Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration, Volume 20, Issue 7-8 (2019)

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Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration, Volume 20, Issue 7-8 (2019)

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Editorial

Editorial
The histological correlates of imaging metrics: postmortem validation of in vivo findings
Peter Bede
Pages: 457-460
Published online: 11 Jul 2019
First Page PreviewforThe histological correlates of imaging metrics: postmortem validation of in vivo findings | Full Text | References | PDF (128.1 KB) | EPUB
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Review

Review Article
Optimizing the noninvasive ventilation pathway for patients with amyotrophic lateral sclerosis/motor neuron disease: a systematic review
Susan Kathryn Baxter, Maxine Johnson, Mark Clowes, David O’Brien, Paul Norman, Theocharis Stavroulakis, Stephen Bianchi, Mark Elliott, Christopher McDermott & Esther Hobson
Pages: 461-472
Published online: 16 Jun 2019
AbstractforOptimizing the noninvasive ventilation pathway for patients with amyotrophic lateral sclerosis/motor neuron disease: a systematic review | Full Text | References | PDF (1.4 MB) | EPUB | Supplemental
  • 959 Views
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Clinical

Article
Implications of spirometric reference values for amyotrophic lateral sclerosis
Ruben P.A. van Eijk, Jaap N.E. Bakers, Michael A. van Es, Marinus J.C. Eijkemans & Leonard H. van den Berg
Pages: 473-480
Published online: 04 Jul 2019
AbstractforImplications of spirometric reference values for amyotrophic lateral sclerosis | Full Text | References | PDF (1 MB) | EPUB
  • 1762 Views
  • 4 CrossRef citations
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Open Access
Article
Longitudinal analysis of sniff nasal inspiratory pressure assessed using occluded and un-occluded measurement techniques in amyotrophic lateral sclerosis and primary lateral sclerosis
Deirdre Murray, James Rooney, Anna Campion, Lauren Fenton, Michaela Hammond, Mark Heverin, Dara Meldrum, Hannah Moloney, Rachel Tattersall & Orla Hardiman
Pages: 481-489
Published online: 17 Jul 2019
AbstractforLongitudinal analysis of sniff nasal inspiratory pressure assessed using occluded and un-occluded measurement techniques in amyotrophic lateral sclerosis and primary lateral sclerosis | Full Text | References | PDF (1 MB) | EPUB
  • 196 Views
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Article
Nutritional prognostic factors for survival in amyotrophic lateral sclerosis patients undergone percutaneous endoscopic gastrostomy placement
Michele Barone, Maria Teresa Viggiani, Alessandro Introna, Eustachio D’errico, Antonio Scarafino, Andrea Iannone, Alfredo Di Leo & Isabella Laura Simone
Pages: 490-496
Published online: 26 Jul 2019
AbstractforNutritional prognostic factors for survival in amyotrophic lateral sclerosis patients undergone percutaneous endoscopic gastrostomy placement | Full Text | References | PDF (288.4 KB) | EPUB | Supplemental
  • 544 Views
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Article
Loss of appetite is associated with a loss of weight and fat mass in patients with amyotrophic lateral sclerosis
Shyuan T. Ngo, Ruben P.A. van Eijk, V. Chachay, Leonard H. van den Berg, Pamela A. McCombe, Robert D. Henderson & Frederik J. Steyn
Pages: 497-505
Published online: 30 May 2019
AbstractforLoss of appetite is associated with a loss of weight and fat mass in patients with amyotrophic lateral sclerosis | Full Text | References | PDF (941 KB) | EPUB
  • 4140 Views
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Open Access
Article
A case of ALS with posterior cortical atrophy
Tanja C. W. Nijboer, Bram Nitert, Henk-Jan Westeneng, Leonard H. Van Den Berg & Michael A. van Es
Pages: 506-510
Published online: 08 Jul 2019
AbstractforA case of ALS with posterior cortical atrophy | Full Text | References | PDF (579.9 KB) | EPUB
  • 1761 Views
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Open Access
Article
Exploring patient and public involvement in motor neuron disease research
Lucy S. Musson, Christopher J. McDermott & Esther V. Hobson
Pages: 511-520
Published online: 02 Aug 2019
AbstractforExploring patient and public involvement in motor neuron disease research | Full Text | References | PDF (3 MB) | EPUB | Supplemental
  • 401 Views
  • 7 CrossRef citations
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Article
Needs and preferences for psychological interventions of people with motor neuron disease
Kirsty R. Weeks, Rebecca L. Gould, Christopher Mcdermott, Jessica Lynch, Laura H. Goldstein, Christopher D. Graham, Lance McCracken, Marc Serfaty, Robert Howard, Ammar Al-Chalabi, David White, Mike Bradburn, Tracey Young, Cindy Cooper, Dame Pamela J. Shaw & Vanessa Lawrence
Pages: 521-531
Published online: 12 Jul 2019
AbstractforNeeds and preferences for psychological interventions of people with motor neuron disease | Full Text | References | PDF (1.1 MB) | EPUB | Supplemental
  • 6339 Views
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Open Access

Epidemiology

Article
Amyotrophic lateral sclerosis as a multi-step process: an Australia population study
Steve Vucic, Henk-Jan Westeneng, Ammar Al-Chalabi, Leonard H. Van Den Berg, Paul Talman & Matthew C. Kiernan
Pages: 532-537
Published online: 08 Jul 2019
AbstractforAmyotrophic lateral sclerosis as a multi-step process: an Australia population study | Full Text | References | PDF (577.3 KB) | EPUB
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Biomarkers

Article
Neurofilaments in pre-symptomatic ALS and the impact of genotype
Michael Benatar, Joanne Wuu, Vittoria Lombardi, Andreas Jeromin, Robert Bowser, Peter M. Andersen & Andrea Malaspina
Pages: 538-548
Published online: 21 Aug 2019
AbstractforNeurofilaments in pre-symptomatic ALS and the impact of genotype | Full Text | References | PDF (982 KB) | EPUB | Supplemental
  • 975 Views
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Article
Unveiling early cortical and subcortical neuronal degeneration in ALS mice by ultra-high field diffusion MRI
Rodolfo G. Gatto, Manish Amin, Ariel Finkielsztein, Carina Weissmann, Thomas Barrett, Caroline Lamoutte, Osvaldo Uchitel, Ronen Sumagin, Thomas H. Mareci & Richard L. Magin
Pages: 549-561
Published online: 03 Jun 2019
AbstractforUnveiling early cortical and subcortical neuronal degeneration in ALS mice by ultra-high field diffusion MRI | Full Text | References | PDF (3.6 MB) | EPUB | Supplemental
  • 512 Views
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Article
Split-hand index in amyotrophic lateral sclerosis: an F-wave study
Zhi-Li Wang, Mingsheng Liu, Qingyun Ding, Youfang Hu & Liying Cui
Pages: 562-567
Published online: 31 Jul 2019
AbstractforSplit-hand index in amyotrophic lateral sclerosis: an F-wave study | Full Text | References | PDF (297.3 KB) | EPUB
  • 374 Views
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Genomics

Article
Clinicopathologic correlations in a family with a TBK1 mutation presenting as primary progressive aphasia and primary lateral sclerosis
Veronica Hirsch-Reinshagen, Omar A. Alfaify, Ging-Yuek R. Hsiung, Cyril Pottier, Matt Baker, Ralph B. Perkerson III, Rosa Rademakers, Hanna Briemberg, Dean J. Foti & Ian R. Mackenzie
Pages: 568-575
Published online: 27 Jun 2019
AbstractforClinicopathologic correlations in a family with a TBK1 mutation presenting as primary progressive aphasia and primary lateral sclerosis | Full Text | References | PDF (1.5 MB) | EPUB
  • 423 Views
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Clinical Trials

Article
ALS/SURV: a modification of the CAFS statistic
Stephen A. Goutman, Morton B. Brown, Merit Cudkowicz, Nazem Atassi & Eva L. Feldman
Pages: 576-583
Published online: 23 Jul 2019
AbstractforALS/SURV: a modification of the CAFS statistic | Full Text | References | PDF (698.6 KB) | EPUB
  • 287 Views
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Article
A phase III trial of tirasemtiv as a potential treatment for amyotrophic lateral sclerosis
Jeremy M. Shefner, Merit E. Cudkowicz, Orla Hardiman, Bettina M. Cockroft, Jacqueline H. Lee, Fady I. Malik, Lisa Meng, Stacy A. Rudnicki, Andrew A. Wolff, Jinsy A. Andrews & on behalf of the VITALITY-ALS STUDY GROUP
Pages: 584-594
Published online: 13 May 2019
AbstractforA phase III trial of tirasemtiv as a potential treatment for amyotrophic lateral sclerosis | Full Text | References | PDF (416.9 KB) | EPUB
  • 5842 Views
  • 24 CrossRef citations
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Open Access
Article
Safety and tolerability of Triumeq in amyotrophic lateral sclerosis: the Lighthouse trial
Julian Gold, Dominic B. Rowe, Matthew C. Kiernan, Steve Vucic, Susan Mathers, Ruben P. A. van Eijk, Avindra Nath, Marta Garcia Montojo, Gina Norato, Ulisses A. Santamaria, Mary-Louise Rogers, Andrea Malaspina, Vittoria Lombardi, Puja R. Mehta, Henk-Jan Westeneng, Leonard H. van den Berg & Ammar Al-Chalabi
Pages: 595-604
Published online: 08 Jul 2019
AbstractforSafety and tolerability of Triumeq in amyotrophic lateral sclerosis: the Lighthouse trial | Full Text | References | PDF (1 MB) | EPUB | Supplemental
  • 8620 Views
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Open Access
Article
Radicava (edaravone) for amyotrophic lateral sclerosis: US experience at 1 year after launch
Carlayne Jackson, Terry Heiman-Patterson, Pamela Kittrell, Tatyana Baranovsky, Glenn McAnanama, Laura Bower, Wendy Agnese & Mike Martin
Pages: 605-610
Published online: 31 Jul 2019
AbstractforRadicava (edaravone) for amyotrophic lateral sclerosis: US experience at 1 year after launch | Full Text | References | PDF (597.6 KB) | EPUB
  • 6228 Views
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Open Access

Report

Report
Genotype–phenotype correlation and evidence for a common ancestor in two Italian ALS patients with the D124G SOD1 mutation
Claudia Ricci, Fabio Giannini, Enrica Intini & Stefania Battistini
Pages: 611-614
Published online: 07 Jun 2019
AbstractforGenotype–phenotype correlation and evidence for a common ancestor in two Italian ALS patients with the D124G SOD1 mutation | Full Text | References | PDF (229.9 KB) | EPUB | Supplemental
  • 217 Views
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Letters

Letter
The “split-leg” syndrome in ALS: specific or variable?
Mamede de Carvalho & Michael Swash
Pages: 615-616
Published online: 24 Jul 2019
CitationforThe “split-leg” syndrome in ALS: specific or variable? | Full Text | References | PDF (112.2 KB) | EPUB
  • 108 Views
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Letter
Preventive effect of coffee and tea on amyotrophic lateral sclerosis
Tomoyuki Kawada
Page: 617
Published online: 28 Aug 2019
CitationforPreventive effect of coffee and tea on amyotrophic lateral sclerosis | Full Text | References | PDF (201.2 KB) | EPUB
  • 131 Views
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Letter
Author response to a Letter to the Editor entitled: Preventive effect of coffee and tea on amyotrophic lateral sclerosis
Elisabetta Pupillo & Ettore Beghi
Page: 618
Published online: 27 Aug 2019
CitationforAuthor response to a Letter to the Editor entitled: Preventive effect of coffee and tea on amyotrophic lateral sclerosis | Full Text | References | PDF (211.4 KB) | EPUB
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Als Untangled

ALSUntangled no. 49: resveratrol
THE ALSUNTANGLED GROUP
Pages: 619-624
Published online: 04 Apr 2019
First Page PreviewforALSUntangled no. 49: resveratrol | Full Text | References | PDF (133.2 KB) | EPUB
  • 4500 Views
  • 1 CrossRef citations
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Free Access
ALSUntangled No. 50: Antifungal Therapy
THE ALSUNTANGLED GROUP
Pages: 625-629
Published online: 03 Jun 2019
First Page PreviewforALSUntangled No. 50: Antifungal Therapy | Full Text | References | PDF (132.1 KB) | EPUB
  • 5057 Views
  • 2 CrossRef citations
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Free Access

Correction

Correction
Correction
Page: (630)
Published online: 14 Jul 2019
CitationforCorrection | Full Text | PDF (87.7 KB) | EPUB
  • 509 Views
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Free Access

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