Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration, Volume 24, Issue 3-4 (2023)

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Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration, Volume 24, Issue 3-4 (2023)

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Review

Review Article
The future of ALS diagnosis and staging: where do we go from here?
Angela Genge & Adriano Chio
Pages: 165-174
Published online: 12 Dec 2022
AbstractforThe future of ALS diagnosis and staging: where do we go from here? | Full Text | References | PDF (764.7 KB) | EPUB
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Open Access

Clinical

Article
Remote digital assessment of amyotrophic lateral sclerosis functional rating scale – a multicenter observational study
Thomas Meyer, Susanne Spittel, Torsten Grehl, Ute Weyen, Robert Steinbach, Dagmar Kettemann, Susanne Petri, Patrick Weydt, René Günther, Petra Baum, Elena Schlapakow, Jan Christoph Koch, Matthias Boentert, Joachim Wolf, Julian Grosskreutz, Annekathrin Rödiger, Benjamin Ilse, Moritz Metelmann, Jenny Norden, Ruhan Yasemin Koc, Péter Körtvélyessy, Alessio Riitano, Bertram Walter, Barbara Hildebrandt, Friedrich Schaudinn, Christoph Münch & André Maier
Pages: 175-184
Published online: 01 Aug 2022
AbstractforRemote digital assessment of amyotrophic lateral sclerosis functional rating scale – a multicenter observational study | Full Text | References | PDF (498.5 KB) | EPUB | Supplemental
  • 2436 Views
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Open Access
Article
Association between vascular risk factors and cognitive impairment in amyotrophic lateral sclerosis: a case-control study
Tianmi Yang, Qianqian Wei, Chunyu Li, Bei Cao, Ruwei Ou, Yanbing Hou, Lingyu Zhang, Yongping Chen & Huifang Shang
Pages: 185-194
Published online: 19 Aug 2022
AbstractforAssociation between vascular risk factors and cognitive impairment in amyotrophic lateral sclerosis: a case-control study | Full Text | References | PDF (685.7 KB) | EPUB | Supplemental
  • 173 Views
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Epidemiology

Article
The incidence and prevalence of motor neurone disease in South Australia
Jackson Luker, Richard Woodman & David Schultz
Pages: 195-202
Published online: 08 Aug 2022
AbstractforThe incidence and prevalence of motor neurone disease in South Australia | Full Text | References | PDF (802 KB) | EPUB
  • 458 Views
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Article
Survival and epidemiology of amyotrophic lateral sclerosis (ALS) cases in the Chicago and Detroit metropolitan cohort: incident cases 2009–2011 and survival through 2018
Reshma Punjani, Theodore C. Larson, Laurie Wagner, Bryn Davis, D. Kevin Horton & Wendy Kaye
Pages: 203-211
Published online: 05 Oct 2022
AbstractforSurvival and epidemiology of amyotrophic lateral sclerosis (ALS) cases in the Chicago and Detroit metropolitan cohort: incident cases 2009–2011 and survival through 2018 | Full Text | References | PDF (482.4 KB) | EPUB
  • 1490 Views
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Open Access
Article
Impact of occupational categories on the incidence of amyotrophic lateral sclerosis in Sardinia Island, Italy
Vincenzo Pierri, Giuseppe Borghero, Francesca Pili, Tommaso Ercoli, Angelo Fabio Gigante, Luigi Isaia Lecca, Rosario Vasta, Marcello Campagna, Adriano Chiò & Giovanni Defazio
Pages: 212-218
Published online: 07 Dec 2022
AbstractforImpact of occupational categories on the incidence of amyotrophic lateral sclerosis in Sardinia Island, Italy | Full Text | References | PDF (470.6 KB) | EPUB
  • 134 Views
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Article
Occupational history associates with ALS survival and onset segment
Stephen A. Goutman, Jonathan Boss, Christopher Godwin, Bhramar Mukherjee, Eva L. Feldman & Stuart A. Batterman
Pages: 219-229
Published online: 03 Oct 2022
AbstractforOccupational history associates with ALS survival and onset segment | Full Text | References | PDF (811.9 KB) | EPUB | Supplemental
  • 1461 Views
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Open Access
Article
A revision to the United States national ALS registry’s algorithm to improve Case-Ascertainment
Paul Mehta, Jaime Raymond, Moon Han, Reshma Punjani, Theodore Larson, James D. Berry, Benjamin Rix Brooks, Björn Oskarsson, Stephen a. Goutman & Kevin Horton
Pages: 230-236
Published online: 04 Oct 2022
AbstractforA revision to the United States national ALS registry’s algorithm to improve Case-Ascertainment | Full Text | References | PDF (1.1 MB) | EPUB
  • 1004 Views
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Open Access

Health Services

Article
Dying from ALS in Sweden: clinical status, setting, and symptoms
Stefan Sennfält, Ulf Kläppe, Sebastian Thams, Kristin Samuelsson, Rayomand Press, Fang Fang & Caroline Ingre
Pages: 237-245
Published online: 11 Jul 2022
AbstractforDying from ALS in Sweden: clinical status, setting, and symptoms | Full Text | References | PDF (833.7 KB) | EPUB | Supplemental
  • 1686 Views
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Open Access
Article
Amyotrophic lateral sclerosis (ALS) health charities are central to ALS care: perspectives of Canadians affected by ALS
Mira Ahmad, Shelagh K. Genuis, Westerly Luth, Tania Bubela & Wendy S. Johnston
Pages: 246-255
Published online: 16 Sep 2022
AbstractforAmyotrophic lateral sclerosis (ALS) health charities are central to ALS care: perspectives of Canadians affected by ALS | Full Text | References | PDF (509.2 KB) | EPUB
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Open Access
Article
The involvement of palliative care with neurology – a comparison of UK, Switzerland and Italy
David Oliver, Idris Baker, Gian Domenico Borasio, Patrick Cras, Christina Faull, Nilay Hepgul, Stefan Lorenzl, Claire Stockdale, Marianne de Visser, Ludo Vanopdenbosch, Raymond Voltz & Simone Veronese
Pages: 256-262
Published online: 26 Oct 2022
AbstractforThe involvement of palliative care with neurology – a comparison of UK, Switzerland and Italy | Full Text | References | PDF (723.3 KB) | EPUB
  • 1083 Views
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Open Access

Clinical Trials

Article
Combination of ciprofloxacin/celecoxib as a novel therapeutic strategy for ALS
Shiran Salomon-Zimri, Avital Pushett, Niva Russek-Blum, Ruben P. A. Van Eijk, Nurit Birman, Beatrice Abramovich, Erez Eitan, Katya Elgrart, Danielle Beaulieu, David L. Ennist, James D. Berry, Sabrina Paganoni, Jeremy M. Shefner & Vivian E. Drory
Pages: 263-271
Published online: 15 Sep 2022
AbstractforCombination of ciprofloxacin/celecoxib as a novel therapeutic strategy for ALS | Full Text | References | PDF (604.3 KB) | EPUB
  • 7118 Views
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Open Access

Clinical Measurement

Article
A qualitative evaluation of the revised amyotrophic lateral sclerosis functional rating scale (ALSFRS-R) by the patient community: a web-based cross-sectional survey
Danielle Boyce, Michael Robinson, Jesse M. Cedarbaum, Lisa M. Shank, Christopher J. McDermott & Ruben P. A. van Eijk
Pages: 272-280
Published online: 04 Nov 2022
AbstractforA qualitative evaluation of the revised amyotrophic lateral sclerosis functional rating scale (ALSFRS-R) by the patient community: a web-based cross-sectional survey | Full Text | References | PDF (712 KB) | EPUB | Supplemental
  • 1978 Views
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Open Access
Article
Incorporating patient preferences and burden-of-disease in evaluating ALS drug candidate AMX0035: a Bayesian decision analysis perspective
Qingyang Xu, Joonhyuk Cho, Zied Ben Chaouch & Andrew W. Lo
Pages: 281-288
Published online: 26 Oct 2022
AbstractforIncorporating patient preferences and burden-of-disease in evaluating ALS drug candidate AMX0035: a Bayesian decision analysis perspective | Full Text | References | PDF (255.9 KB) | EPUB
  • 1654 Views
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Open Access
Article
Impact of mode of training and recertification on ALSFRS-R rater performance
Jenny Hamilton, Praveena Mohan, Gale Kittle & Jeremy M. Shefner
Pages: 289-294
Published online: 23 Nov 2022
AbstractforImpact of mode of training and recertification on ALSFRS-R rater performance | Full Text | References | PDF (424.4 KB) | EPUB
  • 136 Views
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Article
Yield of EEG features as markers of disease severity in amyotrophic lateral sclerosis: a pilot study
Francesca Notturno, Pierpaolo Croce, Raffaele Ornello, Simona Sacco & Filippo Zappasodi
Pages: 295-303
Published online: 15 Dec 2022
AbstractforYield of EEG features as markers of disease severity in amyotrophic lateral sclerosis: a pilot study | Full Text | References | PDF (1,001.5 KB) | EPUB
  • 210 Views
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Article
MiToS and King’s staging as clinical outcome measures in ALS: a retrospective analysis of the FORTITUDE-ALS trial
Paulos Gebrehiwet, Lisa Meng, Stacy A. Rudnicki, Phil Sarocco, Jenny Wei, Andrew A. Wolff, Adriano Chiò, Jinsy A. Andrews, Angela Genge, Carlayne E. Jackson, Noah Lechtzin, Timothy M. Miller & Jeremy M. Shefner
Pages: 304-310
Published online: 12 Dec 2022
AbstractforMiToS and King’s staging as clinical outcome measures in ALS: a retrospective analysis of the FORTITUDE-ALS trial | Full Text | References | PDF (1.3 MB) | EPUB
  • 1941 Views
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Open Access
Article
Clinically meaningful change: evaluation of the Rasch-built Overall Amyotrophic Lateral Sclerosis Disability Scale (ROADS) and the ALSFRS-R
Christina N. Fournier, Virginia James & Jonathan D. Glass
Pages: 311-316
Published online: 07 Dec 2022
AbstractforClinically meaningful change: evaluation of the Rasch-built Overall Amyotrophic Lateral Sclerosis Disability Scale (ROADS) and the ALSFRS-R | Full Text | References | PDF (190.1 KB) | EPUB
  • 2223 Views
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Open Access

Quality of Life & Burden

Article
The quality of life and depression in primary caregivers of patients with amyotrophic lateral sclerosis is affected by patient-related and culture-specific conditions
Anna Maksymowicz-Śliwińska, Dorothée Lulé, Krzysztof NieporĘcki, Katarzyna Ciećwierska, Albert C. Ludolph & Magdalena Kuźma-Kozakiewicz
Pages: 317-326
Published online: 12 Dec 2022
AbstractforThe quality of life and depression in primary caregivers of patients with amyotrophic lateral sclerosis is affected by patient-related and culture-specific conditions | Full Text | References | PDF (224.2 KB) | EPUB
  • 1346 Views
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Open Access
Article
Stigma experienced by ALS/PMA patients and their caregivers: a mixed-methods study
Marion Sommers-Spijkerman, Melinda S. Kavanaugh, Esther Kruitwagen-Van Reenen, Aimée Zwarts-Engelbert, Johanna M. A. Visser-Meily & Anita Beelen
Pages: 327-338
Published online: 02 Jan 2023
AbstractforStigma experienced by ALS/PMA patients and their caregivers: a mixed-methods study | Full Text | References | PDF (547.4 KB) | EPUB
  • 1352 Views
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Open Access

Brief Reports

Report
Reliable change indices for the Italian Edinburgh Cognitive and Behavioral ALS Screen (ECAS)
Edoardo Nicolò Aiello, Federica Solca, Silvia Torre, Laura Carelli, Alessia Monti, Roberta Ferrucci, Federico Verde, Nicola Ticozzi, Vincenzo Silani & Barbara Poletti
Pages: 339-342
Published online: 26 Oct 2022
AbstractforReliable change indices for the Italian Edinburgh Cognitive and Behavioral ALS Screen (ECAS) | Full Text | References | PDF (597.9 KB) | EPUB | Supplemental
  • 171 Views
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Report
Exposure to electromagnetic fields does not modify neither the age of onset nor the disease progression in ALS patients
Rosario Vasta, Stefano Callegaro, Maurizio Grassano, Antonio Canosa, Sara Cabras, Francesca Di Pede, Enrico Matteoni, Filippo De Mattei, Federico Casale, Paolina Salamone, Letizia Mazzini, Fabiola De Marchi, Cristina Moglia, Andrea Calvo, Adriano Chiò & Umberto Manera
Pages: 343-346
Published online: 11 Nov 2022
AbstractforExposure to electromagnetic fields does not modify neither the age of onset nor the disease progression in ALS patients | Full Text | References | PDF (753.6 KB) | EPUB
  • 170 Views
  • 1 CrossRef citations
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Report
Expanding the spectrum of KIF5A mutations—case report of a large kindred with familial ALS and overlapping syndrome
JarosŁaw Dulski, Audrey J. Strongosky, Rana Hanna Al-Shaikh & Zbigniew K. Wszolek
Pages: 347-350
Published online: 05 Jan 2023
AbstractforExpanding the spectrum of KIF5A mutations—case report of a large kindred with familial ALS and overlapping syndrome | Full Text | References | PDF (411.7 KB) | EPUB
  • 385 Views
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ALS Untangled

ALSUntangled #65: glucocorticoid corticosteroids
Jill Ann Goslinga, Mark Terrelonge Jr., Richard Bedlack, Paul Barkhaus, Benjamin Barnes, Tulio Bertorini, Mark Bromberg, Gregory Carter, Amy Chen, Jesse Crayle, Mazen Dimachkie, Leanne Jiang, Gleb Levitsky, Isaac Lund, Sarah Martin, Christopher Mcdermott, Gary Pattee, Kaitlyn Pierce, Dylan Ratner, Lenka Slachtova, Yuyao Sun & Paul Wicks
Pages: 351-357
Published online: 23 Aug 2022
AbstractforALSUntangled #65: glucocorticoid corticosteroids | Full Text | References | PDF (478.7 KB) | EPUB
  • 2791 Views
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