kanthasamay, S. Hannaoui, S.C. Chang, S. Gilch, S. Smiley, G. Mitchell, A.D. Lehmkuhl & B.V. Thomsen
Pages: 47-55
Published online: 23 Jan 2020
AbstractforCross-validation of the RT-QuIC assay for the antemortem detection of chronic wasting disease in elk | Full Text | References | PDF (951 KB) | EPUB
  • 2249 Views
  • 16 CrossRef citations
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Open Access
Article
Predicting the spread-risk potential of chronic wasting disease to sympatric ungulate species
Catherine I. Cullingham, Rhiannon M. Peery, Anh Dao, Debbie I. McKenzie & David W. Coltman
Pages: 56-66
Published online: 03 Feb 2020
AbstractforPredicting the spread-risk potential of chronic wasting disease to sympatric ungulate species | Full Text | References | PDF (2.5 MB) | EPUB | Supplemental
  • 3778 Views
  • 15 CrossRef citations
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Open Access
Article
Effect of the fluorescent probes ThT and ANS on the mature amyloid fibrils
M. I. Sulatsky, A. I. Sulatskaya, O. I. Povarova, Iu. A. Antifeeva, I. M. Kuznetsova & K. K. Turoverov
Pages: 67-75
Published online: 03 Feb 2020
AbstractforEffect of the fluorescent probes ThT and ANS on the mature amyloid fibrils | Full Text | References | PDF (3.4 MB) | EPUB
  • 3820 Views
  • 41 CrossRef citations
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Open Access
Article
Management of chronic wasting disease in ranched elk: conclusions from a longitudinal three-year study
N.J. Haley, D.M. Henderson, R. Donner, S. Wyckoff, K. Merrett, J Tennant, E.A. Hoover, D. Love, E. Kline, A.D. Lehmkuhl & B.V. Thomsen
Pages: 76-87
Published online: 07 Feb 2020
AbstractforManagement of chronic wasting disease in ranched elk: conclusions from a longitudinal three-year study | Full Text | References | PDF (1.9 MB) | EPUB | Supplemental
  • 2439 Views
  • 7 CrossRef citations
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Open Access

Back Matter

RT-QuIC-based detection of alpha-synuclein seeding activity in brains of dementia with Lewy Body patients and of a transgenic mouse model of synucleinopathy
Jung-Youn Han, Hyung-Sup Jang, Alison J. E. Green & Young Pyo Choi
Pages: 88-94
Published online: 10 Feb 2020
AbstractforRT-QuIC-based detection of alpha-synuclein seeding activity in brains of dementia with Lewy Body patients and of a transgenic mouse model of synucleinopathy | Full Text | References | PDF (1.4 MB) | EPUB
  • 2889 Views
  • 18 CrossRef citations
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Open Access

Research Article

Article
The role of cellular prion protein in lipid metabolism in the liver
Amandeep Singh Arora, Saima Zafar, Umair Latif, Franc Llorens, Sabine Mihm, Prateek Kumar, Waqas Tahir, Katrin Thüne, Mohsin Shafiq, Matthias Schmitz & Inga Zerr
Pages: 95-108
Published online: 05 Mar 2020
AbstractforThe role of cellular prion protein in lipid metabolism in the liver | Full Text | References | PDF (5 MB) | EPUB | Supplemental
  • 2605 Views
  • 2 CrossRef citations
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Open Access

Case Report

Case Report
Clinicopathological findings of a long-term survivor of V180I genetic Creutzfeldt-Jakob disease
Yuichi Hayashi, Yasushi Iwasaki, Masahiro Waza, Shinei Kato, Akio Akagi, Akio Kimura, Takashi Inuzuka, Katsuya Satoh, Tetsuyuki Kitamoto, Mari Yoshida & Takayoshi Shimohata
Pages: 109-117
Published online: 16 Mar 2020
AbstractforClinicopathological findings of a long-term survivor of V180I genetic Creutzfeldt-Jakob disease | Full Text | References | PDF (3.5 MB) | EPUB
  • 2124 Views
  • 11 CrossRef citations
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Open Access

Research Article

Article
Estimation of amyloid aggregate sizes with semi-denaturing detergent agarose gel electrophoresis and its limitations
Polina B. Drozdova, Yury A. Barbitoff, Mikhail V. Belousov, Rostislav K. Skitchenko, Tatyana M. Rogoza, Jeremy Y. Leclercq, Andrey V. Kajava, Andrew G. Matveenko, Galina A. Zhouravleva & Stanislav A. Bondarev
Pages: 118-128
Published online: 19 Apr 2020
AbstractforEstimation of amyloid aggregate sizes with semi-denaturing detergent agarose gel electrophoresis and its limitations | Full Text | References | PDF (3.3 MB) | EPUB
  • 3489 Views
  • 10 CrossRef citations
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Open Access
Article
Analysis of Chinese patients with sporadic Creutzfeldt-Jakob disease
Jing Yang, Haiyan Kuang, Qiong Wang, Jiao Liu, Xueping Chen & Huifang Shang
Pages: 137-142
Published online: 07 May 2020
AbstractforAnalysis of Chinese patients with sporadic Creutzfeldt-Jakob disease | Full Text | References | PDF (602.6 KB) | EPUB | Supplemental
  • 1519 Views
  • 4 CrossRef citations
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Open Access

Case Report

Case Report
Rare genetic E196A mutation in a patient with Creutzfeldt–Jakob disease: a case report and literature
Xiping Wu, Zhao Cui, Xie Guomin, Haifeng Wang, Xiaoling Zhang, Zhiguang Li, Qi Sun & Feiteng Qi
Pages: 143-148
Published online: 05 Jun 2020
AbstractforRare genetic E196A mutation in a patient with Creutzfeldt–Jakob disease: a case report and literature | Full Text | References | PDF (2.3 MB) | EPUB
  • 1254 Views
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Open Access

Research Paper

Article
Determination of amyloid core regions of insulin analogues fibrils
Alexey K. Surin, Sergei Yu. Grishin & Oxana V. Galzitskaya
Pages: 149-162
Published online: 16 Jun 2020
AbstractforDetermination of amyloid core regions of insulin analogues fibrils | Full Text | References | PDF (2.8 MB) | EPUB | Supplemental
  • 2027 Views
  • 12 CrossRef citations
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Open Access

Research paper

Article
Different post-mortem brain regions from three Chinese FFI patients induce different reactive profiles both in the first and second generation RT-QuIC assays
Kang Xiao, Qi Shi, Wei Zhou & Xiao-Ping Dong
Pages: 163-169
Published online: 23 Jun 2020
AbstractforDifferent post-mortem brain regions from three Chinese FFI patients induce different reactive profiles both in the first and second generation RT-QuIC assays | Full Text | References | PDF (824 KB) | EPUB
  • 1165 Views
  • 6 CrossRef citations
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Open Access

Review

Prion domains as a driving force for the assembly of functional nanomaterials
Weiqiang Wang & Salvador Ventura
Pages: 170-179
Published online: 28 Jun 2020
AbstractforPrion domains as a driving force for the assembly of functional nanomaterials | Full Text | References | PDF (2.9 MB) | EPUB
  • 1686 Views
  • 5 CrossRef citations
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Open Access

Case report

Serial evaluation of swallowing function in a long-term survivor of V180I genetic Creutzfeldt-Jakob disease
Kenjiro Kunieda, Yuichi Hayashi, Megumi Yamada, Masahiro Waza, Tomonori Yaguchi, Ichiro Fujishima & Takayoshi Shimohata
Pages: 180-184
Published online: 05 Jul 2020
AbstractforSerial evaluation of swallowing function in a long-term survivor of V180I genetic Creutzfeldt-Jakob disease | Full Text | References | PDF (1.7 MB) | EPUB
  • 1506 Views
  • 4 CrossRef citations
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Open Access

Short communication

Rapid Communication
Geographic variation in the PRNP gene and its promoter, and their relationship to chronic wasting disease in North American deer
Robert M. Zink, Nadje Najar, Hernán Vázquez-Miranda, Brittaney L. Buchanan, Duan Loy & Bruce W. Brodersen
Pages: 185-192
Published online: 26 Jul 2020
AbstractforGeographic variation in the PRNP gene and its promoter, and their relationship to chronic wasting disease in North American deer | Full Text | References | PDF (1.8 MB) | EPUB
  • 1161 Views
  • 9 CrossRef citations
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Open Access

Review

Methionine oxidation within the prion protein
John Bettinger & Sina Ghaemmaghami
Pages: 193-205
Published online: 02 Aug 2020
AbstractforMethionine oxidation within the prion protein | Full Text | References | PDF (1.8 MB) | EPUB
  • 2290 Views
  • 16 CrossRef citations
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Open Access

Correction

Correction
Correction
Page: 206
Published online: 19 Aug 2020
CitationforCorrection | Full Text | PDF (151.9 KB) | EPUB
  • 403 Views
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Open Access

Research paper

Article
Focal sharp waves are a specific early-stage marker of the MM2-cortical form of sporadic Creutzfeldt-Jakob disease
Taiki Matsubayashi, Miho Akaza, Yuichi Hayashi, Tsuyoshi Hamaguchi, Masahito Yamada, Takayoshi Shimohata, Takanori Yokota & Nobuo Sanjo
Pages: 207-213
Published online: 13 Aug 2020
AbstractforFocal sharp waves are a specific early-stage marker of the MM2-cortical form of sporadic Creutzfeldt-Jakob disease | Full Text | References | PDF (856.8 KB) | EPUB | Supplemental
  • 1715 Views
  • 3 CrossRef citations
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Open Access
Article
Association of chronic wasting disease susceptibility with prion protein variation in white-tailed deer (Odocoileus virginianus)
Yasuko Ishida, Ting Tian, Adam L. Brandt, Amy C. Kelly, Paul Shelton, Alfred L. Roca, Jan Novakofski & Nohra E. Mateus-Pinilla
Pages: 214-225
Published online: 23 Aug 2020
AbstractforAssociation of chronic wasting disease susceptibility with prion protein variation in white-tailed deer (Odocoileus virginianus) | Full Text | References | PDF (1.3 MB) | EPUB | Supplemental
  • 1928 Views
  • 10 CrossRef citations
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Open Access

Case Report

Case Report
A patient with spastic paralysis finally diagnosed as V180I genetic Creutzfeldt-Jakob disease 9 years after onset
Taichi Nomura, Ikuko Iwata, Ryoji Naganuma, Masaaki Matsushima, Katsuya Satoh, Tetsuyuki Kitamoto & Ichiro Yabe
Pages: 226-231
Published online: 17 Sep 2020
AbstractforA patient with spastic paralysis finally diagnosed as V180I genetic Creutzfeldt-Jakob disease 9 years after onset | Full Text | References | PDF (1,015.8 KB) | EPUB
  • 991 Views
  • 3 CrossRef citations
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Open Access
Case Report
Corticobasal manifestations of Creutzfeldt-Jakob disease with D178N-homozygous 129M genotype
Yumeng Huang, Ma Jianfang, Rodrigo Morales & Huidong Tang
Pages: 232-237
Published online: 18 Sep 2020
AbstractforCorticobasal manifestations of Creutzfeldt-Jakob disease with D178N-homozygous 129M genotype | Full Text | References | PDF (2.2 MB) | EPUB
  • 1672 Views
  • 1 CrossRef citations
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Open Access

Research Paper

Article
Age structuring and spatial heterogeneity in prion protein gene (PRNP) polymorphism in white-tailed deer
Tyler K. Chafin, Marlis R. Douglas, Bradley T. Martin, Zachery D. Zbinden, Christopher R. Middaugh, Jennifer R. Ballard, M. Cory Gray, Don White Jr & Michael E. Douglas
Pages: 238-248
Published online: 20 Oct 2020
AbstractforAge structuring and spatial heterogeneity in prion protein gene (PRNP) polymorphism in white-tailed deer | Full Text | References | PDF (5.1 MB) | EPUB | Supplemental
  • 1634 Views
  • 10 CrossRef citations
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Open Access
Article
RT-QuIC detection of tauopathies using full-length tau substrates
Joanne M. Tennant, Davin M. Henderson, Thomas M. Wisniewski & Edward A. Hoover
Pages: 249-256
Published online: 10 Nov 2020
AbstractforRT-QuIC detection of tauopathies using full-length tau substrates | Full Text | References | PDF (4.1 MB) | EPUB
  • 2087 Views
  • 15 CrossRef citations
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Open Access

Review

On the role of the cellular prion protein in the uptake and signaling of pathological aggregates in neurodegenerative diseases
Giuseppe Legname & Carlo Scialò
Pages: 257-270
Published online: 19 Dec 2020
AbstractforOn the role of the cellular prion protein in the uptake and signaling of pathological aggregates in neurodegenerative diseases | Full Text | References | PDF (1.2 MB) | EPUB
  • 1744 Views
  • 9 CrossRef citations
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Open Access

Research Paper

Article
Experimental oral transmission of chronic wasting disease to sika deer (Cervus nippon)
Hyun-Joo Sohn, Gordon Mitchell, Yoon Hee Lee, Hyo Jin Kim, Kyung-Je Park, Antanas Staskevicus, Ines Walther, Andrei Soutyrine & Aru Balachandran
Pages: 271-277
Published online: 10 Dec 2020
AbstractforExperimental oral transmission of chronic wasting disease to sika deer (Cervus nippon) | Full Text | References | PDF (1.8 MB) | EPUB
  • 1227 Views
  • 8 CrossRef citations
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Open Access

Short Communication

Search for functional amyloid structures in chicken and fruit fly female reproductive cells
V. A. Siniukova, J. V. Sopova, S. A. Galkina & A. P. Galkin
Pages: 278-282
Published online: 10 Dec 2020
AbstractforSearch for functional amyloid structures in chicken and fruit fly female reproductive cells | Full Text | References | PDF (3.2 MB) | EPUB | Supplemental
  • 1070 Views
  • 8 CrossRef citations
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Open Access

Research Paper

Article
Involvement of N- and C-terminal region of recombinant cervid prion protein in its reactivity to CWD and atypical BSE prions in real-time quaking-induced conversion reaction in the presence of high concentrations of tissue homogenates
Akio Suzuki, Kazuhei Sawada, Takeshi Yamasaki, Nathaniel D Denkers, Candace K Mathiason, Edward A Hoover & Motohiro Horiuchi
Pages: 283-295
Published online: 19 Dec 2020
AbstractforInvolvement of N- and C-terminal region of recombinant cervid prion protein in its reactivity to CWD and atypical BSE prions in real-time quaking-induced conversion reaction in the presence of high concentrations of tissue homogenates | Full Text | References | PDF (2 MB) | EPUB | Supplemental
  • 846 Views
  • 2 CrossRef citations
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